Results 141 to 150 of about 17,667 (261)

Mechanism-based Inactivation of Human Glutaryl-CoA Dehydrogenase by 2-Pentynoyl-CoA [PDF]

, 2003
K. Sudhindra Rao, Mark Albro, Jerry Vockley, Frank E. Frerman   +3 more
openalex   +1 more source

3-Hydroxyglutaric acid fails to affect the viability of primary neuronal rat cells

Neurobiology of Disease, 2004
Glutaric aciduria type I (GA I) is an autosomal recessive inherited metabolic disorder caused by deficiency of glutaryl-CoA dehydrogenase (GCD) resulting in the accumulation of 3-hydroxyglutaric acid (3OHG), glutaric acid and glutaconic acid in body ...
F Freudenberg, Z Lukacs, K Ullrich
doaj  

Identification and analysis of a glutaryl‐CoA dehydrogenase‐encoding gene and its cognate transcriptional regulator from Azoarcus sp. CIB [PDF]

, 2007
Blas Blázquez, Manuel Carmona, José L. Garcı́a, Eduardo Dı́az   +3 more
openalex   +1 more source

Hallazgos neurorradiológicos de la Acidosis Glutárica tipo I [PDF]

, 2007
Glutaric aciduria type I is a rare disorder of organic acid metabolism caused by deficiency of glutaryl-CoA dehydrogenase, a mitochondrial enzyme. Improper degeneration of amino acids: tryptophan, lysine, and hydroxylysine, results in
Garcia-de-Eulate, R. (Reyes), Larrache, J. (Javier), Luis, E. (Esther) de, Narbona, J. (Juan), Zubieta, J.L. (José L.)   +4 more
core  

Quantitative Fibroblast Acylcarnitine Profiling In The Diagnostic and Prognostic Assessment of Mitochondrial fatty acid [beta]-oxidation disorders [PDF]

, 2002
Mitochondrial fatty acid ß-oxidation disorders are a group of clinically and biochemically heterogeneous defects mainly associated with intolerance to catabolic stress.
Sim, Keow Giak
core  

Primary hyperoxaluria Type 1: organic aciduria diagnosed in plasma [PDF]

, 2013
Background: Primary hyperoxaluria Type 1 (PH1) is a rare autosomal recessive inborn error of glyoxylate metabolism, caused by a deficiency of the liver-specific peroxisomal enzyme alanine:glyoxylate aminotransferase.
Dias, Aureliano, Rodrigues, Marilia, Valongo, Carla, Vilarinho, Laura   +3 more
core  

Teaching Neuro Images : Glutaric aciduria type 1 (glutaryl-CoA dehydrogenase deficiency) [PDF]

, 2011
Paramdeep Singh, Jatinder S. Goraya, Archana Ahluwalia, Kavita Saggar   +3 more
openalex   +1 more source

Microbial diversity and metabolic pathways linked to benzene degradation in petrochemical-polluted groundwater

Environment International
The rapid advance in shotgun metagenome sequencing has enabled us to identify uncultivated functional microorganisms in polluted environments. While aerobic petrochemical-degrading pathways have been extensively studied, the anaerobic mechanisms remain ...
Ruihuan Zhang, Zhencheng Ye, Xue Guo, Yunfeng Yang, Guanghe Li   +4 more
doaj  

[Effect of glutaryl-CoA dehydrogenase gene silencing and high-concentration lysine on the viability of BRL hepatocytes]. [PDF]

Zhongguo Dang Dai Er Ke Za Zhi, 2017
Gao JZ, Zhang C, Yi Q, Ying YQ, Luo XP.
europepmc   +1 more source

Analysis of the effects of β-mannanase on immune function and intestinal flora in broilers fed the low energy diet based on 16S rRNA sequencing and metagenomic sequencing

Poultry Science
: As an enzyme, β-mannanase (BM) can be widely used as feed additive to improve the growth performance of animals. This experiment aimed to determine the effect of the addition of BM to low-energy diet on the immune function and intestinal microflora of ...
Xiaodan Zhang, Yanhong Chen, Zengpeng Lv, Liangjuan Zhou, Yuming Guo   +4 more
doaj