Results 141 to 150 of about 3,031 (152)

Functional characterization of rat glutaryl-CoA dehydrogenase and its comparison with straight-chain acyl-CoA dehydrogenase

Bioorganic & Medicinal Chemistry Letters, 2011
Glutaryl-CoA dehydrogenase catalyzes the oxidative decarboxylation of the γ-carboxylate of the substrate, glutaryl-CoA, to yield crotonyl-CoA and CO(2). The enzyme is a member of the acyl-CoA dehydrogenase (ACD) family of flavoproteins. In the present study, the catalytic properties of this enzyme, including its substrate specificity, isomerase ...
Long, Wu, Yuqin, Qiao, Jinbo, Gao, Guisheng, Deng, Wenhua, Yu, Gong, Chen, Ding, Li   +6 more
openaire   +2 more sources

Glutaryl-CoA dehydrogenase

1993
Dietmar Schomburg, Margit Salzmann, Dörte Stephan   +2 more
openaire   +1 more source

Early signs and course of disease of glutaryl‐CoA dehydrogenase deficiency

Journal of Inherited Metabolic Disease, 1995
Hoffmann GF, Bohles HJ, Burlina A, Duran M, Herwig J, Lehnert W, Leonard JV, Muntau A, Plecko-Starting PK, Superti-Furga A, Trefz FK, Christensen E   +11 more
openaire   +3 more sources

Glutaryl-CoA Dehydrogenase Deficiency

2009
David J. Timson, Richard J. Reece, James B. Thoden, Hazel M. Holden, Andrea L. Utz, Beverly M. K. Biller, Eugen-Matthias Strehle, Markus Böhm, Thomas A. Luger, Alexander K. C. Leung, Andrew L. Wong, Markus G. Donner, Dieter Häussinger, Nirmal S. Mann, Marcus Schmitt, Alexander K. C. Leung, William Lane M. Robson, Andrew L. Wong, Manisha Balwani, Ainu Prakash-Cheng*, Robert J. Desnick, Holger Lerche, Ingrid E. Scheffer, Samuel F. Berkovic, Brigitte M. Lobnig, Peter L. M. Jansen, Siegfried Waldegger, Florian Lang, Hugo ten Cate, Hagen Thieme, Michael Weller, Bärbel Schütte, Ronnie Fass, Hideki Kato, Masaomi Nangaku, Hideki Kato, Masaomi Nangaku, Anthony Chang, Pradeep V. Kadambi, Jessy J. Alexander, Pierre Ronco, Hanna Debiec, Christian Hugo, Brigitte M. Lobnig, Brigitte M. Lobnig, John-John B. Schnog, Victor E. A. Gerdes, Jean Francis, David S. Geller, Knut Brockmann, Dong Wang, Darryl C. Vivo, Stefan Kölker, Stefan Kölker, Elardus Erasmus, Lodewyk J. Mienie, John Vissing, Arnold Reuser, Catherine E. Correia, David A. Weinstein, Joseph I. Wolfsdorf, Yoon S. Shin, Reinout P. Hesselink, Maarten R. Drost, Anton J. M. Wagenmakers, Ger J. Vusse, Stefan Kiechl, Jonas Denecke, Ute Schepers, Thomas Kolter, Konrad Sandhoff, Dianna C. Martin, Barbara L. Triggs-Raine, Seda Sancak, Ralf Paschke, Dorin-Bogdan Borza, Sonja Ständer, Heiko Traupe, Michael A. Becker, Hanneke M. Straaten, Leo F. Verdonck, Hugo Ten Cate, Martin Mempel, Dietrich Abeck, Ismat Ghanem, Samer El Hage, Johannes G. Bode, Thomas A. Fleisher, Steven M. Holland, Bennett Myers, David Herrmann, Zaki Kraiem, Yaron Tomer, Terry F. Davies, James G. White, Sylvia Stöckler-Ipsiroglu, Guido Stoll, Klaus V. Toyka, Valéria Lamounier-Zepter, Klaus Ruether   +99 more
openaire   +1 more source

Glutaric aciduria: Inherited deficiency of glutaryl-CoA dehydrogenase activity

Biochemical Medicine, 1975
S I, Goodman, J G, Kohlhoff
openaire   +2 more sources

Synthesis of Substrate Analogs for Glutaryl-CoA Dehydrogenase: 3-Thia-Glutaryl-CoA and 4-Nitrobutyryl-CoA

Microchemical Journal, 1997
Patricia L. Kultgen, Leonard Edwards, Jr., Colleen M. Byron   +2 more
openaire   +1 more source

Treatment of glutaryl-CoA dehydrogenase deficiency (glutaric aciduria)

The Journal of Pediatrics, 1979
Niels Jacob Brandt, Niels Gregersen, Ernst Christensen, Ida Howard Grøn, Karsten Rasmussen   +4 more
openaire   +1 more source

P287 Acute metabolic presentation in heterozygote glutaryl CoA dehydrogenase mutation

European Journal of Paediatric Neurology, 2009
E. Davies, M. Sharrard, P. Rao, S. Mordekar   +3 more
openaire   +1 more source

Pork and human cDNAs encoding glutaryl-CoA dehydrogenase.

Progress in clinical and biological research, 1992
S I, Goodman, L E, Kratz, F E, Frerman
openaire   +1 more source

Oxidation-reduction potential of glutaryl-CoA dehydrogenase from Paracoccus denitrifleans

1987
Colleen M. Byron, Marian T. Stankovich, Mazhar Husain   +2 more
openaire   +1 more source