Results 131 to 140 of about 2,281,943 (313)

Goal structures in family firms: empirical evidence on the relationship between firm and family goals [PDF]

Goal structures in family firms seems of particular interest to the field as the overall orientation and the objectives of family firms are determined in an area of potential conflict between the two subsystems of firm and family.
Schraml, Stephanie, Achleitner, Ann-Kristin, Braun, Reiner, Welter, Juliane   +3 more
core  

Goals for the rich: Indispensable for a universal post-2015 agenda [PDF]

, 2015
The paper deals with the question of how a fair sharing of costs, responsibilities and opportunities among and within countries can be achieved in formulating and implementing a post-2015 sustainability agenda.
Civil Society Reflection Group on Global Development Perspectives
core  

Creative Hubs and Urban Development Goals: Policy Report [PDF]

, 2018
This report highlights the key policy implications of the AHRC-funded research and knowledge exchange project, 'Creative Hubs and Urban Development Goals: (UK/Brazil)' for the funding and design of creative hubs in the State of São ...
Virani, T, Poli, K, SHIACH, ME, Nakano, D   +3 more
core   +1 more source

Analyzing the observational capabilities of a Moon-based platform for monitoring Earth’s outgoing radiation

Geo-spatial Information Science
A Moon-based platform can observe the whole Earth’s disk instantaneously. This paper introduces a fully linked scheme to analyze the observational capabilities of Earth’s outgoing radiation from a Moon-based platform.
Guang Liu, Runbo Dong, Yin Jin, Mengxiong Zhou, Hanlin Ye, Rui Song, Jan-Peter Muller, Huadong Guo   +7 more
doaj   +1 more source

Clinical Variability and Genotype Driven Outcomes in an International Cohort of 14 Pediatric FIG4 Patients

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Background Biallelic FIG4 variants classically cause distinct conditions characterized by peripheral neuropathy (Charcot‐Marie‐Tooth disease type 4J) or skeletal dysplasia (Yunis‐Varón syndrome). However, central nervous system involvement is increasingly recognized. The prevalence and specific characteristics of movement disorders within FIG4‐
Andrea Gangfuß, Vykuntaraju K. Gowda, Daniel Natera‐de Benito, Pinki Munot, Maria Vanegas, Alejandra Darling, Constanze Reutlinger, Laura Carrera‐Garcia, Gilbert Wunderlich, Heike Kölbel, Burkhard Stüve, David Muhmann, Lucía Monfort Belenguer, Diana‐Gabriela Barca, Viveka Santhosh Reddy C, Varunvenkat M. Srinivasan, Cristina Molina Anguita, Heinz Jungbluth, Hormos Salimi Dafsari, Thomas Rossor, Johann Böhm, Ulrike Schara‐Schmidt, Andreas Roos   +22 more
wiley   +1 more source

Axial Function Reflects Global Severity in Inherited Ataxias: The Upright Stability Score in Ambulatory Friedreich vs. Spinocerebellar Ataxia

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective Inherited ataxias are clinically diverse neurodegenerative diseases, complicating the choice of outcome measures for trials. In spinocerebellar ataxia (SCA), regulatory concerns about the Scale for the Assessment and Rating of Ataxia (SARA) caused a shift toward functional SARA (f‐SARA), contributing to pivotal trial failure.
Christian Rummey, S. H. Subramony, David R. Lynch, Louise A. Corben, Martin B. Delatycki, Jörg B. Schulz, Kathrin Reetz, Massimo Pandolfo, Matthis Synofzik, Theresa Zesiewicz, Antoine Duquette, Matthew Burns, Martin Vyhnálek, Lucie Stovickova, Sinead M. Murphy, Petya Bogdanova‐Mihaylova, Mary Kearney, Richard Walsh, Richard H. Roxburgh, Khalaf Bushara, Marie Y. Davis, Enrico S. Bertini, Gessica Vasco, Shweta Sahni, Mohammed Faruq, Achal K. Srivastava, Bart van de Warrenburg, Elisabetta Indelicato, Sylvia Boesch, Andrew Billnitzer, Tetsuo Ashizawa, Anoopum S. Gupta, Grace Yoon, Georgios Koutsis, Chrysoula Koniari, Zofia Fleszar, Christopher M. Gomez, Andrea Martinuzzi, Gabriella Paparella, Ali G. Hamedani, Puneet Opal, Rizwan S. Akhtar, Caterina Mariotti, Henry Paulson, Peter Todd, Sharan R. Srinivasan, George Wilmot, Ludger Schöls, Susan Perlman, Jeremy D. Schmahmann, Sheng‐Han Kuo, Liana S. Rosenthal, Vikram G. Shakkottai   +52 more
wiley   +1 more source

Myostatin/Smad3 in Spinal Muscular Atrophy: Biomarkers of Disease Severity and Treatment Response

Annals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective Given the role of Myostatin (MSTN) in muscle homeostasis and its modulation by current spinal muscular atrophy (SMA) therapies, we investigated serum MSTN and, for the first time, its downstream effector Smad3 as candidate non‐invasive biomarkers in SMA patients undergoing disease‐modifying therapies (DMTs).
Giorgia Riolo, Claudia Dosi, Stefano Parravicini, Riccardo Zanin, Marta Cheli, Eleonora Giacopuzzi Grigoli, Amalia Canciello, Francesca Andreetta, Riccardo Masson, Silvia Bonanno, Stefania Marcuzzo, Lorenzo Maggi   +11 more
wiley   +1 more source

Quantifying Global Cooperation in the Sustainable Development Goals

Achieving the Sustainable Development Goals (SDGs) hinges critically on extensive international cooperation. However, the extent and evolution of such cooperation at the global level, along with the relative synergy contributions of different country ...
Rongqing Liu, Ying Zhang
core   +1 more source

Goal Modification, Learning Styles, and Achievement in Mathematics [PDF]

, 2010
This study investigated whether mastery and competitive goals could be developed among students, while controlling for the possible effects of student learning styles.
Ganaden, Mildred S., Joaquin, Ma. Nympha B., Ibe, Milagros D.   +2 more
core  

Multi-scale differential network for landslide extraction from remote sensing images with different scenarios

International Journal of Digital Earth
Landslides are major geological hazards globally, causing significant economic losses each year. Accurate landslide detection is essential for disaster prevention, risk assessment, and timely emergency response.
Bo Yu, Meijiang Zhu, Fang Chen, Ning Wang, Huichen Zhao, Lei Wang   +5 more
doaj   +1 more source