Clinical observation and risk assessment after splenectomy in hepatolenticular degeneration patients associated with hypersplenism [PDF]
Frontiers in Surgery, 2022 BackgroundBoth hepatolenticular degeneration (HLD) and viral hepatitis B (HBV) can cause hypersplenism, but whether splenectomy is needed or can be performed in HLD patients associated with hypersplenism is still controversial.
Zhang Wanzong +2 more
exaly +4 more sources
Hepatolenticular degeneration-induced hepatic dysfunction with extremely atypical clinical manifestations: a Case Report [PDF]
Frontiers in MedicineHepatolenticular Degeneration (HLD) is a rare condition caused by a genetic copper metabolism disorder and a basal ganglia-dominated degenerative brain disease. Its characteristic clinical features include progressive extrapyramidal symptoms, psychiatric
Zhuang Tao, Wang Meixia, Meixia Wang
exaly +4 more sources
Бюллетень сибирской медицины, 2005 Hepatolenticular degeneration or Wilson's disease is the hereditary disease, caused by derangement of copper metabolism and its precipitation in brain and internal.
O. Yu. Koryagina +2 more
doaj +2 more sources
Differentially expressed lncRNAs in liver tissues of TX mice with hepatolenticular degeneration [PDF]
Scientific Reports, 2021 Wilson's Disease (WD), an ATP7B-mutated inherited disease that affects copper transport, is characterised by liver and nervous system manifestations. Long non-coding (ln-c) RNAs are widely involved in almost all physiological and pathological processes ...
Juan Zhang +8 more
doaj +2 more sources
Hepatic Lenticular Degeneration With Renal Tumors: A Case Series. [PDF]
Clin Case RepABSTRACT This article presents a series of cases involving hepatic lenticular degeneration (Wilson's disease) complicated by renal tumors. It details the clinical manifestations, diagnostic procedures, treatment strategies, pathological features and outcomes of these patients. We found that this type of patient has an early‐onset disease, complex tumor
Xiao H +9 more
europepmc +2 more sources
Social Support, Self-Management Behaviors, and Coping Styles of Patients With Wilson's Disease: A Quantitative Empirical Research. [PDF]
Brain BehavABSTRACT Purpose Based on Roy's Adaptation Model, this study explores the relationship between social support, coping styles, and self‐management behaviors in patients with Wilson's disease (WD), as well as the underlying mechanisms. Methods A cross‐sectional survey was conducted among 230 WD patients from a tertiary hospital using the Social Support ...
Zhan T +8 more
europepmc +2 more sources
A Diagnosis Hidden in Plain Sight: A Rare Presentation of Isolated Dysarthria in Wilson's Disease-A Case Report. [PDF]
Clin Case RepABSTRACT A clinical picture of isolated dysarthria is relatively uncommon, and the underlying condition causing it can be easily misdiagnosed. In this case, a 24‐year‐old Indian male presented with complaints of slurring of speech occurring for the past 9 months. The patient also complained of difficulty swallowing food using his tongue. There was also
Reddy K +7 more
europepmc +2 more sources
Nomogram-based prediction of portal vein system thrombosis formation after splenectomy in patients with hepatolenticular degeneration [PDF]
Frontiers in Medicine, 2023 Zhang Wanzong, Yu Qingsheng
exaly +2 more sources
Gandou Decoction Decreases Copper Levels and Alleviates Hepatic Injury in Copper-Laden Hepatolenticular Degeneration Model Rats [PDF]
Frontiers in Pharmacology, 2020 An Zhou, Wu Huan, Huan Wu
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Wilson’s disease: Food therapy out of trace elements
Frontiers in Cell and Developmental Biology, 2022 Hepatolenticular degeneration, also known as Wilson’s disease (WD), is an autosomal recessive inheritance nervous disorder of copper metabolism. The treatment of hepatolenticular degeneration emphasizes the combination of medical therapy and dietary ...
Wen-Jie Li +6 more
doaj +1 more source