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HISTOCHEMICAL STUDY ON HEPATOLENTICULAR DEGENERATION
Psychiatry and Clinical Neurosciences, 1963SummaryThe brain and liver of five classical cases of hepatolenticular degeneration were histochemically examined for copper and iron. Within the brain, both copper and iron were detected in two cases. Coppsr was demonstrated in the liver of all cases and iron in two cases. The histochemical findings obtained were discussed.
I, ARIOKA +4 more
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Penicillamine Therapy for Hepatolenticular Degeneration
JAMA, 1964Ingestion of copper was reduced and its excretion was enhanced pharmacologically, principally by the administration of penicillamine, in 33 patients with hepatolenticular degeneration, of whom eight were asymptomatic. Concomitant clinical improvement was noted most markedly and regularly in the neurological manifestations of the disease, whereas the ...
I, STERNLIEB, I H, SCHEINBERG
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Epilepsy and hepatolenticular degeneration
Russian Journal of Child NeurologyBackground. The problem of clarification of the mechanisms of joint formation of epilepsy and extrapyramidal motor defects is of particular interest in the medical community. Aim.
E. V. Ovchinnikova
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Archives of Neurology & Psychiatry, 1941
The question whether the entity described by Kinnier Wilson should be expanded to include additional symptoms and signs reported by others in similar cases has been debated in the scientific literature for the past two decades. The case presented here is of interest because of the nature of the onset, the absence of tremor, the clinical methods used in
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The question whether the entity described by Kinnier Wilson should be expanded to include additional symptoms and signs reported by others in similar cases has been debated in the scientific literature for the past two decades. The case presented here is of interest because of the nature of the onset, the absence of tremor, the clinical methods used in
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[Hepatolenticular degeneration].
Neurologija, 1991Hepatolenticular degeneration (Wilson's disease) is a hereditary disease in which metabolic disorder of copper leads to its accumulation in the liver, brain, cornea and kidneys with consequent pathologic changes in those organs. Hereditary mechanism of the disease is autosomal recessive with prevalence of 30-100 per 1,000,000 inhabitants.
D, Zudenigo, M, Relja
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[Factors influencing the clinical phenotype of hepatolenticular degeneration].
Zhonghua gan zang bing za zhi = Zhonghua ganzangbing zazhi = Chinese journal of hepatology, 2023Q. Xiao, Z. X. Wang, J. G. Fan
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[Guidelines for the diagnosis and treatment of hepatolenticular degeneration (2022 edition)].
Zhonghua gan zang bing za zhi = Zhonghua ganzangbing zazhi = Chinese journal of hepatology, 2022semanticscholar +1 more source
Hepatolenticular Degeneration (Wilson's Disease)
New England Journal of Medicine, 1964WILSON'S disease has for a long time been of particular interest to the neurologist because it exemplifies a specific metabolic disorder involving some special relation between hepatic cirrhosis and degeneration of the brain. The special fea tures of this relation have become of greater interest in recent years in the light of increasing knowledge of ...
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