Results 11 to 20 of about 2,833 (190)

Acute appendicitis in a patient with heterotaxy syndrome

Journal of Pediatric Surgery Case Reports, 2018
Heterotaxy syndrome, also known as situs ambiguous, is a congenital condition that results in an abnormal distribution of visceral organs in the chest and abdomen. Heterotaxy syndrome has generally been categorized into two forms: a left-atrial isomerism
Mariam Selevany, Manrique Guerrero, John A. Perrone, Maryam Hussain   +3 more
doaj   +3 more sources

Early and long-term outcomes following cardiac surgery for patients with heterotaxy syndromeCentral MessagePerspective [PDF]

JTCVS Open
Objective: Heterotaxy syndrome is a complex multisystem abnormality historically associated with high morbidity and mortality. We sought to evaluate the early and long-term outcomes after cardiac surgery in heterotaxy syndrome.
Victor S. Alemany, MD, MS, Alexis Crawford, BA, Kimberlee Gauvreau, ScD, Emily M. Bucholz, MD-PhD, MPH, Pedro J. del Nido, MD, David N. Schidlow, MD, MMus, Meena Nathan, MD, MPH   +6 more
doaj   +2 more sources

Heterotaxy Syndrome Diagnosed in an Adult. [PDF]

Ochsner J
Background: Heterotaxy syndrome, a condition in which the internal organs are abnormally arranged in the thorax or abdomen, is generally diagnosed early in life, often during the neonatal period. Case Report: We present the case of a 42-year-old male who was incidentally diagnosed with polysplenia syndrome and subsequently diagnosed with heterotaxy ...
Guney G, Aydinli F, Aksit S, Kadirli K, Salmanoglu M.   +4 more
europepmc   +3 more sources

Classifying Heterotaxy Syndrome [PDF]

Circulation: Cardiovascular Imaging, 2018
Heterotaxy syndrome is a complex set of abnormalities related to abnormal left–right axis patterning. Although rare (occurring in just over 1 in 10 000 live births1), congenital heart defects associated with heterotaxy syndrome carry a disproportionate burden of morbidity and mortality.2,3 Despite numerous investigations on the genetic underpinning ...
Tal Geva
exaly   +3 more sources

Noncompaction cardiomyopathy and heterotaxy syndrome. [PDF]

Prog Pediatr Cardiol, 2017
Left ventricular noncompaction cardiomyopathy (LVNC) is characterized by compact and trabecular layers of the left ventricular myocardium. This cardiomyopathy may occur with congenital heart disease (CHD). Single cases document co-occurrence of LVNC and heterotaxy, but no data exist regarding the prevalence of this association.
Martinez HR, Ware SM, Schamberger MS, Parent JJ.   +3 more
europepmc   +4 more sources

Unravelling the complexity of heterotaxy syndrome. [PDF]

BMJ Case Rep, 2023
Bilamge A, Vallabhaneni P, Didel S, Rajagopal R.   +3 more
europepmc   +4 more sources

Heterotaxy syndrome. [PDF]

Radiol Bras, 2018
Pauvels LSP, Langer FW, Dos Santos D, Haygert CJP.   +3 more
europepmc   +7 more sources

Heterotaxy syndrome and interrupted inferior vena cava (IVC) with azygos continuation [PDF]

Journal of Kerman University of Medical Sciences, 2020
Heterotaxy syndrome or situs ambiguous is a rare congenital disease in which the pattern of anatomical organization of the thoraco-abdominal visceral and vascular structures is not arranged in normal position.
Mohammad Amin Dolatkhah, Mohammad Sadegh Gholami Farashah, Nastaran Hesam Shariati, khadije dizaji, Susan Mohammadi, Mohammad Bakhtiar Hesam Shariati   +5 more
doaj   +1 more source

Outcomes of Cardiac Repair in Heterotaxy Syndrome Patients—Tertiary Center Experience [PDF]

CJC Pediatric and Congenital Heart Disease

exaly   +2 more sources

Heterotaxy Syndrome [PDF]

Korean Circulation Journal, 2011
Heterotaxy is defined as an abnormality where the internal thoraco-abdominal organs demonstrate abnormal arrangement across the left-right axis of the body. This broad term includes patients with a wide variety of very complex cardiac lesions. Patients with heterotaxy can be stratified into the subsets of asplenia syndrome and polysplenia syndrome, or ...
  +5 more sources