Primary Hemophagocytic Lymphohistiocytosis in a Newborn Child
The article presents the data of clinical observation of hemophagocytic lymphohistiocytosis in newborn child, complicated with spontaneous splenic rupture. Issues of diagnosis according to the recommendations of the International society for the study of
A.I. Kozhemyaka+7 more
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Atypical Histiocyte-Rich Sweet’s Syndrome
Sweet’s Syndrome is a rare neutrophilic dermatosis thought to be a result of immune dysregulation occurring in the setting of drug exposure, recent infection, pregnancy, and underlying malignancy or idiopathic with specific and widely accepted diagnostic
Sharon Chi+4 more
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Rare Presentation of Rosai-Dorfman Disease in Soft Tissue: Diagnostic Findings and Surgical Treatment. [PDF]
Introduction and Importance. Rosai-Dorfman disease (RDD) is a rare, benign type II histiocytosis characterized by the infiltration of S100+ histiocytes and emperipolesis.
Betini, N.+5 more
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Inflammatory Leiomyosarcoma and Histiocyte-rich Rhabdomyoblastic Tumor : a clinicopathological, immunohistochemical and genetic study of 13 cases, with a proposal for reclassification as Inflammatory Rhabdomyoblastic Tumor [PDF]
Inflammatory leiomyosarcoma (ILMS), defined as a malignant neoplasm showing smooth muscle differentiation, a prominent inflammatory infiltrate, and near-haploidization , is a very rare soft tissue tumor with a generally favorable prognosis.
Charville, Gregory W+8 more
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Feline histiocytic diseases are uncommon and rarely reported. Feline progressive histiocytosis (FPH) is the most common histiocytic disease in cats, predominantly affecting middle-aged animals.
Bruna Voltolin de Sena+8 more
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O’Brien’s Granuloma- A Case Report [PDF]
Actinic granuloma is a self-limiting chronic disorder with elastolytic granulomas, mainly of the sun exposed skin and unknown pathogenesis. We report a case of a middle aged woman with multiple annular erythematous lesions.
Pratik Mukesh Thacker+3 more
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Primary oral manifestation of Langerhans cell histiocytosis refractory to conventional therapy but susceptible to BRAF-specific treatment: a case report and review of the literature [PDF]
Langerhans cell histiocytosis (LCH) is a diagnostic and therapeutic challenge. We report on a rare case of its primary oral manifestation that was treated successfully with the BRAF-specific agent, vemurafenib, after insufficient standard LCH treatment ...
Beck-Broichsitter, Benedicta+8 more
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T Cell Histiocyte Rich Large B Cell Lymphoma Presenting as Hemophagocytic Lymphohistiocytosis: An Uncommon Presentation of a Rare Disease [PDF]
T cell histiocyte rich large B cell lymphoma (THRLBCL) is a rare subtype of non-Hodgkin’s lymphoma characterized by malignant B cells with reactive T lymphocytes.
Amina Saqib+4 more
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Nodular histiocytic/mesothelial hyperplasia, a benign entity posing diagnostic challenge
Nodular histiocytic/mesothelial hyperplasia (NHMH) is a benign entity that can simulate malignancies histologically. NHMH was initially described in 13 hernia sacs in 1975.
Hasan Basri Aydin+2 more
doaj
Hemophagocytic lymphohistiocytosis (HLH) is a potentially fatal immune disorder which is uncommon in a nonimmunocompromised adult. A 27-year-old female who presented with fever, hematuria, generalized lymphadenopathy was clinically suspected to have ...
Thondavadi Subbanna Rekha+3 more
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