An unusual Erdheim-Chester disease with orbital involvement: A case report [PDF]
Erdheim-Chester disease is a rare non-Langerhans cell histiocytosis with multiorgan involvement and a specific tropism for perivascular and fatty connective tissue, of unclear origin, with poor response to therapy. Its identification is difficult because
Bencivinni, F.+5 more
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رتيکولوهيستيوسيتوز خود محدود شونده مادرزادی (گزارش 1 مورد با ضايعه منفرد) [PDF]
رتيکولوهيستيوسيتوز خود محدود شونده مادرزادی نوعی هيستيوسيتوز سلول لانگرهانس میباشد که پاتوفيزيولوژی و عامل آن به خوبی مشخص نشده است. برخی از مولفان مکانيسمهای ايمنی که موجب افزايش توليد سيتوکينها میشوند را در ايجاد آن موثر میدانند.
ارجمندی رفسنجانی, خدیجه+2 more
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Langerhans’ cell histiocytosis diagnosed due to dermatological perianal lesion
Langerhans’ cell histiocytosis is a rare disease characterized by proliferation of Langerhans cells in the body. It affects mainly males, predominantly in childhood. Ulcerated plaques are one of the cutaneous forms of presentation.
Bruno Lorenzo Scolaro+5 more
doaj +1 more source
A Case of Refractory Langerhans Cell Histiocytosis Complicated with Hemophagocytic Lymphohistiocytosis Rescued by Cord Blood Transplantation with Reduced-intensity Conditioning [PDF]
We diagnosed a female infant with Langerhans cell histiocytosis (LCH) who was refractory to conventional chemotherapy. She showed refractory inflammation that was complicated with hemophagocytic lymphohistiocytosis (HLH) during LCH chemotherapy ...
Kanamitsu, Kiichiro+4 more
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Langerhans Cell Histiocytosis of the Clavicle in a 13-Year-Old Boy
Langerhans Cell Histiocytosis (LCH) is a rare neoplasm characterized by abnormal proliferation of histiocytic cells. In this case report, we describe a unique case of a 13-year-old boy who presented to the clinic with an insidious onset of mid-clavicular
Shital N. Parikh+3 more
doaj +1 more source
Langerhans cell histiocytosis of the sacrum
Langerhans cell histiocytosis is a rare disease with a wide spectrum of clinical presentations. It is a multisystemic disease with organ system involvement ranging from simple-where it involves only one organ-to widespread progressive disease. Although it can affect any age group, the peak incidence is between 1 and 3 years of age.
openaire +4 more sources
Background:Langerhans cell histiocytosis is a rare disease characterized by the abnormal proliferation of Langerhans cells within a single organ or multiple organs.
Yuqing Liu+3 more
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Paediatric Langerhans cell histiocytosis with diabetes insipidus: remarkable recovery journey
A rare condition known as Langerhans cell histiocytosis (LCH) is characterised by the clonal growth of dendritic cells called Langerhans cells, which play a significant role in the immune system. A diverse range of clinical presentations are probable as
Versha Rani Rai+4 more
doaj +1 more source
Histiocytosis X: Langerhans’ Cell Histiocytosis
Histiocytosis X is a complex and poorly understood entity. Nevertheless, it would appear as if certain themes are found recurrently throughout the literature dealing with this disease and a review of them serves as a useful summary. 1. Problems with Nomenclature.
openaire +3 more sources
Isolated Langerhans cell histiocytosis of the vulva: a case report and review of the literature [PDF]
Isolated Langerhans cell histiocytosis (LCH) of the female genital tract is very rare. A review of the literature revealed that only 15 cases of primary vulvar LCH have previously been published in the English literature.
Beer, Karl+5 more
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