Results 81 to 90 of about 4,921,202 (211)

Langerhans cell histiocytosis; an institutional study [PDF]

, 2017
Background: Langerhans cell histiocytosis is a complex rare disease of the dendritic cell system.The disease can occur at any age, with a peak at 5-10 years.
Shovana Karki, Aasia Rajbhandari
core   +1 more source

Pulmonary Langerhans' cell histiocytosis (histiocytosis X) following metastasising malignant melanoma

, 2002
Background: Pulmonary Langerhans' cell histiocytosis (histiocytosis X) is an uncommon, diffuse interstitial lung disease of unknown cause, mostly presenting in young smokers.
Mirzaie, Masoud, Tirilomis, Theodor, Dalichau, H., Zenker, Dieter   +3 more
core   +1 more source

Polyostotic Langerhans cell histiocytosis presenting as halitosis in a 24-year-old man: a case report

Journal of Medical Case Reports
Background Langerhans cell histiocytosis is a rare disease of the reticuloendothelial system. This report presents a novel case of Langerhans cell histiocytosis with systemic involvement that started with a simple chief complaint.
Hassan Mirmohammad Sadeghi, Sanaz Gholami Toghchi, Fatemeh Mashhadiabbas, Milad Baseri, Maryam Mohammadalizadeh Chafjiri, Parnian Nikraftar, Ardeshir Khorsand   +6 more
doaj   +1 more source

Langerhans Cell Histiocytosis (LCH) and Diabetes Insipidus with Mandibular lesion

, 2012
Langerhans cell histicytosis (LCH) is a rare disorder that primarily affects children. Its occurrence in adult is very rare. We report a case of 42 year old female patient who presented polyuria and polydipsia, loosing teeth and diplopia added to symptom
Sayeh Alizad jahani, Mohammad Reza Mohajeri Tehrani, Bgher Larijani, Somaye Khosravi   +3 more
core  

Skull Base Langerhans Cell Histiocytosis with Diabetes Insipidus and Panhypopituitarism- A Rare Clinical Entity

Bengal Journal of Otolaryngology and Head Neck Surgery, 2017
Introduction A case of Langerhans cell histiocytosis (LGH) involving extensive area of base of skull resulting in panhypopituitarism and diabetes insipidus (DI) is reported.
Anirban Ghosh, Mithun Chaudhury, Abhishek Mukherjee   +2 more
doaj   +3 more sources

Doença de células de langerhans e mama.

Acta Médica Portuguesa, 2011
Langerhans cell histiocytosis (LCH) is a rare systemic disorder, with a diversified presentation and natural history. It can compromise any organ. We report a case of a 32-year-old woman who came to our clinic with an asymptomatic palpable breast mass ...
Cátia Rodrigues, Paulo Santos, Dora Simões, Maria Odete Valério, C Calhaz-Jorge   +4 more
doaj   +1 more source

MEK inhibition achieves robust and durable responses in Erdheim–Chester disease

HemaSphere, Volume 10, Issue 10, October 2026.
Abstract Erdheim–Chester disease (ECD) is a rare histiocytic neoplasm characterized by heterogeneous clinical manifestations and limited evidence to guide targeted therapy. While MEK inhibitors (MEKi) are increasingly used, data on their real‐world efficacy, durability, and safety remain incomplete.
Francesco Pegoraro, Félicien Triboulet, Matthias Papo, Francesco Peyronel, Anita Argentieri, Jerome Razanamahery, Ahmed Idbaih, Polyzois Makras, Ofer Shpilberg, Oshrat Hershkovitz‐Rokah, Michael Girschikofsky, Matthew Collin, Kristian Bowles, Satyen H. Gohil, Rodothea Amerikanou, Emmanuel Ledoult, Tanguy Le Scornet, Mathilde de Menthon, Etienne Riviere, Xavier Boulu, Henry Dupuy, Achille Aouba, Stanislas Faguer, Xavier Solanich, Elena Sieni, Stéphane Barete, Chiara Bellino, Alessandro Tomelleri, Corrado Campochiaro, Lorenzo Dagna, Zahir Amoura, Jean‐François Emile, Fleur Cohen‐Aubart, Augusto Vaglio, Julien Haroche   +34 more
wiley   +1 more source

Langerhans cell and non Langerhans cell histiocytosis: So different?

, 2007
The Author reports the clinical and laboratory criteria that do not support the strict distinction between Langerhans cell and non Langerhans cell histiocytosis as reported in the relevant ...
C. Gelmetti
core   +2 more sources

A large multilobulated cutaneous nodule in infancy

JDDG: Journal der Deutschen Dermatologischen Gesellschaft, EarlyView.
Hannah Wahida, Andy Yan, Stephan Forchhammer   +2 more
wiley   +1 more source

Adult‐Onset Central Nervous System Erdheim–Chester Disease Successfully Treated With Cladribine and Cytarabine: Case Report and Literature Review

eJHaem, Volume 7, Issue 5, October 2026.
ABSTRACT Erdheim–Chester disease (ECD) is a rare histiocytic disorder with heterogeneous clinical manifestations. Central nervous system (CNS) involvement is associated with poor prognosis. Although targeted therapies have improved outcomes in patients with mitogen‐activated protein kinase (MAPK) pathway alterations, optimal treatment strategies for ...
Naoki Watanabe, Hajime Yasuda, Midori Ishii, Norihide Izumi, Ayaka Goto, Tadaaki Inano, Yuji Tomizawa, Taku Hatano, Miki Ando   +8 more
wiley   +1 more source