Results 131 to 140 of about 28,424 (265)

Human inborn errors of the phagocyte respiratory burst: Chronic granulomatous disease and beyond. [PDF]

J Hum Immun
Neehus AL, Sankaran VG, Casanova JL, Bustamante J.   +3 more
europepmc   +1 more source

Inborn Errors [PDF]

Bone Marrow Transplantation, 1999
openaire   +1 more source

Lactobacillus derived small RNAs protect against Klebsiella pneumoniae infection

iMeta, EarlyView.
This study reveals that plant‐derived natural products confer protection against carbapenem‐resistant Klebsiella pneumoniae (CRKP) infection via remodeling the gut microbiota, with Lactobacillus identified as the core beneficial genus. Mechanistically, Lactobacillus murinus (L.
Tingting Xu, Xiuying Tao, Dan Fang, Haijie Zhang, Zhiqiang Wang, Yuan Liu   +5 more
wiley   +1 more source

Effect of Driver Material Properties and Excitation Frequencies on Quantitative Myocardial Stiffness Measurements in Magnetic Resonance Elastography

iRADIOLOGY, EarlyView.
Selecting appropriate driver material and vibration frequency is essential for reliable myocardial stiffness measurement using magnetic resonance elastography. Optimized settings can enhance accuracy for cardiac stiffness assessment. ABSTRACT Background Myocardial stiffness is a crucial indicator of cardiac function and is associated with various ...
Yong Cheng, Jun Wang, Shuangshuang Xu, Zijun Zheng, Yewen Jiang, Peiyang Zheng, Shutian An, Zhanglei Li, Jun Chen, Kiaran P. McGee, Yongqiang Yu, Ren Zhao, Xiaohu Li   +12 more
wiley   +1 more source

Updated EBMT/ESID inborn errors working party guidelines for haematopoietic stem cell transplantation for inborn errors of immunity and metabolism. [PDF]

Bone Marrow Transplant
Albert MH, Lankester AC, Wynn R, Gennery AR, Hoenig M, Kreins A, Morris EC, Slatter M, Bernardo ME, Neven B, Inborn Errors Working Party of the European Society for Blood and Marrow Transplantation and the European Society for Immune Deficiencies, and the European Reference Network on Rare Primary Immunodeficiency Autoinflammatory Autoimmune diseases (RITA).   +11 more
europepmc   +1 more source

Diaphragm Ultrasonography Reveals Progressive Changes in Diaphragmatic Function, Morphology, and Muscle Trophism During Invasive Mechanical Ventilation in Children

Journal of Clinical Ultrasound, EarlyView.
Diaphragm ultrasonography detected progressive structural and functional deterioration in mechanically ventilated children. Prolonged invasive mechanical ventilation and neuromuscular blocking agent use were associated with ventilator‐induced diaphragmatic dysfunction, highlighting ultrasound as a valuable bedside tool to support individualized ...
Juliana Bezerra dos Santos, Emmerson Carlos Franco de Farias, Mary Lucy Ferraz Maia Fiuza de Mello, Rodrigo Santiago Barbosa Rocha   +3 more
wiley   +1 more source

Sarcopenia in Pediatric Intoxication Type Inborn Errors of Metabolism: A Frequent and Underrecognized Condition. [PDF]

J Inherit Metab Dis
Veraldi S, Basso MS, Soglia G, Cirelli R, Spagnoletti G, Bernabei SM, Esposito A, Rizzo C, Cairoli S, Martinelli D, Monti L, Spada M, Pietrobattista A, Dionisi-Vici C.   +13 more
europepmc   +1 more source

National trends in pediatric sepsis hospitalizations, case mix, and mortality, 2016–2022

Journal of Hospital Medicine, EarlyView.
Abstract Introduction Sepsis is a life‐threatening organ dysfunction caused by a dysregulated host response to infection. We evaluated changes in hospitalizations for children with sepsis between 2016 and 2022 and investigated factors associated with in‐hospital mortality.
Sriram Ramgopal
wiley   +1 more source

In a nutshell: Pandora's Box-B-cell lymphoproliferation masking inborn errors of immunity. [PDF]

Br J Haematol
Sánchez-Ramón S, Bussel JB.
europepmc   +1 more source

Causes of death among veterans with alcohol use disorder‐related conditions: A 5‐year follow‐up study of Veterans Health Administration hospitalizations

Journal of Hospital Medicine, EarlyView.
Abstract Background Alcohol use disorder‐related (AUD) diagnoses are common among hospitalized Veterans. Our prior research found that the presence of any AUD‐related diagnosis during hospital admission is associated with a 30% 5‐year mortality rate. Objective To compare demographics and causes of death between hospitalized patients within the Veterans
James C. Willey, Shivali Patel, Bjarni Haraldsson, George Bailey, Andrea Holcombe, Amy M. J. O'Shea, Thad Abrams, Jeydith Gutierrez   +7 more
wiley   +1 more source