Results 51 to 60 of about 57,172 (214)

Clinical Characterization of Patients With 5q Spinal Muscular Atrophy Types 2 and 3 in Brazil: A Cross‐Sectional Observational Study

open access: yesClinical Genetics, Volume 110, Issue 2, Page 172-188, August 2026.
This study describes the clinical heterogeneity of Brazilian patients with 5q spinal muscular atrophy types 2 and 3, highlighting prolonged diagnostic delays and the impact of disease duration on motor function. Early genetic diagnosis and access to multidisciplinary care are crucial to preserve functional outcomes.
Elice Carneiro Batista   +31 more
wiley   +1 more source

Os impactos econômicos da realização das obras de infraestrutura da Copa do Mundo FIFA 2014 no Estado do Rio de Janeiro [PDF]

open access: yes, 2013
Dissertação (mestrado) - Universidade Federal de Santa Catarina, Centro Sócio-Econômico, Programa de Pós-Graduação em Economia, Florianópolis, 2013.Este trabalho tem como objetivo calcular os impactos econômicos, decorrentes dos investimentos em ...
Pinheiro, Felipe Guimarães
core  

Effects of Extrusion Conditions and Oil Addition on the Characteristics of Cheese‐Flavored Corn Snacks and Food Bolus Formation and Properties

open access: yesJournal of Texture Studies, Volume 57, Issue 4, August 2026.
The independent variables influenced the oral processing of corn snacks, and temporality had a low importance in characterizing them. The sunflower oil content had little impact on their sensory profile, suggesting that low sunflower oil content may be sensorially acceptable, contributing to improved nutritional value of corn snacks.
Juliana de Carvalho Marchesin   +2 more
wiley   +1 more source

Modelo insumo producto regional dinámico

open access: yesRevista de Economía, 2015
En tiempos recientes la ciencia económica ha mostrado un creciente interés por conocer la dimensión temporal de prácticamente todos los fenómenos. Esto no es una excepción para los analistas del modelo de insumo producto.
Noé Aarón Fuentes Flores   +2 more
doaj   +1 more source

Sistema interestadual de insumo-produto do Brasil: uma aplicação do método SUIT

open access: yesEconomia Aplicada, 2019
Este artigo propõe um método para a estimação de Tabelas de Produção e Uso Inter-regionais em condições de informação limitada denominado Supply and Use Interregional Tables – SUIT.
J. Guilhoto   +4 more
semanticscholar   +1 more source

Commercial clays in cosmetic formulations for hair care: Characterization and application to improve the mechanical properties of hair fibre

open access: yesInternational Journal of Cosmetic Science, Volume 48, Issue 3, Page 549-561, June 2026.
The shampoo and conditioner bar formulations enhanced hair gloss, promoting softness, improved cuticle alignment, and effective protection of hair shafts against external aggressors. Findings from mechanical properties measurements indicate that the clay‐containing formulations enhance the mechanical strength of hair, contributing to stronger and more ...
João Pedro Gonçalves de Souza Soares   +2 more
wiley   +1 more source

El litio en Argentina: de insumo estratégico a commodity [PDF]

open access: yes, 2014
Es común que, cuando el precio de una materia prima poco conocida crece repentinamente, impulse una serie de abordajes (primero periodísticos, luego académicos) que automáticamente encuentran la explicación del fenómeno en la forma puramente física con ...
Nacif, Federico
core   +1 more source

Democratic Control and Legitimacy of Finnish European Union Policy Process in Crisis Test: Trust, Openness, and the NextGenerationEU

open access: yesEuropean Policy Analysis, Volume 12, Issue 3, Summer 2026.
ABSTRACT Crisis management tests the openness of decision‐making. This threatens the EU's weak democratic legitimacy. Simultaneously, on the national level, Nordic EU decision‐making is considered democratic. However, this model system is understudied, especially in a crisis that highlights its limitations.
Laura Nordström   +2 more
wiley   +1 more source

Estudo comparativo da evolução da produção física e da utilização da capacidade produtiva do Brasil e de Santa Catarina (1994 — 2003) [PDF]

open access: yes, 2005
TCC (graduação) - Universidade Federal de Santa Catarina. Centro Sócio-Econômico. Economia.A proposta deste trabalho foi o de comparar a evolução da produção física e da utilização da capacidade instalada dos setores industriais, para o Brasil e Santa ...
Souza, Octavio Augusto Puccini de
core  

Hurdles to overcome to achieve biostimulant‐driven, low chemical input crop production

open access: yesPLANTS, PEOPLE, PLANET, Volume 8, Issue 3, Page 783-791, May 2026.
Crop production requires considerable chemical inputs that result in significant greenhouse gas emissions and other environmental costs. Biostimulants are natural agents, such as microorganisms or seaweed, applied to plants and soil to stimulate plant growth and reduce chemical inputs. Biostimulant use is rapidly increasing globally, but hurdles remain,
Wolfram Buss   +6 more
wiley   +1 more source

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