Results 21 to 30 of about 9,638 (167)

Swelling of bilateral parotid glands: An unusual symptom of multisystem Langerhans cell histiocytosis

open access: yesSAGE Open Medical Case Reports, 2014
Objective: Langerhans cell histiocytosis is an unusual disorder of unknown etiology with heterogeneous clinical behaviors and variable outcomes. It can involve one or more organs or systems, but to our best knowledge, parotid glands involvement in ...
Xiaojun Yuan   +4 more
doaj   +1 more source

Langerhans cell sarcoma of the skin in association with superficial atypical Langerhans cell proliferation

open access: yesRare Tumors, 2017
Langerhans cell sarcoma of the skin is a rare tumor with aggressive behavior. There are reports of Langerhans cell sarcoma involving the skin in patients with underlying systemic Langerhans cell histiocytosis.
Alejandro Peralta Soler   +2 more
doaj   +1 more source

A Case of Multisystemic Langerhans Cell Histiocytosis in an Adult

open access: yesProceedings of Singapore Healthcare, 2011
Langerhans cell histiocytosis is a rare disease in adults with a myriad of clinical presentations. A case of multisystemic Langerhans cell histiocytosis with involvement of bone, skin, lungs, and the hypothalamic-pituitary-axis is reported.
Chiaw Ling Chng MBBS, MRCP
doaj   +1 more source

Langerhans Cell Histiocytosis: An Unusual Presentation

open access: yesPhilippine Journal of Otolaryngology Head and Neck Surgery, 2008
Objective:  To describe an unusual presentation of Langerhans cell histiocytosis in the craniofacial skeleton in a patient previously diagnosed with Pott’s disease. Methods: Design: Case report. Setting:  Tertiary care center.  Patient: One
Kathleen R. Fellizar   +1 more
doaj   +1 more source

A Case of Orbital Langerhans Cell Histiocytosis in an Adult

open access: yesActa Médica Portuguesa, 2019
Langerhans cell histiocytosis remains an enigmatic disease with a very heterogeneous presentation. We describe a rare case of orbital Langerhans cell histiocytosis in a 39-year-old female patient who presented right orbital pain and edema of the upper ...
Inês Carneiro   +2 more
doaj   +1 more source

Three cases of congenital self‐healing Langerhans cell histiocytosis with BRAF‐V600E mutation

open access: yesJEADV Clinical Practice, 2022
Congenital self‐healing Langerhans cell histiocytosis (CSHLCH) is a rare variant of Langerhans cell histiocytosis characterised by the presence of skin lesions in the neonate and spontaneous self‐healing after a variable period of time.
Mar Ramírez‐Lluch   +7 more
doaj   +1 more source

Isolated Langerhans Histiocytosis in Thyroid: Thyroidectomy or Chemotherapy? [PDF]

open access: yesJournal of Clinical and Diagnostic Research, 2015
Langerhans cell histiocytosis (LCH) is a rare disorder of mononuclear phagocytic system whose clinical presentation varies from the localised involvement of a single bone to a widely disseminated disease.
Anoop Attakkil   +4 more
doaj   +1 more source

Langerhans cell histiocytosis

open access: yesClinical and Translational Oncology, 2008
Langerhans cell histiocytosis (LCH) is a poorly understood proliferative disease, with different patterns of clinical presentation. Currently it is classified according to the number and type of system involved and the degree of organ dysfunction. The aetiology of the disease remains uncertain, and in some cases the disease is polyclonal, suggesting a ...
Joan Manel, Gasent Blesa   +6 more
openaire   +5 more sources

Infantile Central Nervous System Juvenile Xanthogranuloma With Somatic CSF1R Mutation Responsive to Imatinib Monotherapy

open access: yesPediatric Blood &Cancer, EarlyView.
ABSTRACT Juvenile xanthogranuloma (JXG) of the central nervous system (CNS) is a rare non‐Langerhans cell histiocytosis. CSF1R mutations have been reported for peripheral JXG, but not in CNS JXG. A 3‐month‐old male presented with fever, lymphadenopathy, and macrocephaly with bulging fontanelles.
Sima Vazquez   +8 more
wiley   +1 more source

Spontaneous pneumothorax with isolated pulmonary Langerhans cell histiocytosis in an adult case: A common manifestation of rare disease

open access: yesClinical Case Reports, 2023
Key Clinical Message Pulmonary Langerhans cell histiocytosis should be evaluated even in adults with no previous medical history and no history of cigarette smoking who have spontaneous pneumothorax and evidence of multiple lung cystic lesions, and other
Mitra Samareh Fekri   +3 more
doaj   +1 more source

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