Results 41 to 50 of about 3,332,803 (291)
ABSTRACT Objective Facioscapulohumeral muscular dystrophy (FSHD) is one of the most debilitating and common muscular dystrophies. Despite its severity, no approved therapy exists for FSHD patients. However, several therapeutic candidates are currently under development, and some have recently entered clinical trials, marking the need for reliable ...
Mustafa Bilal Bayazit +11 more
wiley +1 more source
One of the directions of reforming the system of deposit insurance in the world is risk-oriented approach, which means that the degree of involvement in the system is determined by the degree of exposure of the participant’s operations to risk.
Oleh Ilnytskyi +2 more
doaj +1 more source
The Legal Deposit of Non-Print Publications: The 1998 Working Party on Legal Deposit
The Government has accepted the recommendation of the Working Party, chaired by Sir Anthony Kenny, that legislation for the legal deposit of non-print publications is necessary in order to maintain the UK published archive. As an interim measure, representatives of the publishers and the legal deposit libraries are seeking agreement on a system of ...
openaire +2 more sources
Juvenile Huntington Disease With Cerebellar‐Predominant Atrophy Identified by Genome Sequencing
ABSTRACT Juvenile Huntington disease accounts for a small fraction of Huntington disease cases and is driven by the largest trinucleotide repeat expansions. We describe a 6‐year‐old boy with progressive global regression, generalized dystonia, and epilepsy, in whom serial imaging showed striking cerebellar‐predominant atrophy with an initially normal ...
Enrique Gonzalez Saez‐Diez +5 more
wiley +1 more source
Legal deposit in the Map and Picture Collection of the National and University Library
Legal deposit has been the most important way of the acquisition of cartographic and pictorial library materials. For the period from 1948 to 1991, it represented up to 80 % of the inflow, composed mostly of postcards, obituaries, posters, congratulation
Renata Šolar
doaj +1 more source
A mask‐free and cost‐effective UV‐pico‐second laser‐based microfabrication method is proposed to fabricate large‐area biodegradable microelectrode arrays and pressure sensors. These devices demonstrate low impedance, good conformability, excellent biocompatibility, and rapid degradation, providing a new route for next‐generation transient electronics ...
Bhavani Prasad Yalagala +5 more
wiley +1 more source
Implementing e-legal deposit: a British Library perspective [PDF]
An account of progress since 2004, from the enabling legislation provided by the U.K. Legal Deposit Libraries Act, towards secondary legislation through which deposit of electronic and other non-print material can commence.
Tuck, John, Milne, Ronald
core +3 more sources
From Lab to Landscape: Environmental Biohybrid Robotics for Ecological Futures
This Perspective explores environmental biohybrid robotics, integrating living tissues, microorganisms, and insects for operation in real‐world ecosystems. It traces the leap from laboratory experiments to forests, wetlands, and urban environments and discusses key challenges, development pathways, and opportunities for ecological monitoring and ...
Miriam Filippi
wiley +1 more source
Printing and publishing production with regard to legal deposit for the period 1991-2006
The paper presents a statistical survey of Slovenian printing and publishing production in the light of legal deposit for the period 1991-2006. The Slovenian printing and publishing production of monographic publications is presented according to ...
Damijana Kisovec-Trček
doaj +1 more source
ATTRACTED RESOURCES OF A COMMERCIAL BANK
The relevance of this work is confirmed by the fact that in the modern Russian economy there is a tendency towards a decrease in liquidity, as well as a continuing crisis in the financial sector, in connection with which the competition for inexpensive ...
O. Belyaeva
doaj +1 more source

