Results 111 to 120 of about 6,813 (202)
The main problem in the treatment of pulmonary lymphangioleiomyomatosis, which frequently occurs in the reproductive age, is the control of chylothorax and disease progression.
Mario Lise +3 more
core +1 more source
Pulmonary lymphangioleiomyomatosis (LAM) and renal angiolipomas are rare but distinct clinical entities that share similar morphological features. Lung transplantation is considered as a valuable therapeutic modality in patients with end-stage pulmonary ...
Robert, John +4 more
core +1 more source
Lymphangioleiomyomatosis and TSC2-/- cells
The cells comprising pulmonary lymphangioleiomyomatosis (LAM) and renal angiomyolipomas (AMLs) are heterogeneous, with variable mixtures of cells exhibiting differentiation towards smooth muscle, melanocytic, and lymphatic or blood endothelial cells ...
G. Pacheco Rodriguez +5 more
core +1 more source
Repurposing Nitazoxanide for Potential Treatment of Rare Disease Lymphangioleiomyomatosis
Lymphangioleiomyomatosis (LAM) is a rare genetic lung disease. Unfortunately, treatment with the mTORC1 inhibitor Rapamycin only slows disease progression, and incomplete responses are common.
Stella Bähr +6 more
doaj +1 more source
Pulmonary Lymphangioleiomyomatosis [PDF]
U, Costabel, J, Guzman
openaire +2 more sources
Spontaneous Pneumothorax Secondary to Lymphangioleiomyomatosis
Lymphangioleiomyomatosis (LAM) is a rare cystic lung disease presenting primarily in women of child-bearing age. It can occur sporadically or in association with tuberous sclerosis.
Michelle Sharp +4 more
core +1 more source
Lymphangioleiomyomatosis and SZ alpha(1)-antitrypsin disease: a unique combination?
We describe a case of a 37-year-old female ex-smoker with lymphangioleiomyomatosis and SZ alpha(1)-antitrypsin disease who underwent successful bilateral sequential lung transplantation.
Kwack, Sunye +4 more
core +1 more source
Lymphangioleiomyomatosis of the lungs with staged bilateral chylothorax
. Lymphangioleiomyomatosis (LAM) is a slowly progressive, low-grade, metastasising neoplasm of women, characterised by infiltration of the lung parenchyma with abnormal smooth muscle-like cells, resulting in cystic lung destruction.
M.S. Opanasenko +10 more
doaj +1 more source
A Clinicopathological Analysis of Pulmonary Lymphangioleiomyomatosis
Background and objective Pulmonary lymphangioleiomyomatosis (PLAM) is a rare tumor with unique clinicopathological features. The aim of this study is to investigate the clinicopathological features, the diagnosis and differential diagnosis of pulmonary ...
Huijiao CHEN +5 more
core
Angiomyolipomas, Renal Cell Carcinomas and Pulmonary Lymphangioleiomyomatosis [PDF]
Panagiotis J Vlachostergios +3 more
doaj +1 more source

