Results 1 to 10 of about 3,849 (151)

Diffuse Pulmonary Lymphangiomatosis

open access: yesCanadian Respiratory Journal, 2013
Diffuse pulmonary lymphangiomatosis (DPL) is a rare disease characterized by infiltration of the lung, pleura and mediastinum with thin-walled lymphangiomas.
Eunhee S Yi, Kunal C Kadakia
exaly   +4 more sources

Bilateral Renal Lymphangiomatosis

open access: yesSaudi Journal of Kidney Diseases and Transplantation, 2022
Lymphangiomatosis is a rare and benign mesenchymal disorder where there is developmental malformation and dilatation of lymphatic channels. The most common sites for lymphangiomatosis are the cervical neck and axilla, but it can also occur in the ...
Muhammad Tanzeel Abbasi   +5 more
doaj   +3 more sources

Acquired Vulvar Lymphangiomatosis: A Rare Condition After Cervical Cancer Treatment. [PDF]

open access: yesClin Case Rep
Vulvar lymphangiomatosis is a rare but important clinical consideration in the context of cervical cancer history. The differential diagnosis between this condition and vulvar cancer through histopathological confirmation is essential. Despite concerning
Moura M, Brás IM, Alves C, Aguiar T.
europepmc   +2 more sources

Systemic congenital lymphangiomatosis [PDF]

open access: yesSão Paulo Medical Journal, 1996
Systemic lymphangiomatosis is a rare disease characterized by the exageration of lymphatic channel proliferation, occurring in children and young adults.
Ligia Maria Suppo de Souza   +3 more
doaj   +5 more sources

Lymphangiomatosis diagnosed using transbronchial lung cryobiopsy: A case report. [PDF]

open access: yesRespir Med Case Rep
Lymphangiomatosis, a rare systemic condition characterized by abnormally dilated lymphatic structures affecting multiple organs, is typically diagnosed using surgical lung biopsy or lymphangiography, both of which present significant technical challenges.
Ito K   +13 more
europepmc   +2 more sources

Long-Term Remission of Peritoneal Lymphangiomatosis with Sirolimus Therapy: A Case Report with 8-Year Follow-Up. [PDF]

open access: yesCase Rep Gastroenterol
Introduction: Peritoneal lymphangiomatosis is a rare benign lymphatic disorder with diagnostic and therapeutic challenges. It may mimic peritoneal carcinomatosis or mesothelioma, often requiring histological confirmation.
Jovanovic P   +7 more
europepmc   +2 more sources

Case Report: Bilateral renal lymphangiomatosis with atypical manifestations in an elderly patient. [PDF]

open access: yesFront Med (Lausanne)
Renal lymphangiomatosis is a rare, benign malformation of the renal lymphatic system. This case report describes an atypical presentation in a 63-year-old male who presented with acute fever and left lower abdominal pain, accompanied by elevated ...
Hu D, Yuan Y, Wang B, Li Y.
europepmc   +2 more sources

Complex Lymphatic Anomaly Presenting with Chylothorax, Chylous Ascites, and Generalized Subcutaneous Edema in a Young Cat: Comparative Insights Based on the Human ISSVA Classification. [PDF]

open access: yesVet Sci
In human medicine, the 2025 International Society for the Study of Vascular Anomalies (ISSVA) classification distinguishes localized lymphatic malformations from systemic disorders referred to as complex lymphatic anomalies (CLAs), including generalized ...
Terai K   +6 more
europepmc   +2 more sources

Lymphangiomatosis with pulmonary, mediastinal, and spinal involvement in a pediatric patient: a case report. [PDF]

open access: yesBMC Pediatr
Background Lymphangiomatosis is a rare disorder characterized by abnormal proliferation and dilation of lymphatic vessels, resulting in non-specific clinical manifestations.
Sun Y, Zhou J, Hu X, Li M, Tan L.
europepmc   +2 more sources

Case report: Long-term local control of recurrent lymphatic malformations using minocycline sclerotherapy following surgical resection in a dog. [PDF]

open access: yesFront Vet Sci
Lymphatic malformation is a benign congenital vascular anomaly that is rarely reported in veterinary medicine. Complete surgical excision is extremely challenging because the boundary between the abnormal and normal tissues is poorly defined, which ...
Taki H   +6 more
europepmc   +2 more sources

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