Erdheim-Chester Disease Involving Lymph Nodes and Liver Clinically Mimicking Lymphoma: A Case Report [PDF]
Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis and multisystem disease. First described in 1930, there are no more than 750 cases reported.
Yeoun Eun Sung +3 more
doaj +1 more source
Long-standing necrobiotic xanthogranuloma limited to the skin: A case report
Necrobiotic xanthogranuloma is a rare non-Langerhans cell histiocytosis with a known association with monoclonal gammopathies and malignant conditions. There is a lack of consensus regarding the management of necrobiotic xanthogranuloma.
Anne-Sophie Smilga +3 more
doaj +1 more source
The authors report a case of malignant histiocytosis, with sub acute evolution and fatal outcome in a 36 year old male, presenting with fever, hemoptysis, splenomegaly, parietal mass, anemia and bilateral pulmonary nodules.
M João Neto +4 more
doaj +1 more source
Benign TdT-positive cells in pediatric and adult lymph nodes: a potential diagnostic pitfall [PDF]
Benign TdT-positive cells have been documented in a variety of non-hematopoietic tissues. Scant data are however available on their presence in non-neoplastic lymph nodes.
AGOSTINELLI, CLAUDIO +8 more
core +1 more source
A case of Langerhans cell histiocytosis mimicking child abuse
Langerhans cell histiocytosis is a rare non-malignant disease with clinical heterogeneity. The disease may present with various clinical findings and may imitate many other conditions.
Şakire Başer +9 more
doaj +1 more source
Langerhans Cell Histiocytosis Presenting as Anterior Neck Mass in a Child:
Thyroid involvement in Langerhans Cell Histiocytosis (LCH) is rare. We report a 10-year-old Filipino male who presented with a rapidly enlarging goiter.
Kristine Mae Betansos +5 more
doaj +1 more source
A rare cause of recurrent spontaneous pneumothorax: Birt-hogg-dube syndrome [PDF]
Birt-Hogg-Dube (BHD) syndrome is an unusual disorder characterized by the triad of cutaneous lesions, renal tumors and lung cysts. In cases with BHD syndrome, the frequency of recurrent pneumothorax is increased due to presence of multiple lung cysts. It
Demirci, M. +3 more
core +1 more source
A Case of Pulmonary Adenocarcinoma Presenting with Diffuse Cystic Lesions
The main causes of diffuse cystic lung diseases include lymphangioleiomyomatosis, pulmonary Langerhans cell histiocytosis, Birt-Hogg-Dubé syndrome, lymphoid interstitial pneumonia, light chain deposition disease, Pneumocystis jirovecii pneumonia ...
Benjamin Adrian +6 more
doaj +1 more source
Cutaneous and Nodal Histiocytic Sarcoma: A Series of Five Cases [PDF]
Histiocytic Sarcoma (HS) is an extremely rare haematolymphoid neoplasm that exhibits morphological and immunophenotypic features indicative of histiocytic differentiation.
Geeta Yadav +4 more
doaj +1 more source
Langerhans-Cell Histiocytoses - Epidemiology, Classification, Clinical Features, Diagnosis, Complications, Treatment and Prognosis [PDF]
Histiocytoses comprise a group of diverse diseases of unknown etiology with various clinical presentation and evolution. The underlying pathology is characterised by accumulation and infiltration of variable numbers of cells of the monocyte-macrophage ...
Vera Papochieva +3 more
doaj +3 more sources

