Results 231 to 240 of about 35,038 (256)
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American Heart Journal, 1953
Abstract A case of Marfan's syndrome exhibiting medial degeneration and aneurysmal formation with incomplete rupture of the pulmonary artery is reported with a review of the literature.
M, ANDERSON, H R, PRATT-THOMAS
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Abstract A case of Marfan's syndrome exhibiting medial degeneration and aneurysmal formation with incomplete rupture of the pulmonary artery is reported with a review of the literature.
M, ANDERSON, H R, PRATT-THOMAS
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Marfan's syndrome or the Marfan syndrome
International Journal of Cardiology, 1987The eponym of the well-characterised clinical syndrome has peculiarly been accepted both as Marfan’s syndrome and as the Marfan syndrome. Amongst the five major textbooks of internal medicine and cardiology. two have used Marfan’s syndrome (I.21 and three the Marfan syndrome [3-51. Thirty years ago McKusick wrote “Marfan’s Syndrome or better the Marfan
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Critical Care Nurse, 1991
Although Marfan's syndrome is not a frequent occurrence in critical care, serious cardiovascular problems can exist, requiring intensive care. This article has identified the manifestations in those coping with Marfan's syndrome. Critical care nurses need to be aware of the clinical presentation and pathophysiology of the problem to understand the ...
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Although Marfan's syndrome is not a frequent occurrence in critical care, serious cardiovascular problems can exist, requiring intensive care. This article has identified the manifestations in those coping with Marfan's syndrome. Critical care nurses need to be aware of the clinical presentation and pathophysiology of the problem to understand the ...
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Cardiomyopathy in Marfan Syndrome
The Thoracic and Cardiovascular Surgeon, 2014This report aims to evaluate the existence of primary and secondary cardiomyopathy in patients with Marfan syndrome (MFS) who underwent surgical management for primary cardiovascular sequelae of this genetic disorder. Likewise, we aim to determine whether the myocardium in MFS is susceptible to ischaemia independent of myocardial protection used during
Roland, Hetzer +2 more
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Annual Review of Medicine, 2008
Marfan syndrome is a common inherited disorder of connective tissue caused by deficiency of the matrix protein fibrillin-1. Effective surgical therapy for the most life-threatening manifestation, aortic root aneurysm, has led to a nearly normal lifespan for affected individuals who are appropriately recognized and treated.
Daniel P, Judge, Harry C, Dietz
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Marfan syndrome is a common inherited disorder of connective tissue caused by deficiency of the matrix protein fibrillin-1. Effective surgical therapy for the most life-threatening manifestation, aortic root aneurysm, has led to a nearly normal lifespan for affected individuals who are appropriately recognized and treated.
Daniel P, Judge, Harry C, Dietz
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Annual Review of Medicine, 2000
▪ Abstract The Marfan syndrome (MFS), initially described just over 100 years ago, was among the first conditions classified as a heritable disorder of connective tissue. MFS lies at one end of a phenotypic continuum, with people in the general population who have one or another of the features of MFS at the other end, and those with a variety of ...
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▪ Abstract The Marfan syndrome (MFS), initially described just over 100 years ago, was among the first conditions classified as a heritable disorder of connective tissue. MFS lies at one end of a phenotypic continuum, with people in the general population who have one or another of the features of MFS at the other end, and those with a variety of ...
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Hospital Medicine, 2001
Marfan's syndrome is an inherited disorder of connective tissue, in which the most pronounced abnormalities occur in the musculoskeletal, cardiovascular and ocular systems. Aortic dilatation and dissection are the major causes of morbidity and mortality.
E H, Aburawi, J, O'Sullivan, A, Hasan
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Marfan's syndrome is an inherited disorder of connective tissue, in which the most pronounced abnormalities occur in the musculoskeletal, cardiovascular and ocular systems. Aortic dilatation and dissection are the major causes of morbidity and mortality.
E H, Aburawi, J, O'Sullivan, A, Hasan
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Progress in Cardiovascular Diseases, 1973
I N 1896, M A R F A N ~ R E P O R T E D a skeletal anomaly in a 5-yr-old-girl, characterized by unusually long, slender extremities, and suggested the name "dolichostenomelie" (i.e., long, thin extremities) to describe the condition. Although he described the elongation of the fingers and toes, it remained for Achard 2 6 yr later to suggest the term ...
A E, Hirst, I, Gore
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I N 1896, M A R F A N ~ R E P O R T E D a skeletal anomaly in a 5-yr-old-girl, characterized by unusually long, slender extremities, and suggested the name "dolichostenomelie" (i.e., long, thin extremities) to describe the condition. Although he described the elongation of the fingers and toes, it remained for Achard 2 6 yr later to suggest the term ...
A E, Hirst, I, Gore
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Echocardiography in Marfan's Syndrome
Chest, 1976Echocardiographic examinations were performed in 26 patients with clinical evidence of Marfan's syndrome. Twelve patients were demonstrated to have isolated dysfunction of the mitral valvular apparatus of varying severity. Four patients demonstrated involvement of the aortic root as well as mitral valvular abnormalities, and six patients had problems ...
R D, Spangler +4 more
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American Journal of Diseases of Children, 1967
DIAGNOSIS of Marfan's syndrome may come about through recognition of a single finding in the patient which up to that time has not been appreciated as part of the total symptom complex. Diagnosis of Marfan's syndrome is facilitated when familial occurrence, in addition to positive physical findings, is known. Such a situation is illustrated by the case
F J, Heldrich, C E, Wright
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DIAGNOSIS of Marfan's syndrome may come about through recognition of a single finding in the patient which up to that time has not been appreciated as part of the total symptom complex. Diagnosis of Marfan's syndrome is facilitated when familial occurrence, in addition to positive physical findings, is known. Such a situation is illustrated by the case
F J, Heldrich, C E, Wright
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