Results 281 to 290 of about 2,218,154 (303)
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Critical Care Nurse, 1991
Although Marfan's syndrome is not a frequent occurrence in critical care, serious cardiovascular problems can exist, requiring intensive care. This article has identified the manifestations in those coping with Marfan's syndrome. Critical care nurses need to be aware of the clinical presentation and pathophysiology of the problem to understand the ...
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Although Marfan's syndrome is not a frequent occurrence in critical care, serious cardiovascular problems can exist, requiring intensive care. This article has identified the manifestations in those coping with Marfan's syndrome. Critical care nurses need to be aware of the clinical presentation and pathophysiology of the problem to understand the ...
openaire +3 more sources
European Heart Journal, 2016
AIMS To determine the efficacy of losartan vs. atenolol in aortic dilation progression in Marfan syndrome (MFS) patients. METHODS AND RESULTS A phase IIIb, randomized, parallel, double-blind study was conducted in 140 MFS patients, age range: 5-60 ...
A. Forteza +12 more
semanticscholar +1 more source
AIMS To determine the efficacy of losartan vs. atenolol in aortic dilation progression in Marfan syndrome (MFS) patients. METHODS AND RESULTS A phase IIIb, randomized, parallel, double-blind study was conducted in 140 MFS patients, age range: 5-60 ...
A. Forteza +12 more
semanticscholar +1 more source
Cardiomyopathy in Marfan Syndrome
The Thoracic and Cardiovascular Surgeon, 2014This report aims to evaluate the existence of primary and secondary cardiomyopathy in patients with Marfan syndrome (MFS) who underwent surgical management for primary cardiovascular sequelae of this genetic disorder. Likewise, we aim to determine whether the myocardium in MFS is susceptible to ischaemia independent of myocardial protection used during
P. Gehle, EM Delmo Walter, Roland Hetzer
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2006
Abstract Marfan syndrome is the most common inherited multisystem disorder of connective tissue. This autosomal dominant condition, first described by Antoine Marfan in 1896, has a reported incidence of 2 to 3 per 10,000 persons, and it has no particular sex, racial, or ethnic predilection. Early identification and appropriate management
Naser Ammash, Heidi Connolly
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Abstract Marfan syndrome is the most common inherited multisystem disorder of connective tissue. This autosomal dominant condition, first described by Antoine Marfan in 1896, has a reported incidence of 2 to 3 per 10,000 persons, and it has no particular sex, racial, or ethnic predilection. Early identification and appropriate management
Naser Ammash, Heidi Connolly
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Marfan Syndrome: A Clinical Update.
Journal of the American Academy of Orthopaedic Surgeons, 2017Marfan syndrome is a connective tissue disorder that can affect many organ systems. Affected patients present with orthopaedic manifestations of the syndrome during all phases of life.
A. Bitterman, P. Sponseller
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American Journal of Medical Genetics, 1988
AbstractWe describe a girl with Marfan syndrome in whom the clinical expression of the disease was much more evident on the left side of the body.
BURGIO, GIUSEPPE ROBERTO +5 more
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AbstractWe describe a girl with Marfan syndrome in whom the clinical expression of the disease was much more evident on the left side of the body.
BURGIO, GIUSEPPE ROBERTO +5 more
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Annual Review of Medicine, 2008
Marfan syndrome is a common inherited disorder of connective tissue caused by deficiency of the matrix protein fibrillin-1. Effective surgical therapy for the most life-threatening manifestation, aortic root aneurysm, has led to a nearly normal lifespan for affected individuals who are appropriately recognized and treated.
Daniel P. Judge, Harry C. Dietz
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Marfan syndrome is a common inherited disorder of connective tissue caused by deficiency of the matrix protein fibrillin-1. Effective surgical therapy for the most life-threatening manifestation, aortic root aneurysm, has led to a nearly normal lifespan for affected individuals who are appropriately recognized and treated.
Daniel P. Judge, Harry C. Dietz
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Dimensions of Critical Care Nursing, 2000
Cardiac complications of Marfan syndrome can be fatal. This article reviews the assessment of a patient with this hereditary disorder, complications and their treatment, and nursing care.
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Cardiac complications of Marfan syndrome can be fatal. This article reviews the assessment of a patient with this hereditary disorder, complications and their treatment, and nursing care.
openaire +3 more sources