Results 81 to 90 of about 19,820 (226)
The FEBS Journal, EarlyView.The extracellular matrix (ECM) is a dynamic scaffold that orchestrates tissue architecture and cellular communication. A critical but underexplored interplay between proteases and cluster of differentiation molecules (CD) governs ECM turnover and directs cell fate.
David Jurnečka +3 more
wiley +1 more source
Saudi Journal of Anaesthesia, 2013 Due to high mortality associated with aortic dissection, anesthetic management of patients with Marfan syndrome with severe aortic root dilation is a challenging situation.
Tanmoy Ghatak +2 more
doaj +1 more source
Marfan syndrome: An eyesight of syndrome
Meta Gene, 2014 Marfan syndrome (MFS), a relatively common autosomal dominant hereditary disorder of connective tissue with prominent manifestations in the skeletal, ocular, and cardiovascular systems, is caused by mutations in the glycoprotein gene fibrillin-1 (FBN1).
Kumar, Ashok, Agarwal, Sarita
openaire +2 more sources
Multiple External Invasive Root Resorption and Calcification in Systemic Sclerosis—Case Report
International Endodontic Journal, EarlyView.ABSTRACT Aim There are few reports in the literature of multiple external invasive root resorption (EIRR) lesions in patients with systemic sclerosis (SSc), and an association between root resorption and SSc is not well established. We report the only case that comprehensively illustrates—with the combination of histopathology, cone beam computed ...
Jee‐Yun Leung +3 more
wiley +1 more source
Pediatrics and Neonatology, 2018 Neonatal Marfan syndrome, in contrast to classical Marfan syndrome, is characterized by rapidly progressive multi-valvular cardiac disease and death from congestive heart failure, typically within the first year of life.
Lu-Hang Liu +3 more
doaj +1 more source
Orthopaedic Surgery, EarlyView.Generalized joint hypermobility in adolescent idiopathic scoliosis is linked to greater spinal flexibility and increased thoracic kyphosis, but also elevates the risk of surgical complications, despite no significant differences in patient‐reported outcomes.
Di Liu +5 more
wiley +1 more source
Does altered aortic flow in marfan syndrome relate to aortic root dilatation?
, 2017 PurposeTo examine possible hemodynamic alterations in adolescent to adult Marfan syndrome (MFS) patients with aortic root dilatation. ;Materials and MethodsFour-dimensional flow MRI was performed in 20 MFS patients and 12 age-matched normal subjects with
曾文毅 +1 more
core +1 more source
THE CONDITION OF DISTAL AORTA AFTER PROXIMAL RECONSTRUCTION FOR DISSECTION IN MARFAN SYNDROME
Российский кардиологический журнал, 2016 Marfan syndrome is a disease associated with high prevalence of aorta-related morbidity and mortality. Dissections and ruptures of thoracal aorta (ThAo) lead to decreased life duration in persons with Marfan syndrome with mediana at 30 year-old.Aim.
A. M. Chernyavskiy +4 more
doaj +1 more source
Carotid artery dissection linked to intermittent apnoeic swimming: A case–control study
Experimental Physiology, EarlyView.Abstract Internal carotid artery (ICA) dissection is a rare and potentially devastating cause of cerebral ischaemia, initiated by an intimal tear or rupture of the vasa vasorum, that can lead to an intraluminal thrombus, vascular stenosis, occlusion, or dissecting aneurysm formation.
Damian M. Bailey +14 more
wiley +1 more source
Marfan syndrome: current perspectives
, 2016 Guglielmina Pepe,1,2 Betti Giusti,1,2 Elena Sticchi,1,2 Rosanna Abbate,1,2 Gian Franco Gensini,1–3 Stefano Nistri2,4 1Department of Experimental and Clinical Medicine, Section of Critical Medical Care and Medical Specialities, DENOTHE Center ...
Giusti B +5 more
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