Results 21 to 30 of about 1,078 (166)

Intraocular Medulloepithelioma

Archives of Pathology & Laboratory Medicine, 2012
Intraocular medulloepithelioma is a congenital tumor of the ciliary epithelium that typically presents during the first decade of life. The histologic diagnosis is based on characteristic ribbons of pseudostratified neuroepithelium admixed with loose mesenchymal tissue rich in hyaluronic acid, vaguely resembling developing retina and vitreous.
Timothy, Saunders, Curtis E, Margo
openaire   +2 more sources

Successful treatment of metastatic congenital intraocular medulloepithelioma with neoadjuvant chemotherapy, enucleation and superficial parotidectomy

American Journal of Ophthalmology Case Reports, 2018
Purpose: To report a case of metastatic intraocular medulloepithelioma successfully treated with neoadjuvant chemotherapy, superficial parotidectomy, and enucleation.
Justin B. Hellman, George J. Harocopos, Lily Koo Lin   +2 more
doaj   +1 more source

Expanding the Molecular Data of <i>DICER1</i>-Related Tumor Predisposition: Novel Germline Variants in an Argentine Pediatric Cohort. [PDF]

Hum Mutat
Background/Objective DICER1‐related tumor predisposition is a rare hereditary tumor predisposition disorder characterized by autosomal dominant inheritance, reduced penetrance, and variable expressivity. This study is aimed at describing the clinical and molecular spectrum of DICER1‐related tumor predisposition in an Argentine pediatric cohort.
Trobo S, Garrido NP, Ramírez P, Tesan F, Vaiani E, Dujovne N, Gazek N, Martí JL, Lavia M, Felizzia G, Pringles V, Agotegaray M, Saraco N, Ciaccio M, Belgorosky A, Marino R.   +15 more
europepmc   +2 more sources

Atypical clinical presentation and long-term survival in a patient with optic nerve medulloepithelioma: a case report

Journal of Medical Case Reports, 2012
Introduction Medulloepithelioma is a rare congenital tumor of the primitive medullary neuroepithelium. A significant proportion of patients with medulloepithelioma arising from the optic nerve die from intracranial spread or cerebral metastasis.
Pastora-Salvador Natalia, Abelairas-Gómez José, Peralta-Calvo Jesús, García-Fernández Eugenia, Morales-Bastos Carmen, Asencio-Durán Mónica, Carceller-Benito Fernando   +6 more
doaj   +1 more source

A Case Report of Management of Medulloepithelioma of the Ciliary Body and Iris without Recurrence over an Observation Period of Twenty Years

Case Reports in Ophthalmological Medicine, 2023
Intraocular medulloepithelioma is a rare embryonal tumor that is believed to arise from the epithelium of the medullary tube. We report a 37-year-old female with medulloepithelioma presented at the age of 17 with a one-month history of left-sided visual ...
N. Eide, J. Navaratnam, P. Jebsen
doaj   +1 more source

Successful treatment of ciliary body medulloepithelioma with intraocular melphalan chemotherapy: a case report

BMC Ophthalmology, 2020
Background Intraocular medulloepithelioma is commonly treated with primary enucleation. Conservative treatment options include brachytherapy, local resection and/or cryotherapy in selected cases.
Christina Stathopoulos, Marie-Claire Gaillard, Julie Schneider, Francis L. Munier   +3 more
doaj   +1 more source

Peripheral Medulloepithelioma: A Rare Entity to Know

Case Reports in Oncological Medicine, 2020
According to the World Health Organization, medulloepithelioma belongs to the embryonal neoplasm entity. It is a very rare, highly malignant tumor typically affecting infants and young children.
W. Matrane, S. Cherkaoui, M. Regragui, N. Bennani Guebessi, M. Karkouri, S. Salam, A. Madani, A. Quessar, N. Khoubila   +8 more
doaj   +1 more source

Presacral medulloepithelioma with peritoneal carcinomatosis in an 11-year-old boy: An extremely rare association

Radiology Case Reports, 2021
Medulloepithelioma is a rare and highly malignant tumor of infancy and early childhood, and classified as a primitive neuroectodermal tumor. Considering that most cases occur in the central nervous system, development in atypical sites associated with ...
Gabriel Soares Mendonça, MD, Camilla Burla Artiles, MD, Glícia Campanharo Malheiros, MD, Viviane Brandão Amorim, MD, PhD   +3 more
doaj   +1 more source

A case of metastatic non-teratoid ocular medulloepithelioma in an adult horse

Brazilian Journal of Veterinary Pathology, 2021
This case reports an eight-years-old horse that presented a unilateral tumor in the left ocular orbital region diagnosed on the basis of clinical signs, gross anatomopathological and histopathological investigations.
Daniel Lúcio do Nascimento, Gabriel Domingos Carvalho, Idelvânia dos Anjos Nonato, Breno Souza Salgado   +3 more
doaj   +1 more source

INTRAOCULAR MALIGNANT TERATOID MEDULLOEPITHELIOMA

Journal of Nepal Medical Association, 2003
Malignant teratoid medulloepithelioma is an uncommon unilateral intraocular tumor, occuring typically in children. This report concerns a 4-year-old boy, who presented with loss of vision, pain and proptosis of the left eye and showed mass in between ...
Ram Chandra Adhikari, R Sainju, G Sayami, S Dali, H G Shrestha, R B Basnet, J S Pandey   +6 more
doaj   +1 more source