Results 101 to 110 of about 63,395 (317)

Unraveling 4‐Phenylbutyrate's Therapeutic Role in SLC6A1 Disorders: Pharmacochaperoning Over HDAC Inhibition

open access: yesAnnals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective Variants in SLC6A1, encoding the GABA transporter 1 (GAT‐1), cause epilepsy, autism spectrum disorder, and developmental delay via loss of GABA uptake, impaired trafficking, and ER retention. We previously found that 4‐Phenylbutyrate (PBA), an FDA‐approved drug, restores GABA uptake and reduces seizures in SLC6A1‐related disorders ...
Melissa B. DeLeeuw   +5 more
wiley   +1 more source

Micro CHP con motores Stirling

open access: yes, 2017
Situación actual dela legislación y la tecnología de micro CHP con especial enfoque en la utilización de motores stirling.Universidad de Málaga.
Aranceta Aguirre, Francisco Javier
core  

Avaliação dos ensaios de descargas parciais e de rotor bloqueado como formas de detecção de defeitos de fabricação em estatores de motores de indução monofásicos [PDF]

open access: yes, 2013
Dissertação (mestrado) - Universidade Federal de Santa Catarina, Centro Tecnológico, Programa de Pós-Graduação em Engenharia Mecânica, Florianópolis, 2013.Como parte da garantia da qualidade na produção de estatores de motores de indução monofásicos, são
Cristancho Caviativa, Jorge Alejandro
core  

Peripheral Neutrophil Activation and Extracellular Trap Formation in Amyotrophic Lateral Sclerosis

open access: yesAnnals of Clinical and Translational Neurology, EarlyView.
Markers of neutrophil activation are increased in plasma during ALS, and markers of NET formation associate with ALS survival. ABSTRACT Objectives Peripheral neutrophil levels in amyotrophic lateral sclerosis (ALS) inversely correlate with survival, suggesting a role for neutrophils in disease progression.
Lillia A. Baird   +9 more
wiley   +1 more source

Autori-LABINF - MOTORES - Letter - LABMCI

open access: yes, 2017
Autori-LABINF - MOTORES - Letter ...
LRCancino
core  

Sílabo de Motores eléctricos [PDF]

open access: yes, 2022
La asignatura corresponde al área de estudios de especialidad, es de naturaleza teórico-práctica. Tiene como propósito desarrollar en el estudiante la capacidad de seleccionar un motor eléctrico adecuado que cumpla con los requerimientos de diseño de ...
Universidad Continental
core  

Sex‐Stratified Association of Regional Dopamine Transporter Binding With Disease Progression in Amyotrophic Lateral Sclerosis

open access: yesAnnals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective To clarify the clinical relevance of dopamine transporter single‐photon emission computed tomography (DAT‐SPECT) abnormalities in amyotrophic lateral sclerosis (ALS), with a prespecified focus on sex‐stratified associations with disease progression and short‐term prognosis.
Tomoya Kawazoe   +7 more
wiley   +1 more source

Desarrollo de un modelo para el dimensionamiento de mezcladores aire-gas natural para motores

open access: yesRevista Facultad de Ingeniería Universidad de Antioquia, 2002
El artículo presenta un método para el diseño de mezcladores aire-gas natural de venturi fijo o variable en motores de aspiración natural o turboalimentados, en el cual se utiliza el modelo de flujo incompresible en estado estable unidimensional.
John R. Agudelo, Ricardo Mejía
doaj   +1 more source

Introducción a los motores de gasolina

open access: yes, 1992
Presenta las clases de los motores de gasolina existentes y las diferencias de los motores de gasolina con las demás máquinas térmicas.It presents the classes of the existing gasoline engines and the differences of the gasoline engines with the other ...

core  

Onasemnogene Abeparvovec in Patients With SMA: Interim Results of the RESTORE Registry in Japan

open access: yesAnnals of Clinical and Translational Neurology, EarlyView.
ABSTRACT Objective There are limited real‐world data regarding the safety and effectiveness of onasemnogene abeparvovec (OA; Zolgensma) infusion, a one‐time gene replacement therapy, for Japanese patients with spinal muscular atrophy (SMA). We aimed to improve understanding of the real‐world outcomes for OA in Japan.
Kayoko Saito   +8 more
wiley   +1 more source

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