Results 41 to 50 of about 1,257,065 (134)

Mounier-Kuhn syndrome: Case report and literature review [PDF]

, 2022
El síndrome de Mounier-Kuhn o traqueobroncomegalia es una condición rara caracterizada por dilatación de la tráquea y del árbol bronquial, la cual se produce por la reducción y atrofia de las fibras elásticas de la tráquea y los bronquios, por lo que ...
Villacrés, Fabián, Díaz, Israel, Lara, Bastián, Vicentela, Andrés, González-Brevis, Pablo   +4 more
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An unusual cause of recurrent spontaneous pneumothorax: the Mounier-Kuhn syndrome [PDF]

, 2016
Balbay, Ege Gulec/0000-0002-1557-7019; Annakkaya, Ali Nihat N/0000-0002-7661-8830;WOS: 000366159400049PubMed: 26127019We present a case of 63-year-old man who was referred to the emergency department with a right-sided pneumothorax.
Safçı, Sinem, Balbay, Ege Güleç, Ünlü, Elif Nisa, Annakkaya, Ali Nihat, Aydın, Leyla Yılmaz, Boran, Mertay, Güçlü, Derya   +6 more
core   +1 more source

Mounier-Kuhn syndrome or congenital tracheobronchomegaly: A literature review [PDF]

, 2013
SummaryMounier-Kuhn syndrome or congenital tracheobronchomegaly is a chronic airway condition which for currently unknown reasons mostly affects males.
Buls, Atis, Krustins, Eduards, Kravale, Zaiga   +2 more
core   +1 more source

A Case of Tracheo-Bronchomegaly Section in a Young Male [PDF]

Journal of Clinical and Diagnostic Research, 2020
Tracheobronchomegaly (TBM) or Mounier-Kuhn syndrome is a disorder characterised by dilatation of trachea and major bronchi with tracheal diverticula leading to bronchiectasis as a complication.
Priti Meshram, Sanchit Mohan, Vishwanath Pujari, Rohit Hegde   +3 more
doaj   +1 more source

EHA2021 Virtual Congress Abstract Book

, 2021
HemaSphere, Volume 5, Issue S2, June 2021.
wiley   +1 more source

Tracheomalacia Treatment Using a Large‐Diameter, Custom‐Made Airway Stent in a Case with Mounier‐Kuhn Syndrome

Case Reports in Pulmonology, Volume 2014, Issue 1, 2014., 2014
Mounier‐Kuhn Syndrome (MKS) is a rare congenital disease that presents with abnormal enlargement in the central airways. In MKS, tracheomegaly is accompanied by difficulty in expelling recurrent lung infections and bronchiectasia. We presented a patient with MKS where commercially made stents were inadequate for stabilization and a custom‐made, self ...
Cengiz Özdemir, Sinem Nedime Sökücü, Levent Karasulu, Sedat Altın, Levent Dalar, Akif Turna   +5 more
wiley   +1 more source

Mounier Kuhn syndrome presenting with recurrent atelectasis

, 2017
Objective and importance Mounier Kuhn syndrome is usually diagnosed in adulthood, and only a few cases have been described in childhood. Clinical presentation We present the case of a seven-year-old boy suffering from recurrent pneumonia and atelectasis.
Hanssens, Laurence, Bodart, Eddy, Lefevre, Nicolas, Laurence Hanssens, Eddy Bodart, Quentin, Christine, Christine Quentin, Nicolas Lefevre   +7 more
core   +1 more source

Mounier-Kuhn syndrome: a rare entity of bronchiectasis [PDF]

, 2017
Mounier-Kuhn syndrome (MKS) is a rare clinical and radiologic entity characterized by pathologic dilatation of the trachea and bronchi. The etiology of this disorder is uncertain and the clinical presentation is variable. The diagnosis is usually made on
Narahari, Narendra Kumar, Nizami, Mohammed Ismail, Vujhini, Sudhir Kumar, Prasad, Boddula Rajendra   +3 more
core   +1 more source

Severe Tracheobronchomalacia after Prolonged Intubation of Multitrauma Patient

Case Reports in Surgery, Volume 2011, Issue 1, 2011., 2011
Tracheobronchomalacia is a condition with significant morbidity with many etiologies including iatrogenic ones and should be considered in critically ill ventilated trauma patients. We present a case of a multitrauma patient who had difficulty weaning from the ventilator after prolonged intubation followed by tracheostomy tube placement.
V. G. Sams, C. M. Lawson, A. B. Shibli, D. A. Taylor, P. R. Branca, K. Honma, R. Mofidi   +6 more
wiley   +1 more source

Complex Genomic Rearrangement Involving the TBX4 Promoter Manifesting With Variable Expressivity in a Five‐Generation Family

Human Mutation, Volume 2026, Issue 1, 2026.
Variants involving TBX4 are associated with ischiocoxopodopatellar syndrome with or without pulmonary arterial hypertension (ICPPS; also known as small patella syndrome), pulmonary arterial hypertension (PAH), and lethal lung developmental disorders.
Shruti A. Pande, Hiuling Chan Joiner, Przemyslaw Szafranski, Tomasz Gambin, Frank P. Edenborough, Rachael E. Thompson, Michael J. Parker, Carrie Hammond, Shahin Moledina, Justyna A. Karolak, Pawel Stankiewicz, Miklos Sahin -Toth   +11 more
wiley   +1 more source