Congenital tracheobronchomegaly (Mounier-Kuhn syndrome) in a 70-year-old nonsmoking male: A rare presentation in a low-resource setting. [PDF]
Respir Med Case RepBackground Mounier-Kuhn Syndrome (MKS), or congenital tracheobronchomegaly, is a rare disorder characterized by dilation of the trachea and main bronchi due to the atrophy of elastic and smooth muscle fibers.
Aboaziza Y +4 more
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Incidental diagnosis of Mounier-Kuhn syndrome during anesthesia: A case report. [PDF]
Medicine (Baltimore)Rationale: Patients with Mounier–Kuhn syndrome (MKS), a rare disorder characterized by tracheobronchomegaly (80 g/d, and 10-year betel quid use) was scheduled for partial glossectomy because of suspected tongue cancer recurrence.
Feng B +5 more
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Mounier-Kuhn Syndrome Flare With Pleuritic Chest Pain: A Discussion of Complications and Management. [PDF]
Case Rep PulmonolBackground Mounier‐Kuhn syndrome (MKS), or tracheobronchomegaly, is a rare disorder characterized by dilation of the trachea and main bronchi due to atrophy of elastic and smooth muscle fibers.
Maule G +5 more
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Thoracic Computed Tomography Scan and Bronchoscopy Appearance of Mounier-Kuhn Syndrome: A Case Report. [PDF]
J Investig Med High Impact Case Rep, 2020 Mounier-Kuhn syndrome (MKS) is a rare congenital disease with an autosomal recessive inheritance pattern, characterized by an enlargement of the trachea and bronchi.
Fernández-Trujillo L +4 more
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Case report: Mounier-Kuhn syndrome
Indian Journal of Radiology and Imaging, 2008 Tracheobronchomegaly or Mounier-Kuhn syndrome is a rare disorder characterized by marked dilatation of the trachea and main bronchi, bronchiectasis, and recurrent respiratory tract infections.
Satish Kachhawa +3 more
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Tracheobronchomegaly as a Cause of Bronchiectasis in an Adult
Case Reports in Pulmonology, 2016 Mounier-Kuhn syndrome (MKS) is a rare congenital anomaly characterized by dilated trachea and main bronchi due to atrophy of the elastic fibers and smooth muscle cells of the trachea and major airways. Patients of MKS can have varied presentation.
Vishnukanth Govindaraj +3 more
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Flexible bronchoscopy and mechanical ventilation in managing Mounier-Kuhn syndrome: a case report [PDF]
São Paulo Medical Journal, 2017 CONTEXT: Mounier-Kuhn syndrome is a rare congenital condition with distinct dilatation and diverticulation of the tracheal wall. The symptoms may vary and the treatment usually consists of support.
Aslihan Gürün Kaya +3 more
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Mounier-Kuhn Syndrome Mimicking Lymphangioleiomyomatosis. [PDF]
Chest, 2018 We present the case of a man with Mounier-Kuhn syndrome (MKS), or tracheobronchomegaly, who was referred to the National Institutes of Health Clinical Research Center because of a potential diagnosis of lymphangioleiomyomatosis (LAM), a rare condition in men. The patient was evaluated using ongoing protocols and provided written informed consent.
Pacheco GG +5 more
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The Egyptian Journal of Radiology and Nuclear MedicineThe Mounier–Kuhn syndrome (MKS) is a rare chronic respiratory disease, first described in 1932 by Pierre-Louis Mounier–Kuhn, of unknown etiology. It is characterized by marked dilation of the trachea and main bronchi. Anatomically, MKS is classified into
Adriano Costigliola +5 more
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Beyond recurrent infections: a rare case of Mounier-Kuhn syndrome with tracheobronchial dilatation
The Egyptian Journal of BronchologyMounier Kuhn syndrome (MKS), also known as tracheobronchomegaly (TBM), is a very rare and chronic airway disease characterized by marked dilatation of the trachea and central bronchi. Currently, there are few epidemiological studies on MKS, and most data
Mohsen Sadeghi +3 more
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