Results 51 to 60 of about 1,257,115 (148)

Mounier Kuhn syndrome presenting with recurrent atelectasis

, 2017
Objective and importance Mounier Kuhn syndrome is usually diagnosed in adulthood, and only a few cases have been described in childhood. Clinical presentation We present the case of a seven-year-old boy suffering from recurrent pneumonia and atelectasis.
Hanssens, Laurence, Bodart, Eddy, Lefevre, Nicolas, Laurence Hanssens, Eddy Bodart, Quentin, Christine, Christine Quentin, Nicolas Lefevre   +7 more
core   +1 more source

Mounier-Kuhn syndrome: a rare entity of bronchiectasis [PDF]

, 2017
Mounier-Kuhn syndrome (MKS) is a rare clinical and radiologic entity characterized by pathologic dilatation of the trachea and bronchi. The etiology of this disorder is uncertain and the clinical presentation is variable. The diagnosis is usually made on
Narahari, Narendra Kumar, Nizami, Mohammed Ismail, Vujhini, Sudhir Kumar, Prasad, Boddula Rajendra   +3 more
core   +1 more source

Severe Tracheobronchomalacia after Prolonged Intubation of Multitrauma Patient

Case Reports in Surgery, Volume 2011, Issue 1, 2011., 2011
Tracheobronchomalacia is a condition with significant morbidity with many etiologies including iatrogenic ones and should be considered in critically ill ventilated trauma patients. We present a case of a multitrauma patient who had difficulty weaning from the ventilator after prolonged intubation followed by tracheostomy tube placement.
V. G. Sams, C. M. Lawson, A. B. Shibli, D. A. Taylor, P. R. Branca, K. Honma, R. Mofidi   +6 more
wiley   +1 more source

Complex Genomic Rearrangement Involving the TBX4 Promoter Manifesting With Variable Expressivity in a Five‐Generation Family

Human Mutation, Volume 2026, Issue 1, 2026.
Variants involving TBX4 are associated with ischiocoxopodopatellar syndrome with or without pulmonary arterial hypertension (ICPPS; also known as small patella syndrome), pulmonary arterial hypertension (PAH), and lethal lung developmental disorders.
Shruti A. Pande, Hiuling Chan Joiner, Przemyslaw Szafranski, Tomasz Gambin, Frank P. Edenborough, Rachael E. Thompson, Michael J. Parker, Carrie Hammond, Shahin Moledina, Justyna A. Karolak, Pawel Stankiewicz, Miklos Sahin -Toth   +11 more
wiley   +1 more source

Carcinoma pleomórfico do pulmão em doente com síndroma de Mounier-Kuhn

Revista Portuguesa de Pneumologia, 2006
Resumo: O carcinoma pleomórfico do pulmão (CPP) é um tumor maligno raro e de prognóstico reservado. Está inserido no grupo dos carcinomas pulmonares pouco diferenciados não pequenas células, exibe componente sarcomatoso ou sarcoma like (células ...
Daniela Ferreira, Ana Barroso, Ana Oliveira, Rosete Nogueira, Antónia Furtado, Bárbara Parente   +5 more
doaj   +1 more source

Anesthetic management of a patient with Mounier-Kuhn syndrome undergoing off-pump coronary artery bypass graft surgery -A case report- [PDF]

Korean Journal of Anesthesiology, 2011
Mounier-Kuhn-syndrome patients have markedly dilated trachea and main bronchi due to an atrophy or absence of elastic fibers and thinning of smooth muscle layers in the tracheobronchial tree.
Jeong Jin Min, Jung-Man Lee, Jun Hyun Kim, Deok Man Hong, Yunseok Jeon, Jae-Hyon Bahk   +5 more
doaj   +1 more source

Mounier-Kuhn syndrome in an older patient [PDF]

Age and Ageing, 2007
Respiratory problems in older adults are frequently labelled as being due to chronic obstructive airways disease (COAD). However where the presentation may be suggestive of another pathology due to the clinical history or type of pathogen isolated from the sputum, then consideration should be given to appropriate imaging. We describe a case of an older
Marianne, Falconer, D Rónán, Collins, John, Feeney, William C, Torreggiani   +3 more
openaire   +2 more sources

Tracheobronchomegaly: The Mounier-Kuhn Syndrome [PDF]

, 2018
A case of tracheobronchomegaly (Mounier-Kuhn syndrome) is reported. The striking features are gross dilatation of the trachea and both main bronchi with associated chronic pulmonary disease.
Bass, E.M., Bass, EM
core  

A Rare Diagnosis: A Case of Mounier-Kuhn Syndrome [PDF]

Journal of Mazandaran University of Medical Sciences
Mounier-Kuhn syndrome (MKS) is a rare congenital disorder characterized by dilatation of the trachea and main bronchi. It was first described by Pierre-Louis Mounier-Kuhn in 1937 in association with recurrent respiratory infections and was later ...
Farhad Mohammadnejad, Samira Golchinmehr
doaj  

Mounier-Kuhn syndrome: A case study

South African Journal of Radiology, 2002
No abstract available.
M. J. Trollip
doaj   +1 more source