Results 51 to 60 of about 8,071 (187)

Quantum Compression of Tensor Network States [PDF]

, 2019
We design quantum compression algorithms for parametric families of tensor network states. We first establish an upper bound on the amount of memory needed to store an arbitrary state from a given state family.
Bai, Ge, Chiribella, Giulio, Yang, Yuxiang   +2 more
core   +2 more sources

Immune-Mediated Inflammation May Contribute to the Pathogenesis of Cardiovascular Disease in Mucopolysaccharidosis Type I. [PDF]

, 2016
BackgroundCardiovascular disease, a progressive manifestation of α-L-iduronidase deficiency or mucopolysaccharidosis type I, continues in patients both untreated and treated with hematopoietic stem cell transplantation or intravenous enzyme replacement ...
Dickson, Patricia I, Ellinwood, N Matthew, Esko, Jeffrey D, Gordts, Philip L, Khalid, Omar, Schwartz, Philip H, Vera, Moin U, Wang, Raymond Y   +7 more
core   +3 more sources

Development of MPS IVA mouse (Galnstm(hC79S·mC76S)slu) tolerant to human N-acetylgalactosamine-6-sulfate sulfatase [PDF]

Human Molecular Genetics, 2005
Mucopolysaccharidosis IVA (MPS IVA) is an autosomal recessive disease caused by N-acetylgalactosamine-6-sulfate sulfatase (GALNS) deficiency. In recent studies of enzyme replacement therapy for animal models with lysosomal storage diseases, cellular and humoral immune responses to the injected enzymes have been recognized as major impediments to ...
Shunji, Tomatsu, Monica, Gutierrez, Tatsuo, Nishioka, Masamichi, Yamada, Mana, Yamada, Yasuhiro, Tosaka, Jeffrey H, Grubb, Adriana M, Montaño, Matheus B, Vieira, Georgeta G, Trandafirescu, Olga M, Peña, Seiji, Yamaguchi, Koji O, Orii, Tadao, Orii, Akihiko, Noguchi, Leticia, Laybauer   +15 more
openaire   +2 more sources

Atmospheric Deposition of Organic Pollutants: A Comprehensive Review of Sampling and Analytical Methodologies

Analytical Science Advances, Volume 7, Issue 1, June 2026.
ABSTRACT Atmospheric deposition of organic pollutants plays a crucial role in the transport and fate of contaminants in the environment, with implications for ecosystem health and human exposure. Persistent organic pollutants (POPs), polycyclic aromatic hydrocarbons (PAHs) and microplastics are increasingly recognized as transboundary threats due to ...
Iva Smoljo, Gordana Mendaš, Gordana Pehnec   +2 more
wiley   +1 more source

Automated radiotherapy planning for volumetric modulated arc therapy in lung cancer

Journal of Applied Clinical Medical Physics, Volume 26, Issue 10, October 2025.
Abstract Background Volumetric‐modulated arc therapy (VMAT) treatment planning balances the need for adequate coverage of the planning target volume (PTV) and the sparing of organs‐at‐risk (OARs). However, this time‐consuming iterative process is influenced by the planner's experience, personal preferences, and the time devoted to create the plan. This
Johann Brand, Juliane Szkitsak, Bernd‐Niklas Axer, Lucas Pieper, Oliver J. Ott, Marlen Haderlein, Florian Putz, Rainer Fietkau, Christoph Bert, Stefan Speer   +9 more
wiley   +1 more source

Relationships among Height, Weight, Body Mass Index, and Age in Taiwanese Children with Different Types of Mucopolysaccharidoses

Diagnostics, 2019
Background: Children with mucopolysaccharidosis (MPS) generally appear unaffected at birth but may develop multiple clinical manifestations including profound growth impairment as they grow older. Each type of MPS has a variable age at onset and variable
Hsiang-Yu Lin, Chung-Lin Lee, Pao Chin Chiu, Dau-Ming Niu, Fuu-Jen Tsai, Wuh-Liang Hwu, Shio Jean Lin, Ju-Li Lin, Tung-Ming Chang, Chih-Kuang Chuang, Shuan-Pei Lin   +10 more
doaj   +1 more source

Neonatal umbilical cord blood transplantation halts skeletal disease progression in the murine model of MPS-I [PDF]

, 2017
Umbilical cord blood (UCB) is a promising source of stem cells to use in early haematopoietic stem cell transplantation (HSCT) approaches for several genetic diseases that can be diagnosed at birth.
A Oikawa, A Pievani, A Pievani, A Scaradavou, AE Willing, B Sacchetti, C Davenport, C Schulte, CM Simonaro, DC Mendez, DE Harrison, DE Harrison, DJ Rowan, DK Kim, DL Selle, DT Harris, F Gatto, F Kubaski, F Migishima, FL Wilkinson, HE Broxmeyer, J Palis, JJ Boelens, K Ohmi, K Uchida, K Uchida, KK Ballen, L Lu, LA Clarke, LA Clarke, M Aldenhoven, M Aldenhoven, M Aldenhoven, M Aldenhoven, M Beck, M Schmidt, ME Bernardo, MF Garcia-Rivera, O Levy, S Coşkun, S Garbuzova-Davis, S Jayaraman, S Tomatsu, S Tomatsu, S Tomatsu, SC Kuehn, SH Boyer, SJ Morrison, SL Staba, VK Prasad, VK Prasad, W Chuan, XY Zhong, Y Zheng, ZY Li   +54 more
core   +2 more sources

Enzyme Replacement Therapy With Elosulfase Alfa Decreases Storage of Glycosaminoglycan in White Blood Cells of Patients With Morquio A Syndrome

Journal of Inborn Errors of Metabolism and Screening, 2015
Mucopolysaccharidosis IVA (MPS IVA; Morquio A syndrome) is a lysosomal storage disorder caused by a deficient N-acetylgalactosamine-6-sulfate sulfatase activity, leading to cellular storage of undegraded keratan sulfate.
Guilherme Baldo PhD, Fabiano Poswar MD, Andressa Federhen MSc, Camila Bittar MD, Rejane Gus PhD, Fernanda Bender MSc, Roberto Giugliani MD, PhD   +6 more
doaj   +1 more source

MRI morphometric characterisation of the paediatric cervical spine and spinal cord in children with MPS IVA (Morquio‐Brailsford syndrome) [PDF]

Journal of Inherited Metabolic Disease, 2013
AbstractNearly all children with MPS IVA develop skeletal deformities affecting the spine. At the atlanto‐axial spine, odontoid hypoplasia occurs. GAG deposition around the dens, leads to peri‐odontoid infiltration. Transverse/alar ligament incompetence causes instability.
Solanki, Guirish A., Lo, William B., Hendriksz, Christian J.   +2 more
openaire   +2 more sources

Processes for Developing Plain Language Versions of Guidelines Recommendations: A Scoping Review

Journal of Evaluation in Clinical Practice, Volume 31, Issue 6, September 2025.
ABSTRACT Rationale Plain language recommendations (PLRs) offer clear and understandable statements based on trustworthy guidelines. Objective We aimed to synthesise methodological evidence for developing PLRs in the health care context. Methods We followed the JBI methodology for scoping review development and the PRISMA‐ScR guidelines for scoping ...
Alena Langaufova, Tereza Friessova, Dana Dolanova, Tereza Vrbova, Petra Burilova, Natalia Beharkova, Andrea Pokorna   +6 more
wiley   +1 more source