Results 101 to 110 of about 9,764 (249)
Case Reports in Nephrology and Dialysis, 2017 Erdheim-Chester disease (ECD) is a rare, non-Langerhans cell histiocytosis presenting most commonly with bone and central nervous system symptoms, including but not limited to bone pain and diabetes insipidus.
Farid Arman +4 more
doaj +1 more source
A Rare Case of a Systemic Non-Langerhans Histiocytosis Presenting with Diabetes Insipidus and a Tentorial Mass [PDF]
, 2015 Introduction The histiocytoses are a group of clinically diverse diseases distinguished from one another based on the specific immunophenotype of the lesional cells, implying derivation from the same precursor cell.
Barros, MS, Guilherme +5 more
core +2 more sources
Recurrent Pneumothorax Revealing Lymphangioleiomyomatosis in a Young Woman: A Case Report
Clinical Case Reports, Volume 13, Issue 12, December 2025.ABSTRACT Lymphangioleiomyomatosis (LAM) should be considered in young women presenting with recurrent pneumothorax. Early diagnosis through high‐resolution computed tomography(HRCT)and histopathological analysis is essential for timely management and improved patient outcomes.
Qihang Zhang +3 more
wiley +1 more source
BMC Pediatrics, 2019 Background Juvenile xanthogranuloma (JXG) belongs to the heterogeneous group of non-Langerhans cell histiocytosis and is caused by an accumulation and proliferation of macrophages.
Michaela Höck +6 more
doaj +1 more source
Clinical features and outcomes of non-pulmonary unifocal adult Langerhans cell histiocytosis [PDF]
, 2022 Marie Hu +16 more
openalex +1 more source
Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia
Case Reports in Hematology, 2011 Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man.
Peter G. Pavlidakey +3 more
doaj +1 more source
Flat Topped Brown Papules on a Four-Year-Old Male
Revista da Sociedade Portuguesa de Dermatologia e Venereologia, 2020 .
Francisca Alves +3 more
doaj +1 more source
Erdheim-Chester Disease: a comprehensive review of the literature [PDF]
, 2013 Erdheim-Chester Disease (ECD) is a rare form of non Langerhans' cell histiocytosis. Individuals affected by this disease are typically adults between their 5th and 7th decades of life. Males and females are almost equally affected.
Mirra Manevich-Mazor +2 more
core +1 more source
Rosai–Dorfman Disease, Presenting as a Mass in the Trachea: A Case Report
Respirology Case Reports, Volume 13, Issue 12, December 2025.We present a rare case of Rosai–Dorfman disease (RDD) confined solely to the trachea. After initial bronchoscopic resection, systemic corticosteroid therapy was initiated due to lesion progression, successfully stabilizing the disease for 4 years. ABSTRACT A 45‐year‐old woman was referred to our clinic for evaluation of a 17 mm tracheal mass detected ...
Taeho Youn +3 more
wiley +1 more source
Xanthoma Disseminatum with Tumor-Like Lesion on Face
Case Reports in Dermatological Medicine, 2014 Xanthoma disseminatum (XD) is a rare benign mucocutaneous xanthomatosis that is classified as a benign non-Langerhans cell histiocytosis. We report a 62-year-old man who presented with widespread yellow-brown papulonodular and tumoral lesions on face ...
Habib Ansarin +3 more
doaj +1 more source