Results 81 to 90 of about 9,825 (225)
Perianal Paget's Disease: A Case Report
ABSTRACT Perianal Paget's disease is rare and may be secondary to an underlying anorectal adenocarcinoma. Full‐thickness biopsy with immunohistochemistry is key to distinguish primary from secondary disease and to guide staging. Wide local excision is standard, while radiotherapy is a reasonable option when radical surgery is declined.
Daniela Lira +5 more
wiley +1 more source
Abstract Background Childhood cancer survivors (CCS) face elevated skin cancer risk, especially after radiotherapy or hematopoietic stem cell transplantation (HSCT). The authors evaluated the prevalence and predictors of sun protection, sunburn, and physician skin examination (PSE) among CCS in Switzerland.
Carina Nigg +9 more
wiley +1 more source
Erdheim-Chester Disease: a comprehensive review of the literature [PDF]
Erdheim-Chester Disease (ECD) is a rare form of non Langerhans' cell histiocytosis. Individuals affected by this disease are typically adults between their 5th and 7th decades of life. Males and females are almost equally affected.
Mirra Manevich-Mazor +2 more
core +1 more source
A 50‐year‐old man with a 12‐year history of extensive pachymeningeal thickening
Brain Pathology, EarlyView.
Alyssa M. Lee +3 more
wiley +1 more source
Colonic Malakoplakia With an Adenomatous Appearance on Magnification Endoscopy: A Case Report
ABSTRACT Malakoplakia is a rare chronic granulomatous disease associated with impaired macrophage phagocytosis of bacteria. Because colonic malakoplakia presents with varied endoscopic appearances, its characteristic features have not been clearly defined, and differentiation from colorectal neoplasms during endoscopy may be difficult. We report a case
Shima Sono +7 more
wiley +1 more source
A Rare Case of a Systemic Non-Langerhans Histiocytosis Presenting with Diabetes Insipidus and a Tentorial Mass [PDF]
Introduction The histiocytoses are a group of clinically diverse diseases distinguished from one another based on the specific immunophenotype of the lesional cells, implying derivation from the same precursor cell.
Barros, MS, Guilherme +5 more
core +2 more sources
MEK Inhibition with Trametinib in Patients with Non-Langerhans Cell Histiocytosis
Background: Activation of the MAPK pathway through BRAF mutations or other molecular alterations is a hallmark of the non-Lagerhans cell histiocytosis (non-LCH) such Erdheim-Chester disease (ECD) or Rosai-Dorfman disease (RDD). Conventional clinical molecular testing of tumor tissue fails to identify targetable molecular alteration in about one third ...
Filip Janku +5 more
openaire +1 more source
ABSTRACT Introduction Histiocytic sarcoma (HS) is a rare neoplasm derived from non‐Langerhans histiocytic cells, exceptionally arising from B‐ALL. Methods We present the case of a child with high‐risk B‐ALL with PAX5 P80R mutation. Results Despite initial remission, a chemoresistant paravertebral mass was identified as HS.
Laetitia Largeaud +12 more
wiley +1 more source
Erdheim-Chester disease (ECD) is a rare, non-Langerhans cell histiocytosis presenting most commonly with bone and central nervous system symptoms, including but not limited to bone pain and diabetes insipidus.
Farid Arman +4 more
doaj +1 more source

