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Polyneuropathy, organomegaly, endocrinopathy, M-protein and skin changes syndrome (POEMS) – case report
Синдромът на полиневропатия (ПНП), органомегалия, ендокринопатия, М-протеин и кожни промени (POEMS) е рядък паранеопластичен синдром, свързан с плазмоклетъчна дискразия. Представяме клиничен случай на POEMS със специфична подостра болезнена ПНП, загуба на тегло, диария, кожни промени, отоци, JAK2 негативна полицитемия и М-протеин.Valkova, Mirena, Tzolova, Elena, Guergueltcheva, Velina +2 moreopenaire +1 more sourceUbiquitous expression of the Pik3caH1047R mutation promotes hypoglycemia, hypoinsulinemia, and organomegaly
The FASEB Journal, 2015 K. Kinross, K. Montgomery, S. Mangiafico, Lauren M. Hare, Margarete Kleinschmidt, M. Bywater, Ingrid J. Poulton, Christina Vrahnas, H. Henneicke, J. Malaterre, P. Waring, C. Cullinane, N. Sims, G. McArthur, S. Andrikopoulos, W. Phillips +15 moresemanticscholar +1 more sourceLenalidomide as frontline therapy in polyneuropathy, organomegaly, endocrinopathy, monoclonal protein and skin changes syndrome: a retrospective case series of eight patients
Leukemia and Lymphoma, 2015 Elsa Lestang, A. Caristan, A. Néel, J. Graveleau, E. Duhamel, A. Masseau, J. Connault, H. Maisonneuve, S. le Gouill, N. Blin, C. Touzeau, P. Moreau, M. Hamidou +12 moresemanticscholar +1 more source[Recurrent febrile organomegaly].
La Revue de medecine interne, 1998 F, Lecomte, N, Cailleux, I, Marie, H, Lévesque, H, Courtois +4 moreopenaire +1 more source