Results 11 to 20 of about 2,403 (160)

Retroperitoneal Precaval Pecoma – an Incidental Finding [PDF]

Modern Medicine
PEComas are rare mesenchymal tumours of histologically and immunohistochemically distinctive perivascular epithelioid cells. Most of these tumours are benign, but in malignancies the prognosis is usually very poor.
Lucian Sorin ANDREI, Adriana Corina ANDREI, Vlad HERLEA, Florentina ALMARI, Alexandru MICU   +4 more
doaj   +3 more sources

A case of pancreatic PEComa with prominent inflammatory cell infiltration: the inflammatory subtype is a distinct histologic group of PEComa

Diagnostic Pathology
Background PEComa is a mesenchymal tumor that can occur in various organs including the uterus and soft tissues. PEComas are composed of perivascular epithelioid cells, and angiomyolipoma (AML), clear cell sugar tumor (CCST), and lymphangiomyomatosis ...
Hikaru Tsukita, Kei Koyama, Takahiro Ishinari, Ayana Takahashi, Ken Miyabe, Michinobu Umakoshi, Makoto Yoshida, Yukitsugu Kudo-Asabe, Akiko Nishida, Naohiko Otsuka, Ouki Yasui, Ikuma Kato, Noriyoshi Fukushima, Akiteru Goto   +13 more
doaj   +2 more sources

Perivascular epithelioid cell tumor (PEComa) presents an endometrial polyp pattern: Case report and literature review

Human Pathology: Case Reports, 2018
Perivascular epithelioid cell tumor (PEComa) is a rare mesenchymal tumor composed of histologically and immunohistochemically distinctive perivascular epithelioid cells [1, 2], which can arise in a wide array of anatomic locations, and is characterized ...
Xiaomei Wang, Yanbiao Fu, Baizhou Li
doaj   +2 more sources

Malignant perivascular epitheloid cell tumour (PEComa) of the lung – a rare entity

Innovative Surgical Sciences, 2017
Malignant Perivascular Epitheloid Cell Tumour (PEComa) of the lung is very rare, with only six cases reported in literature. This case presented with a large mass originating from right upper lobe of the lung with dilemma in its histopathological ...
Chakrabarti Amitabha, Bandyopadhyay Manujesh, Purkayastha Biswarup   +2 more
doaj   +3 more sources

Malignant MITF-Rearranged PEComa With Novel EEF1A1::MITF Fusion. [PDF]

Genes Chromosomes Cancer
ABSTRACT MITF‐rearranged PEComas are rare, and their relationship to MITF‐altered melanocytic tumors remains incompletely characterized. We report a malignant superficial soft tissue neoplasm of the thigh in a 45‐year‐old woman harboring a novel EEF1A1::MITF fusion. The tumor was composed of epithelioid to plump spindle cells arranged in sheets, nests,
Raney S, Karunamurthy A, Ho J, Bubar R, Mohebnasab M, Skaugen J, Elmoryah M, Nacev B, McGough R, John I.   +9 more
europepmc   +2 more sources

Perivascular epithelioid cell neoplasm (PEComa) of the urinary bladder presenting as urinary tract infection in a young woman

Urology Case Reports
PEComa is a rare mesenchymal tumor with unique features, sometimes manifesting in younger patients and can exhibit malignant transformation. We present a 24-year-old woman with urinary symptoms and hematuria.
Dana Greenberg, Yoav Avidor, Rami Mattar, Muhammad Majdoub, Alona Meir, Ronen Rub   +5 more
doaj   +2 more sources

<i>ASPSCR1: TFE3</i> Fusion-Positive Epithelioid Angiomyolipoma/PEComa Lacking Melanocytic Markers: A Case Report. [PDF]

IJU Case Rep
ABSTRACT Introduction Epithelioid angiomyolipoma is a rare perivascular epithelioid cell tumor subtype with malignant potential. Its morphology mimics renal cell carcinoma, posing diagnostic challenges. Half of these cases harbor TSC1/TSC2 alterations, and a small subset features TFE3 rearrangements, mutually exclusive of TSC mutations.
Kondo Y, Nagashima Y, Zennami K, Sato M, Sumiyoshi S, Sugimoto A, Isomura M, Takahara K, Minamiguchi S.   +8 more
europepmc   +2 more sources

Diagnosis and treatment of malignant PEComa tumours [PDF]

, 2020
PEComa to rodzina rzadkich nowotworów pochodzenia mezenchymalnego, składających się z nabłonkowatych komórek przynaczyniowych, wykazujących ekspresję markerów melanocytarnych i mioidalnych.
Rutkowski, Piotr; Klinika Nowotworów Tkanek Miękkich, Kości i Czerniaków, Narodowy Instytut Onkologii im. Marii Skłodowskiej-Curie — Państwowy Instytut Badawczy w Warszawie, Poland, Szumera-Ciećkiewicz, Anna; Zakład Patologii i Diagnostyki Laboratoryjnej, Narodowy Instytut Onkologii im. Marii Skłodowskiej-Curie — Państwowy Instytut Badawczy w Warszawie, Poland; Zakład Diagnostyki Hematologicznej, Instytut Hematologii i Transfuzjologii w Warszawie, Poland, Świtaj, Tomasz; Klinika Nowotworów Tkanek Miękkich, Kości i Czerniaków, Narodowy Instytut Onkologii im. Marii Skłodowskiej-Curie — Państwowy Instytut Badawczy w Warszawie, Poland, Sobiborowicz, Aleksandra; Klinika Nowotworów Tkanek Miękkich, Kości i Czerniaków, Narodowy Instytut Onkologii im. Marii Skłodowskiej-Curie — Państwowy Instytut Badawczy w Warszawie, Poland; Wydział Lekarski, Warszawski Uniwersytet Medyczny w Warszawie, Poland, Czarnecka, Anna M.; Klinika Nowotworów Tkanek Miękkich, Kości i Czerniaków, Narodowy Instytut Onkologii im. Marii Skłodowskiej-Curie — Państwowy Instytut Badawczy w Warszawie, Poland; Zakład Farmakologii Doświadczalnej, Instytut Medycyny Doświadczalnej i Klinicznej im. M. Mossakowskiego PAN w Warszawie, Poland   +4 more
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Extremely late-onset pulmonary metastasis from uterine PEComa [PDF]

, 2022
A 79-year-old woman underwent surgical resection of a peripheral, solitary, pulmonary lesion that was diagnosed as malignant PEComa. Her clinical history was positive for uterine leiomyosarcoma, excised 20 years before.
Ascione, Andrea, Rocca, Carlo Della, d'Amati, Giulia, d’Amati, Giulia, Martignoni, Guido, Graziano, Paolo, Della Rocca, Carlo, Pernazza, Angelina   +7 more
core   +1 more source

Primary malignant PEComa of the mandible. Report of an unusual case [PDF]

, 2021
Malignant PEComa is a rare entity that usually origins at visceral, retroperitoneal and abdominopelvic sites. In the present paper, we describe an extremely unusual manifestation of malignant PEComa involving the mandible in a 48 years-old female ...
Hernández-Vila, Cristina, Deutor-Garcia, Lourdes, Fraile-Ruiz, Lydia, Pozo Kreilinger, Jose Juan, Chamorro Santos, Clara   +4 more
core   +1 more source