Results 91 to 100 of about 167,430,042 (175)
Complete pentalogy of Cantrell associated with exencephaly: a rare case report [PDF]
Complete pentalogy of Cantrell (PC) is a rare condition with an incidence of 1 in 100000 pregnancies. The spectrum includes defects in the diaphragm, anterior abdominal wall, diaphragmatic pericardium, lower sternum and congenital cardiac anomalies.
Rajasekaran, Anandraj, Ekanath, Latha
core
Pentalogy of Cantrell; complete expression in a nine‑month‑old‑boy
Pentalogy of Cantrell is a rare congenital malformation whose exact cause is not completely understood; it is characterized by defects in the anterior abdominal and thoracic walls consisting of omphalocoele, diaphragmatic defect, ectopia cordis ...
Aliyu, Ibrahim, Mohammad, Mohammad Aminu
core +1 more source
Anaesthesia and Pentalogy of Cantrell [PDF]
pected. The ET tube was replaced but there was no improvement. Further desaturation and bradycardia ensued. Although air entry was poor bilaterally it was thought to be worse on the right. The exomphalos made assessment of the epigastrium difficult and no hepar was palpable. With further deterioration, ongoing bradycardia and absent peripheral pulses a
openaire +1 more source
Pentalogy of Cantrell with double-outlet right ventricle: a case of surgical correction
Pentalogy of Cantrell is characterised by a combination of severe defects in the middle of the chest including the sternum, diaphragm, heart, and abdominal wall. Mortality rate after cardiac surgery is usually high.
Yoshio Ootaki +2 more
core +1 more source
En 1958, Cantrell describió un síndrome caracterizado por cinco defectos que incluyen: ectopia cordis, onfalocele, disrupción del esternón distal, diafragma anterior y pericardio diafragmático.
Hernán Cortés Y +1 more
doaj
Unusual variant of Cantrell′s pentalogy?
A 12-hour-old male infant presented with prolapsed abdominal content through a defect on left side of chest wall with respiratory distress. A thorough clinical examination suggested absence of ectopia cordis, abdominal wall defect, and any bony anomaly.
Kumar, Basant +3 more
openaire +2 more sources
Pentalogy of Cantrell or Cantrell Syndrome: One in a million disease
Introduction: Pentalogy of Cantrell (PS) or Cantrell Sydrome (CS), first described by Cantrell in 1958, is a rare congenital anomaly characterized by defect in lower sternum, anterior abdominal wall defect, defect in anterior diaphragm, ectopia cordis ...
Maria-Desislava Atanasova +4 more
core +1 more source
Goltz-Gorlin syndrome is a highly variable disorder affecting many body parts of meso-ectodermal origin. Mutations in X-linked PORCN have been identified in almost all patients with a classical Goltz-Gorlin phenotype.
Jaworski, Wojciech +6 more
core +1 more source
Pentalogy of cantrell: report of a case with consanguineous parents [PDF]
Pentalogy of Cantrell is a syndrome evidencing five anomalies: a midline, upper abdominal wall abnormality; lower sternal defect; anterior diaphragmatic defect; diaphragmatic pericardial defect, and congenital abnormalities of the heart.
Pachajoa Londoño, Harry Mauricio
core +2 more sources
Pentalogy of Cantrell in a resource-limited setting: A case report
Introduction: Pentalogy of Cantrell is a rare congenital condition involving defects in the abdominal wall, sternum, diaphragm, pericardium, and heart. This report adds to the scarce literature by presenting a unique case from a resource-limited setting.
Suleiman Ayalew +5 more
doaj +1 more source

