Pentalogy of Cantrell with a double-outlet right ventricle: Prenatal Diagnosis, Delivery and Immediate Postnatal Surgical Repair / Pentalogia de Cantrell com um ventrículo direito de saída dupla: Diagnóstico Pré-Natal, Parto e Reparação Cirúrgica Pós-Natal Imediata [PDF]
A Pentalogia de Cantrell é uma doença congênita rara, havendo apenas cerca de 250 casos relatados. A síndrome consiste em uma variedade toracoabdominal de ectopia cordis, associada a cinco defeitos principais em: linha mediana anterior supraumbilical de ...
Bringel, Camilla Azevedo +5 more
core
Anaesthesia and Pentalogy of Cantrell [PDF]
pected. The ET tube was replaced but there was no improvement. Further desaturation and bradycardia ensued. Although air entry was poor bilaterally it was thought to be worse on the right. The exomphalos made assessment of the epigastrium difficult and no hepar was palpable. With further deterioration, ongoing bradycardia and absent peripheral pulses a
openaire +1 more source
partial herniation of the heart through the anterior thoracic wall, diastasis of the rectus abdominis muscles in the supraumbilical anterior abdominal wall, with insinuation and partial herniation of the liver (Figures 1 and 2), in addition to complex ...
Jonathan Guimarães Lombardi +5 more
semanticscholar +1 more source
Pentalogy of Cantrell: Complete expression with mediastinal teratoma
Pentalogy of Cantrell (POC) is a rare, and often fatal congenital disorder that is characterized by a pentad consisting of ectopia cordis, omphalocele, sternal cleft, congenital diaphragmatic hernia, and various intra-cardiac defects.
Michał Błaszczyński +7 more
doaj +1 more source
Asociación de ectopia cordis con pentalogía de Cantrell a partir de variantes en el gen ALDH1A2. [PDF]
Objetivo: Identificar la relación de variantes en el gen ALDH1A2 con la ectopia cordis descrita en los pacientes con pentalogía de Cantrell. Materiales y métodos: Según la declaración PRISMA, se realizó una búsqueda sistematizada de la literatura en ...
Jiménez-Müller, Hana +2 more
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En 1958, Cantrell describió un síndrome caracterizado por cinco defectos que incluyen: ectopia cordis, onfalocele, disrupción del esternón distal, diafragma anterior y pericardio diafragmático.
Hernán Cortés Y +1 more
doaj
DamID Profiling of CTCF and TEAD3 Binding within Chromosome 9p21 [PDF]
The progression of benign tumor growth is often restricted by oncogene-induced senescence (OIS), a state of irreversible cell cycle arrest that frequently involves upregulation of the p16INK4a tumor suppressor.
Sychla, Adam
core
Pentalogia de Cantrell: relato de caso Pentalogy of Cantrell: case report
Os autores descrevem o tratamento cirúrgico de um caso de pentalogia de Cantrell, rara anomalia congênita, caracterizada por defeitos da parede abdominal, terço inferior do esterno, diafragma, pericárdio e coração.The authors describe the surgical cure ...
Sheila Hazin +7 more
doaj
Pentalogy of cantrell: A report of three cases
Pentalogy of Cantrell is a rare upper midline syndrome that may present in association with anomalies outside the torso. The pentad - the supraumbilical body wall defect, sternal defect, deficiency of the anterior diaphragm, defect of the diaphragmatic pericardium, and the intracardiac anomalies - was first described by Cantrell et al., in 1958.
Sowande, O.A +4 more
openaire +4 more sources
Awake percutaneous tracheostomy as an alternative to open emergency tracheostomy in a threatened airway [PDF]
No ...
Hodgson, R.E., Pillay, T.K.
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