Results 31 to 40 of about 6,233 (203)

Pericarditis constrictiva calcificada: una presentación inicial infrecuente de la esclerodermia

Cirugía Cardiovascular, 2017
Resumen: Aunque la afectación pericárdica ha sido demostrada de forma habitual en autopsias de pacientes afectos de esclerodermia, esta afectación pericárdica rara vez es sintomática.
Daniel Hernández-Vaquero, Rubén Álvarez-Cabo, Rocío Díaz, Carlos Morales, Francisco Callejo, Jacobo Silva   +5 more
doaj   +1 more source

Development of a Disease Activity Index for the Assessment of VEXAS Syndrome (VEXAS‐DAI)

Arthritis Care &Research, Accepted Article.
Objective VEXAS syndrome is characterized by a complex spectrum of inflammatory and hematologic manifestations. Clinical research to identify effective therapies is urgently needed but is hindered by the lack of validated outcome measures. A VEXAS‐specific disease activity index (DAI) is an essential tool for reliably capturing changes in disease ...
Kevin Byram, Heřman Mann, Danielle Hammond, Onima Chowdhury, Sinisa Savic, Yohei Kirino, Carmelo Gurnari, Maël Heiblig, Thibault Comont, Arsène Mekinian, Mrinal M. Patnaik, Lachelle D. Weeks, Gary Ho, Adam Al‐Hakim, Scott Goldberg, Marcela A. Ferrada, Sophie Georgin‐Lavialle, Peter C. Grayson, Emma M. Groarke, Bhavisha Patel, Megan Sullivan, Sarah A. Buckley, Bryan G. Harder, Raman Garcha, David B. Beck, Matthew J. Koster   +25 more
wiley   +1 more source

Delayed Diagnosis of Constrictive Pericarditis Resulting in Recurrent Heart Failure: A Case Report

Clinical Medicine Insights: Case Reports
Constrictive pericarditis can lead to compromised diastolic ventricular filling due to pericardial inflammation and fibrosis. A diagnosis of constrictive pericarditis was established by identifying structural and hemodynamic features through ...
Chunliang Wang, Yuzhu Fan, Guiting Liang, Yu Chen, Tian Tu, Juan Du   +5 more
doaj   +1 more source

Cardiovascular Toxicity Associated With Bispecific Antibodies in Hematological Malignancies: A Comprehensive Pharmacovigilance Analysis

American Journal of Hematology, EarlyView.
ABSTRACT Cardiovascular adverse events (CVAEs) associated with bispecific T‐cell engaging antibodies (BsAbs) have not been systematically investigated across approved agents. In this disproportionality analysis of FAERS (December 2014–September 2025), reports listing BsAbs as the primary suspected drug (n = 7647) were compared with all other drugs in ...
Malak Munir, Ahmed Sayed, Dae Hyun Lee, Sanam Ghazi, Mustafa M. Houmsse, Saad Badat, Abdul Moeed, Avirup Guha, Daniel Addison, Narendranath Epperla   +9 more
wiley   +1 more source

Tuberculous constrictive pericarditis [PDF]

BMJ Case Reports, 2019
A previously healthy 53-year-old Brazilian man presented with a 3-month history of anasarca, dyspnoea on minimal exertion, orthopnoea, paroxysmal nocturnal dyspnoea, low-grade fever and an unintentional 12 kg weight loss. No prior medical condition was related.
Neiberg de Alcantara Lima, Danielli Oliveira da Costa Lino, Naiana Medeiros Coelho, Thomas Melgar   +3 more
openaire   +2 more sources

Severe ADEM‐Like Neuroinflammatory Disease and Cerebrovascular Fragility With Recurrent Pseudoaneurysms and Moyamoya in a Familial Germline CBL Mutation: Expanding the Clinical Phenotype

American Journal of Medical Genetics Part A, EarlyView.
ABSTRACT Heterozygous germline variants in CBL disrupt its function as a negative regulator of the Ras/MAPK pathway, classically predisposing to Juvenile myelomonocytic leukemia (JMML) and moyamoya. We describe two affected siblings carrying a paternally inherited CBL variant (c.1210 T> C, p.
Michal Bar‐Hakim, Anat Abramovich, Sara Via‐Dorembus, Gali Heimer, Bruria Ben‐Zeev, Etai Adam, Assaf A. Barg, Jonathan Roth, Basheer Sheick‐Yousif, Rony Beeri Berkowiz, Michal Feldon, Haim Bassan, Moran Hausman‐Kedem   +12 more
wiley   +1 more source

A failing right heart in an eggshell: A case report of idiopathic constrictive pericarditis

Clinical Case Reports
key Clinical Message Constrictive Pericarditis is a rare fibrotic conversion of the pericardium that results in non‐specific clinical symptoms such as hepatomegaly, ascites, pleural effusions, and lower extremity edema.
Nivedha Balaji, Sheriff N. Dodoo, Alex Adams, Priyadarshini Dixit, Giancarlo Acosta, Jaime Burkle   +5 more
doaj   +1 more source

Pericardial mesothelioma presenting as chronic constrictive pericarditis. A series of three cases from a single institution

Indian Journal of Pathology and Microbiology, 2018
Pericardial mesotheliomas are rare tumors which often present with features of constrictive pericarditis. We present clinical, imaging, histological, and immunohistochemical findings of three cases presenting with chronic constrictive pericarditis.
Monalisa Hui, K R Harshavardhana, Shantveer G Uppin   +2 more
doaj   +1 more source

Malignant pleural mesothelioma with constrictive pericarditis as the first manifestation: A case report

Clinical Case Reports, 2023
Pleural mesothelioma (PM) with pericardial involvement is extremely rare. We now report a rare case of malignant PM with constrictive pericarditis as the first presentation.
Cheng‐Peng He, Di‐Wei Tu, Ting‐Wei Zhang, Qian Zhang, Qiang Zhang, Di Kang, Ying‐Ying Wang, Ying‐Ying Li, Bin Zhang, Sha‐Sha Han, Hong‐Bo Li   +10 more
doaj   +1 more source

Therapy for Myhre Syndrome: Goals, Misconceptions, and Current Agents

American Journal of Medical Genetics Part C: Seminars in Medical Genetics, EarlyView.
ABSTRACT Myhre Syndrome (MYHRS, MIM #139210) is a rare, multisystem connective tissue disorder caused by recurrent heterozygous gain‐of‐function pathogenic variants in the SMAD4 gene, a key player in TGF‐β signaling and a regulator of extracellular matrix homeostasis.
Alessandro De Falco, Alfonso Manuel D'Alessio, Nicola Brunetti‐Pierri   +2 more
wiley   +1 more source