Results 31 to 40 of about 4,316 (128)

Advancements in the diagnosis and treatment of renal epithelioid angiomyolipoma: A narrative review

Kaohsiung Journal of Medical Sciences, 2022
Renal epithelioid angiomyolipoma (EAML) is a unique subtype of angiomyolipoma that contains a variety of cytoplasmic‐rich, eosinophilic cytoplasm epithelioid cells in addition to mature adipocytes, hyaline thick‐walled vessels, and smooth muscle‐like ...
Jian‐Wei Yang, Cheng Liang, Li Yang
doaj   +1 more source

Out of the Ordinary, but Not Out of the Question: Atypia in Pancreatic Lesions Is Not Always Carcinoma

Cytopathology, EarlyView.
An incidental pancreatic lesion in a 69‐year‐old woman was sampled by EUS‐guided fine‐needle biopsy. Integrated cytopathological and histopathological evaluation with immunochemical staining supported organ‐preserving surgery. ABSTRACT Pancreatic perivascular epithelioid cell tumours (PEComas) are exceptionally rare mesenchymal neoplasms.
Maja Kebe Radulovic, Branislava Rankovic, Ajda Toni, Margareta Zlajpah, Darko Siuka   +4 more
wiley   +1 more source

Novel and emerging cutaneous soft tissue tumours

Histopathology, EarlyView.
This review outlines the defining histopathological, immunophenotypic and molecular features of novel and emerging cutaneous soft tissue tumours, including hybrid superficial ALK‐rearranged myxoid spindle cell neoplasm/epithelioid fibrous histiocytoma, superficial neurocristic tumour, ALK‐rearranged epithelioid vascular neoplasm and MITF pathway ...
Saba Shafi, Josephine K Dermawan
wiley   +1 more source

Epithelioid PEComa coexisting with angiomyolipoma in the kidney

Radiology Case Reports
Renal epithelioid perivascular epithelioid cell tumors (PEComas) are rare neoplasms with potential for aggressive clinical behaviour that present a significant diagnostic challenge due to imaging features that overlap with renal cell carcinoma (RCC).
Chung Wai Wong, MBBS (HK), FRCR, Richard Wing-Cheuk Wong, MBBS (HK), FHKAM, Novena Lin Sing Cheng, LMCHK, FRCR, FHKAM, Chuen Wai Choi, MBBS (HK), FRCR, FHKAM   +3 more
doaj   +1 more source

Soft Tissue Perivascular Epithelioid Cell Tumour: An Unusual Finding

Prague Medical Report, 2021
Perivascular epithelioid cell tumour (PEComa) is a rare mesenchymal tumour made up of clear perivascular cells with epithelioid characteristics, which co-expresses muscle and melanocytic markers with a component of spindle cells, like sarcoma and variety
Mauricio Bermúdez Sagre, Christian Ospina Pérez, Jennyfer Ortega Guatame, Rosa Ospina Perez, Ivan Lozada Martínez, Jennifer Jiménez Valverde, María Bolaño Romero   +6 more
doaj   +1 more source

Treatment strategies for interstitial granulomatous dermatitis: Systematic review and expert opinion

Journal of the European Academy of Dermatology and Venereology, EarlyView.
Systematic review of 108 studies with a total of 182 patients with interstitial granulomatous dermatitis (IGD). IGD was frequently associated with systemic conditions or drug exposure. Management includes careful medication review and prompt withdrawal of potential triggers. Corticosteroids (systemic and topical) were commonly effective, while biologic
Francesco Bellinato, Sara Salvagno, Chiara Colato, Paolo Gisondi, Giampiero Girolomoni   +4 more
wiley   +1 more source

Recurrence of retroperitoneal localized perivascular epithelioid cell tumor two years after initial diagnosis: case report

São Paulo Medical Journal, 2018
CONTEXT: Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal tumors. Adjuvant radiotherapy and/or chemotherapy are administered according to the patient’s clinical characteristics. CASE REPORT: A 42-year-old female patient was operated
Yasemin Benderli Cihan, Engin Kut, Ali Koç   +2 more
doaj   +1 more source

Idiopathic Granulomatous Inflammation of the Periocular Structures in Four Dogs: Clinical, Histopathological, and Imaging Findings and Therapeutic Outcome

Veterinary Ophthalmology, Volume 29, Issue 6, November 2026.
ABSTRACT Purpose To describe cases of canine idiopathic periocular granulomatous inflammation. Material and Methods Clinical records were reviewed. Animal Studied At the time of presentation, the four patients (German Shepherd dog, mixed breed, Magyar Vizsla, Hovawart) were 1.5–5 (mean 3.75) years old. All dogs were female; two were spayed.
J. Kurwinkel, C. Busse, A. Beineke, I. Gerhauser, S. Pahl, A. H. Marx   +5 more
wiley   +1 more source

A Case of Primary Intramedullary Infantile Fibrosarcoma With an RBPMS::NTRK3 Fusion and Response to Larotrectinib

Neuropathology and Applied Neurobiology, Volume 52, Issue 5, October 2026.
We report a case of primary intramedullary infantile fibrosarcoma (IFS) in a 4‐week‐old infant with rapidly progressive cervical myelopathy. Histology showed a spindle cell tumour with diffuse S100 and pan‐TRK expression. RNA sequencing identified an RBPMS::NTRK3 fusion.
Mégane Le Quang, Julie Tandonnet, Nathalène Truffaux, Lucile Vanhersecke, Jean Delmas, Arthur Durouchoux, Dorian Bochaton, Arnault Tauziède‐Espariat, Guillaume Chotard   +8 more
wiley   +1 more source

Clear cell myomelanocytic tumor of ligamentum teres

Autopsy and Case Reports
Clear cell myomelanocytic tumor (CCMMT) of the falciform ligament/ligamentum teres is a rare hepatic tumor, a variant of the perivascular epithelioid cell tumor (PEComa) family. CCMMT is the rarest variant of hepatic PEComas.
Ariba Zaidi, Debajyoti Chatterjee, Venu Bhargav, Vikas Gupta, Ashim Das   +4 more
doaj   +1 more source