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Central precocious puberty in a 3 year-old girl with Phenylketonuria: a rare association? [PDF]
, 2014 Background Central precocious puberty (CPP) and phenylketonuria (PKU) are two rare conditions, the latter being the rarer. To date, only one case featuring both these conditions has been reported, and hyperphenylalaninemia was assumed triggering CPP.
Donaldson, Malcolm +3 more
core +3 more sources
Metabolites, 2021 Monitoring phenylalanine (Phe) concentrations is critical for the management of phenylketonuria (PKU). This can be done in dried blood spots (DBS) or in EDTA plasma derived from capillary or venous blood. Different techniques are used to measure Phe, the
Dorothea Haas +9 more
doaj +1 more source
Mechanism of phenylalanine regulation of phenylalanine hydroxylase.
Journal of Biological Chemistry, 1990 The mechanism of phenylalanine regulation of rat liver phenylalanine hydroxylase was studied. We show that phenylalanine "activates" phenylalanine hydroxylase, converting it from an inactive to active form, by binding at a true allosteric regulatory site.
S H Jones, R. Shiman, D W Gray
openaire +3 more sources
Applied Sciences, 2020 In this work, we developed a portable device with low production and operation costs for generating ambient-air glow discharge (AAGD) that is transferred to the surface of flowing liquid and demonstrated its applicability to practical use in agriculture.
Vladislav Gamaleev +5 more
doaj +1 more source
Aromatic Dipeptide Homologue-Based Hydrogels for Photocontrolled Drug Release
Nanomaterials, 2022 Peptide-based hydrogels are considered of special importance due to their biocompatibility and biodegradability. They have a wide range of applications in the biomedical field, such as drug delivery, tissue engineering, wound healing, cell culture media,
Chloé Guilbaud-Chéreau +5 more
doaj +1 more source
Enantiomerically pure β-phenylalanine analogues from α–β-phenylalanine mixtures in a single reactive extraction step [PDF]
, 2010 An efficient and selective method for the extraction of α-amino acids in preference over their β-isomers using PdCl2(PPh3)2 was discovered, which enables the separation of product mixtures obtained in the enantioselective enzymatic formation of β-amino ...
Feringa, Ben L., +6 more
core +2 more sources
Dictyostelium phenylalanine hydroxylase is activated by its substrate phenylalanine [PDF]
FEBS Letters, 2012 dicPAH and dicPAH bind by molecular sieving (View Interaction: 1, 2, 3, 4)
Soo-Woong Lee +7 more
openaire +3 more sources
Jornal de Pediatria, 2007 OBJETIVO: Avaliar o efeito do leite materno como fonte de fenilalanina (phe) nos níveis sangüíneos desse aminoácido e no crescimento de fenilcetonúricos.
Viviane C. Kanufre +6 more
doaj +1 more source
JIMD Reports, 2023 Measurement of plasma and dried blood spot (DBS) phenylalanine (Phe) is key to monitoring patients with phenylketonuria (PKU). The relationship between plasma and capillary DBS Phe concentrations has been investigated previously, however, differences in ...
Rachel S. Carling +8 more
doaj +1 more source
Completion of the cytosolic post-chorismate phenylalanine biosynthetic pathway in plants
Nature Communications, 2019 In addition to being a vital component of proteins, phenylalanine is also a precursor of numerous aromatic primary and secondary metabolites with broad physiological functions.
Yichun Qian +5 more
semanticscholar +1 more source