Results 21 to 30 of about 6,021 (252)
Refractory pityriasis rubra pilaris treated with abrocitinib [PDF]
Pityriasis rubra pilaris is a rare idiopathic papulosquamous disorder that significantly impacts the quality of life and is often refractory to conventional therapies. This study presents a case of successful treatment with an abrocitinib JAK1 inhibitor
Filip Rob
doaj +2 more sources
A Rare Post-infectious Rash: Pityriasis Rubra Pilaris After COVID-19 Infection. [PDF]
Pityriasis rubra pilaris (PRP) is a rare papulosquamous skin disorder that often presents with erythematous follicular-based hyperkeratotic papules that can become confluent and lead to erythroderma and electrolyte and thermoregulatory imbalances ...
Duncan P, Flood D, Dietz C.
europepmc +2 more sources
Patients with keratinization disorders due to ABCA12 variants showing pityriasis rubra pilaris phenotypes [PDF]
Pathogenic variants in ABCA12 are important causative genetic defects for autosomal recessive congenital ichthyoses (ARCI), which include congenital ichthyosiform erythroderma (CIE), harlequin ichthyosis, and lamellar ichthyosis.
Akiyama, Masashi +12 more
core +2 more sources
Misdiagnosed Pityriasis Rubra Pilaris Successfully Managed With Isotretinoin: A Case Series. [PDF]
Being a rare inflammatory, hyperproliferative dermatosis, diagnosing pityriasis rubra pilaris (PRP) can be a challenge to many clinicians. Our case reports aim to demonstrate that PRP is frequently diagnosed and managed as atopic dermatitis (AD) and that
Al Khalifa N +3 more
europepmc +2 more sources
A Review of Pityriasis Rubra Pilaris and Rheumatologic Associations [PDF]
Pityriasis rubra pilaris (PRP) is a rare group of hyperkeratotic, papulosquamous disease that can be acquired or inherited. There have been reported cases of rheumatologic associations, mainly arthritis and ...
Happy Chan +2 more
doaj +5 more sources
Successful treatment with cyclosporine and guselkumab for pityriasis rubra pilaris [PDF]
A man with pityriasis rubra pilaris (PRP) showed no improvement in skin symptoms despite treatment with several drugs. The patient was diagnosed as having type 1 PRP. Combination therapy with cyclosporine and guselkumab improved his skin condition. Here,
Mai Nishimura +4 more
doaj +2 more sources
Pityriasis Rubra Pilaris [PDF]
Godfrey Bamber
+8 more sources
Greiling TM, Brown F, Syed HA.
europepmc +4 more sources
Importance There is no US Food and Drug Administration-approved treatment for pityriasis rubra pilaris (PRP), and it is common for patients to fail to experience improvement with several systemic options.
Velasco RC +7 more
europepmc +2 more sources
A case of pityriasis rubra pilaris secondary to ponatinib [PDF]
Ponatinib, a tyrosine kinase inhibitor used for chronic myeloid leukemia and acute lymphoblastic leukemia, can cause rare cutaneous side effects. In this case, a 63-year-old woman developed a pityriasis rubra pilaris-like eruption 1 month after starting ...
Ariana Nateghi +2 more
doaj +2 more sources

