Results 101 to 110 of about 3,342 (255)

Optical mapping reveals a higher level of large‐scale structural variants in a family with paternally transmitted myotonic dystrophy and independent Parkinson's disease

The Journal of Pathology, EarlyView.
Abstract Myotonic dystrophy type 1 (DM1) is a clinically challenging multisystem neuromuscular hereditary disorder, with generational increase in severity and earlier age at onset. It is caused by an unstable cytosine‐thymine‐guanine repeat expansion at the DMPK locus, accompanied by associated genetic and epigenetic modifications.
Md Mehedi Hasan, Jenna Craddock, Tingting Gong, Ruth J Lyons, Igor Stevanovski, Sanjog R Chintalaphani, Ira W Deveson, Weerachai Jaratlerdsiri, Kishore R Kumar, Vanessa M Hayes   +9 more
wiley   +1 more source

Prediction of In‐Plane Shear Mechanical Properties Through Degree of Bonding Characterization as a Function of Automated Fiber Placement Processing Parameters for Carbon Fiber/PEKK Composite Laminates

Polymer Composites, EarlyView.
Graphical abstract demonstrating manufacturing process and property characterization used in process modelling of interlaminar behavior across the range of process parameters. ABSTRACT Automated Fiber Placement (AFP) of fiber‐reinforced thermoplastic tapes enables rapid manufacturing by leveraging precise robotic lamination and in situ consolidation ...
Abd‐Elrahman Korayem, Chandra Kishore Reddy Emani, Saratchandra Kundurthi, Karthik Venkatesan, Si Chen, Javed Mapkar, Mahmoodul Haq   +6 more
wiley   +1 more source

Characteristics, properties and limitations of per‐ or polyfluoroalkyl substances (PFASs) and fluoropolymers

Polymer International, EarlyView.
An overview and categorization of man‐made per‐ or polyfluoroalkyl substances (PFASs) including low‐molar‐mass and high‐molar‐mass fluorochemicals, and their international regulations is presented. Though certain PFASs are toxic, bioaccumulative and cross the human cellular membranes, others, such as fluoropolymers, are safe, reliable and involved in ...
Bruno Améduri
wiley   +1 more source

Addressing Biases in Ice Jam Observations by Integrating Multi‐Source Data in a Forested Fluvial Landscape, Southern Quebec

River Research and Applications, EarlyView.
ABSTRACT Exhaustive long‐term and large‐scale ice jam records are scarce in most cold river environments. Many discrete events occur in small, sparsely populated river systems and are poorly represented in open‐source databases. These observation biases are transferred to predictive models of ice jams and the collective understanding of their formation
Lisane Arsenault‐Boucher, Étienne Boucher, Rachid Lhissou, Karem Chokmani, Christophe Kinnard   +4 more
wiley   +1 more source

The Fargo‐Moorhead Diversion: Flood Protection or Sprawl Promotion?

River Research and Applications, EarlyView.
ABSTRACT Urban growth and development opportunities are needed worldwide, but growth and development must be hazard‐aware and should follow smart‐growth principles. The $2.89 billion Fargo‐Moorhead Area Diversion Project was designed to provide flood protection following damaging floods on the Red River of the North.
Nicholas Pinter, Ryan G. Miller, Joel Paulsen   +2 more
wiley   +1 more source

UNMANNED GROUND VEHICLES - PERSPECTIVES OF APPLICATION IN THE POLISH ARMY

PROBLEMY TECHNIKI UZBROJENIA
The paper presents perspectives of using unmanned ground vehicles (UGV) in the Polish Army. Demands of the Armed Forces on them are discussed both with the current state of UGV technology in the world and in Poland, and the potential of the Polish industry and the chances and challenges for implementation of UGV into the Polish Army.
openaire   +1 more source

National Policy Coherence Counts for Reducing Inequality in Global Climate and Development Agendas

Sustainable Development, EarlyView.
ABSTRACT International institutions promote policy coherence as crucial to the effective and fair implementation of global sustainability agendas, though the evidence for its benefits is slim. We present here the first systematic cross‐country dataset on the consequences of national government efforts to promote policy coherence for vulnerable groups ...
Katherine Browne, Adis Dzebo, Zoha Shawoo, Mario Cardenas, Pierrick Chalaye, Alexia Faus Onbargi, Cassilde Muhoza, Patricia Nicdao, Nokwethaba Makhanya, Navam Niles, Priyatma Singh   +10 more
wiley   +1 more source

Transforming Paper into Plasmonic Sensors: One‐Step Fabrication of High‐Enhancement SERS Nanosubstrates via Surface Energy Control

Small Methods, EarlyView.
Cellulose paper is transformed into a high‐performance plasmonic sensor through a process called SILVERED, which involves single‐step vapor deposition onto fluorosilanized fibers. Surface‐energy contrast drives uniform silver nanoparticle growth with sub‐10 nm hot‐spot gaps, achieving 2 pM detection of rhodamine B.
Farbod Ebrahimi, Anjali Kumari, Kyle Nowlin, Tohid Didar, Kristen Dellinger   +4 more
wiley   +1 more source

Assessing Capability Complexity Using Enterprise Architecture Framework

Systems Engineering, EarlyView.
ABSTRACT This study proposes a structured and quantitative methodology to evaluate the holistic complexity of system‐of‐systems (SoSs), employing the Zachman Architecture Framework (ZAF) as its foundational analytical tool. A five‐phase analytical procedure is developed and empirically validated, encompassing: (1) refinement of complexity measures, (2)
Javad Bakhshi, Mahmoud Efatmaneshnik
wiley   +1 more source

Systematic Learning and Pedagogy Through a Modular, Progressive‐Based Simulation Modeling Framework for Complex Systems

Systems Engineering, EarlyView.
ABSTRACT Smart Transportation Systems (SmTS) will exceed complex systems with their classification as complex, sociotechnical, and AI‐based systems. Possessing a toolkit that helps systemically understand, analyze, and assess these systems will be advantageous in the early stages of the systems engineering (SE) lifecycle, and Agent Based Models (ABMs ...
Ifezue V. Obiako, Sean B. Walker, Kari J. Lippert, Robert J. Cloutier   +3 more
wiley   +1 more source