Results 41 to 50 of about 16,344 (265)
Optimal management of Cogan’s syndrome: a multidisciplinary approach [PDF]
, 2017 Cogan's syndrome (CS) is a rare disorder characterized by nonsyphilitic interstitial keratitis (IK) and audio-vestibular symptoms. CS affects mainly young Caucasian adults, mostly during their first three decades of age, and may develop into typical and ...
D'Aguanno, Vittorio +3 more
core +1 more source
Arthritis &Rheumatology, Accepted Article.Objective To assess the 2022‐ACR/EULAR classification criteria for ANCA‐associated vasculitis (AAV) in children with chronic small‐to‐medium vessel vasculitis. Methods A cohort of 574 patients, identified by physician's‐(MD)‐diagnosis in A‐Registry‐of‐Childhood‐Vasculitis, were classified by computation of registry data, as having granulomatosis with ...
David A. Cabral +41 more
wiley +1 more source
Fulminant Wegener's granulomatosis: A case report [PDF]
, 2013 Introduction. Granulomatosis Wegener is anti-neutrophil cytoplasmic antibodies (ANCAs)-associated systemic vasculitis of unknown etiology. It is manifested as granulomatous necrotizing inflammation of the upper and lower parts of the respiratory tract,
Dinić Miroslav Ž. +3 more
core +1 more source
Clinical Case Reports, Volume 14, Issue 5, May 2026.ABSTRACT The coexistence of primary phospholipase A2 receptor positive membranous nephropathy and AA amyloidosis in a patient with chronic hepatitis B is an exceedingly rare triad presenting a profound diagnostic and therapeutic challenge. A 38‐year‐old Ethiopian man with nephrotic syndrome and chronic hepatitis B had dual pathology on renal biopsy ...
Betelhem Abreham +4 more
wiley +1 more source
Cutaneous polyarteritis nodosa: Diagnosis lies skin deep
Indian Journal of Paediatric Dermatology, 2018 Cutaneous polyarteritis nodosa (CPAN) is an uncommon form of cutaneous vasculitis. Definitive diagnosis is based on skin biopsy. We present a rare case of CPAN in a 2-year-old male child who presented with a history of fever, cutaneous ulcers, and ...
Raghavendraswami Amoghimath +3 more
doaj +1 more source
ACR Open Rheumatology, Volume 8, Issue 4, April 2026.Objective Gain‐of‐function variants in IDH1 and IDH2 are enriched among individuals with coexisting myeloid neoplasms and autoimmune diseases. However, the association between IDH1/IDH2 variants and rheumatic diseases independent of hematologic neoplasms remains unclear. We investigated the association between rare gain‐of‐function and loss‐of‐function
Mahmut S. Kaymakci +3 more
wiley +1 more source
HYPERTROPHIC CARDIOMYOPATHY ASSOCIATED WITH POLYARTERITIS NODOSA: A CASE OF SUDDEN CARDIAC DEATH
Euromediterranean Biomedical Journal, 2018 This case concerns a rare sudden cardiac death characterized by macroscopic and microscopic post-mortem findings of hypertrophic cardiomyopathy and polyarteritis nodosa.
Elvira Ventura Spagnolo
doaj +1 more source
ACR Open Rheumatology, Volume 8, Issue 4, April 2026.Objective Medium‐vessel vasculitis involving the visceral vasculature in adults is rare. Pancreatic ductal adenocarcinoma (PDAC) has been implicated in medium artery vascular thickening secondary to extravascular migratory metastasis with involvement of the celiac and superior mesenteric vessels.
Maryam Own +2 more
wiley +1 more source
DEN Open, Volume 6, Issue 1, April 2026.Abstract Direct oral anticoagulants (DOACs), including edoxaban, are widely used for stroke prevention in atrial fibrillation and venous thromboembolism. While gastrointestinal bleeding and diarrhea are recognized adverse effects, DOAC‐induced enterocolitis has not been established as a distinct clinical entity.
Katsuya Endo +8 more
wiley +1 more source
대한영상의학회지, 2017 Multiple intrahepatic arterial aneurysms and spontaneous aneurysmal rupture associated with polyarteritis nodosa leading to hemoperitoneum are extremely rare occurrences, but the conditions can be life-threatening if left untreated because of the risk of
Myung Jin Seol +3 more
doaj +1 more source