Polyostotic Fibrous Dysplasia With and Without McCune-Albright Syndrome-Clinical Features in a Nordic Pediatric Cohort. [PDF]
Front Endocrinol (Lausanne), 2018 Objective Fibrous dysplasia (FD) presents as skeletal lesions in which normal bone is replaced by abnormal fibrous tissue due to mosaic GNAS mutation.
Utriainen P +4 more
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Diagnosis and conservative treatment of a rare case of femoral intraosseous arteriovenous malformation in a patient with polyostotic fibrous dysplasia: A case report. [PDF]
Mol Clin Oncol, 2019 Pure intraosseous arteriovenous malformation (AVM) in a limb bone is extremely rare. Furthermore, there is currently insufficient information on the diagnostic and therapeutic strategies for pure intraosseous AVMs.
Ohshika S +3 more
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Polyostotic Fibrous Dysplasia: A Case Report of Rarity. [PDF]
Cureus, 2023 A skeletal condition known as fibrous dysplasia (FD) is characterized by the replacement of healthy bone with fibrous bone tissue. One bone (monostotic) or several bones could be involved (polyostotic).
Wadewale SN, Bhola ND, Agarwal A.
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Lower-limb intramedullary nailing in patients with polyostotic fibrous dysplasia who had a previous unsuccessful treatment. A report of 48 cases. [PDF]
J Orthop Traumatol, 2023 Background Intramedullary nailing (IN) seems to be the best primary surgical treatment for patients with either polyostotic fibrous dysplasia or McCune–Albright syndrome (PFD/MAS) when the femur and tibia are totally affected by fibrous dysplasia (FD ...
Ippolito E +5 more
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Surgical correction of valgus deformities of the knee in Polyostotic Fibrous Dysplasia. [PDF]
Orthop Rev (Pavia), 2022 Coxa vara and shepherd's crook deformity represent the most common femoral deformities in patients affected by polyostotic fibrous dysplasia (PFD) and McCune Albright syndrome (MAS).
Gorgolini G +5 more
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Cross-sectional evaluation of FGD-avid polyostotic fibrous dysplasia: MRI, CT and PET/MRI findings. [PDF]
Eur J Hybrid Imaging, 2022 A 42-year-old male with left hip pain was diagnosed of several right femoral and tibial bone tumours. All lesions were osteolytic with sclerotic margins. The symptomatic lesion in the proximal femur also showed bone expansion and focal cortical thinning.
Pozzessere C +6 more
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Surgical treatment of femoral deformities in polyostotic fibrous dysplasia and McCune-Albright syndrome: A literature review. [PDF]
World J Orthop, 2022 BACKGROUND Surgical correction of femoral deformities in polyostotic fibrous dysplasia (PFD) or McCune-Albright syndrome (MAS), such as coxa vara or shepherd’s crook deformity, is a challenge.
Gorgolini G +5 more
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Journal of Clinical and Biomedical Sciences, 2022 Fibrous dysplasia is a disease that causes aberrant development of osteoblasts, which results in fibrous stroma replacing normal bone. Lichtenstein first described it in 1938. It is a sporadic disorder caused due to a postzygotic mutation in the
R B Revanth +5 more
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Journal of the Belgian Society of Radiology, 2013 Background: A 51-year-old male was referred to the hospital with pain on the right side of the thorax, without any apparent trauma. There was no medical history. He had a nonproductive cough and smoked 15 cigarettes a day.
BJ Schouten, HM Suliman
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Increasing serum alkaline phosphatase is associated with bone deformity progression for patients with polyostotic fibrous dysplasia. [PDF]
J Orthop Surg Res, 2020 Background Fibrous dysplasia (FD) is a rare bone disorder in which normal intramedullary bone is replaced by fibro-osseous tissue, which is complicated by the progression of Shepherd’s crook deformity.
Wang J +6 more
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