Craniofacial polyostotic fibrous dysplasia
Contemporary Clinical Dentistry, 2010 An unusual case of fibrous dysplasia involving right craniofacial region in a female is reported. The clinical features, radiological findings, and treatment have been discussed.
Yadavalli Guruprasad, Chandan Prabhakar
doaj +5 more sources
Polyostotic fibrous dysplasia (McCune-Albright) with rare multiple epiphyseal lesions in association with aneurysmal bone cyst and pathologic fracture [PDF]
Radiology Case Reports, 2021 Fibrous dysplasia, including McCune-Albright syndrome, is a genetic, non-inheritable benign bone disorder that may involve a single or multiple bone, typically occurring in the diaphysis or the metaphysis of long bones. In very rare instances polyostotic
Alvaro Burdiles, MD +7 more
doaj +2 more sources
Polyostotic Fibrous Dysplasia Complicated by Pathological Fracture of Right Femoral Shaft with Nonunion: A Case Report [PDF]
Frontiers in Surgery, 2022 IntroductionFibrous dysplasia is a benign fibrous bone tumor that accounts for 5% to 10% of benign bone tumors. It can manifest as simple fibrous dysplasia (70%–80%), polyostotic fibrous dysplasia (20%–30%), with approximately the same incidence in men ...
Qifan Yang +4 more
doaj +2 more sources
Polyostotic fibrous dysplasia: Unveiling the complexity of a rare bone disorder through a case report [PDF]
Radiology Case ReportsPolyostotic fibrous dysplasia is a benign but potentially debilitating bone disorder characterized by the gradual replacement of normal bone with fibrous tissue.
Siham Nasri +3 more
doaj +2 more sources
Journal of the Belgian Society of Radiology, 2013 Background: A 51-year-old male was referred to the hospital with pain on the right side of the thorax, without any apparent trauma. There was no medical history. He had a nonproductive cough and smoked 15 cigarettes a day.
BJ Schouten, HM Suliman
doaj +5 more sources
Polyostotic Fibrous Dysplasia: A Case Report [PDF]
CureusPolyostotic fibrous dysplasia (PFD) is a scarce noncancerous bone condition characterized by the failure to form mature lamellar bone and arrest in the form of woven bone, resulting in deformities and functional limitations. Extreme forms of craniofacial fibrous dysplasia can lead to leontiasis ossea, an exceptionally uncommon presentation. We report a
Arun Aram +3 more
europepmc +4 more sources
Polyostotic Fibrous Dysplasia With and Without McCune-Albright Syndrome-Clinical Features in a Nordic Pediatric Cohort. [PDF]
Front Endocrinol (Lausanne), 2018 Objective: Fibrous dysplasia (FD) presents as skeletal lesions in which normal bone is replaced by abnormal fibrous tissue due to mosaic GNAS mutation.
Utriainen P +4 more
europepmc +3 more sources
Pamidronic acid and cabergoline as effective long-term therapy in a 12-year-old girl with extended facial polyostotic fibrous dysplasia, prolactinoma and acromegaly in McCune-Albright syndrome: a case report [PDF]
Journal of Medical Case Reports, 2012 Introduction McCune-Albright syndrome is a complex inborn disorder due to early embryonal postzygotic somatic activating mutations in the GNAS1 gene. The phenotype is very heterogeneous and includes polyostotic fibrous dysplasia, typically involving the ...
Classen Carl +4 more
doaj +5 more sources
Pagetoid polyostotic fibrous dysplasia. [PDF]
BMJ Case Rep, 2015 Fibrous dysplasia (FD) is a benign skeletal lesion occurring due to mutation of Gs α gene and involves one or multiple bones. We present a case of a 30-year-old female patient, with a 1-year history of swelling under her right eye that had gradually increased in size.
Hosalkar RM +3 more
europepmc +4 more sources
Bone-Grafting in Polyostotic Fibrous Dysplasia [PDF]
J Bone Joint Surg Am, 2016 Polyostotic fibrous dysplasia is a skeletal disease that results from somatic activating mutations in the gene GNAS in skeletal stem cells, leading to proliferation of immature osteogenic cells with replacement of normal marrow and bone with fibro-osseous tissue. Lesions may cause bone deformity or fracture.
Arabella I. Leet +5 more
europepmc +5 more sources