Results 41 to 50 of about 1,222,131 (133)
Student's Journal of Health Research Africa, 2023 Biliary atresia is a destructive, idiopathic, and inflammatory cholangiopathy that affects intra and extra-hepatic bile ducts leading to fibrosis and obliteration of the biliary tract and development of liver cirrhosis.
Evalyne Tukwasibwe +3 more
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Aortic pseudocoarctation associated with polysplenia/heterotaxy syndrome
Revista Portuguesa de Cardiologia, 2015 Polysplenia/heterotaxy syndrome is a rare congenital disorder associated with a wide spectrum of anomalies in various organ systems. Although anomalies of the cardiovascular system are common in this syndrome, the authors report a rare case of ...
Ricardo Duarte, Humberto Morais
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Analysis of associated malformations by computed tomography in adults with polysplenia syndrome: A pilot study. [PDF]
PLoS OneObjectiveTo analytically depict the associated malformations of polysplenia syndrome (PS) in adults via computed tomography (CT).Materials and methodsThe incidence of malformations associated with PS in twelve adult patients was retrospectively analyzed ...
Gu X +8 more
europepmc +2 more sources
Clinical implications of congenital interruption of inferior vena cava
Journal of the Formosan Medical Association, 2022 Background/purpose: Inferior vena cava (IVC) interruption is rare and can be detected through prenatal or postnatal imaging. It usually occurs in patients with heterotaxy syndrome with bilateral left-sidedness (left isomerism or polysplenia syndrome ...
Shyh-Jye Chen, Mei-Hwan Wu, Jou-Kou Wang
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Anomalies of Abdominal Organs in Polysplenia Syndrome: Multidetector Computed Tomography Findings
대한영상의학회지, 2016 Polysplenia syndrome is a rare situs ambiguous anomaly associated with multiple spleens and anomalies of abdominal organs. Because most of the minor anomalies do not cause clinical symptoms, polysplenia syndrome is detected incidentally in the adults ...
Sungwon Kim, Yong Seok Lee, Jin-Hee Jung
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Clinical Case Reports, 2021 Heterotaxy syndrome is associated with asplenia/polysplenia and complex congenital heart disease. Facial palsy in heterotaxy is very rare. The management is still challenging with a poor prognosis. Proper counseling to the family about the disease course,
Sanjeev Kharel +6 more
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A Case of Polysplenia Syndrome Presenting with Ascites
, 2012 Polysplenia syndrome is a rare congenital anomaly frequently associated with various visceral anomalies. The most frequent manifestations of this syndrome, in addition to polysplenia are malrotation, congenital heart diseases and gastrointestinal ...
Ozgur, ORHAN +5 more
core +1 more source
Heterotaxy Syndrome with Polysplenia, Fused Adrenal Glands, and Diabetes Mellitus
Clinical Medicine Insights: Cardiology, 2022 Heterotaxy syndrome is a rare congenital heart disease with a disarrangement of the heart and abdominal organs. We present a young African female with features of heart failure, diffuse irregular cardiac murmurs, and palpable, tender epigastric mass.
Abid M Sadiq, Adnan M Sadiq
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Hepatology Research, EarlyView.ABSTRACT Aim In Fontan‐associated liver disease (FALD), chronic congestion often confounds conventional fibrosis markers, complicating surveillance for hepatocellular carcinoma (HCC). Although lymphatic dysfunction is fundamental to Fontan physiology, its contribution to hepatocarcinogenesis remains unclear.
Koji Imoto +14 more
wiley +1 more source
Unusual, unexpected course of temporary pacing lead leading to diagnosis of a rare syndrome
IHJ Cardiovascular Case Reports, 2019 We describe a case of an elderly female with complete heart block where temporary pacemaker insertion led to diagnosis of inferior vena cava interruption, leading further to diagnosis of polysplenia syndrome.
M.P. Girish +4 more
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