Results 251 to 260 of about 37,969 (302)
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Neurologic Clinics, 2015
Progressive muscular atrophy (PMA) is a rare, sporadic, adult-onset motor neuron disease, clinically characterized by isolated lower motor neuron features; however, clinically evident upper motor neuron signs may emerge in some patients. Subclinical upper motor neuron involvement is identified pathologically, radiologically, and neurophysiologically in
Teerin, Liewluck, David S, Saperstein
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Progressive muscular atrophy (PMA) is a rare, sporadic, adult-onset motor neuron disease, clinically characterized by isolated lower motor neuron features; however, clinically evident upper motor neuron signs may emerge in some patients. Subclinical upper motor neuron involvement is identified pathologically, radiologically, and neurophysiologically in
Teerin, Liewluck, David S, Saperstein
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Progress in spinal muscular atrophy research
Current Opinion in Neurology, 2022Purpose of review The development of new therapies has brought spinal muscular atrophy (SMA) into the spotlight. However, this was preceded by a long journey – from the first clinical description to the discovery of the genetic cause to molecular mechanisms of RNA and DNA technology.
Claudia, Wurster, Susanne, Petri
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2017
Progressive muscular atrophy is a chronic, sporadic, slowly progressive degeneration of the anterior horn cells and cranial nerve nuclei. It differs from amyotrophic lateral sclerosis in that there are no pyramidal signs. However, it has links and overlaps with amyotrophic lateral sclerosis. The condition needs to be considered in the wide differential
Satish V. Khadilkar +2 more
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Progressive muscular atrophy is a chronic, sporadic, slowly progressive degeneration of the anterior horn cells and cranial nerve nuclei. It differs from amyotrophic lateral sclerosis in that there are no pyramidal signs. However, it has links and overlaps with amyotrophic lateral sclerosis. The condition needs to be considered in the wide differential
Satish V. Khadilkar +2 more
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Progressive juvenile segmental spinal muscular atrophy
Pediatric Neurology, 1993Juvenile segmental spinal muscular atrophy (JSSMA) typically involves the distal upper extremities and follows a benign course over 2-4 years then stabilizes. We report 2 males who presented in their teens with insidious distal upper extremity atrophy and weakness as in typical JSSMA but who then progressed to involvement of the lower extremities and ...
G T, Liu, L A, Specht
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Unilateral progressive muscular atrophy with fast symptoms progression
Neurologia i Neurochirurgia Polska, 2016Progressive muscular atrophy (PMA), or the lower motor neuron disease, is a sporadic disorder characterized by onset in adulthood, pure lower motor neuron involvement and relatively benign course. Muscle atrophy and weakness may be symmetrical or asymmetrical, but they are always bilateral.
Andrzej, Bogucki +3 more
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FAMILIAL PROGRESSIVE MUSCULAR ATROPHY
Archives of Neurology And Psychiatry, 1932Chronic progressive wasting of the skeletal muscles as a clinical observation has claimed the attention and interest of neurologic observers for many years. The underlying cause is a subject regarding which opinions have varied considerably from time to time.
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