Results 11 to 20 of about 239 (99)
Pulmonary Alveolar Proteinosis in an AIDS Patient without Concurrent Pulmonary Infection [PDF]
Patients with acquired immunodeficiency syndrome (AIDS) are potentially at increased risk for developing secondary pulmonary alveolar proteinosis because of underlying immunosuppression and frequent opportunistic lung infections. This condition. however,
Allen T Liu +4 more
core +2 more sources
PROTEINOSE ALVEOLAR PULMONAR SEVERA EM CRIANÇA: RELATO DE CASO E DESAFIOS NO TRATAMENTO [PDF]
Introdução: A proteinose alveolar pulmonar (PAP) é uma doença rara caracterizada pelo acúmulo de surfactante nos alvéolos ocasionando piora da função ventilatória afetando predominantemente crianças pequenas e recém-nascidas.Os exames de imagem e a biópsia são os principais meios de diagnóstico. A lavagem pulmonar é o tratamento mais eficaz. Objetivo:
Felipe Rocha +1 more
openaire +3 more sources
PROTEINOSE ALVEOLAR PULMONAR - UM DIAGNÓSTICO DIFÍCIL: A PROPÓSITO DE UM CASO CLÍNICO
As doenças do interstício pulmonar (DIP) são um extenso grupo de entidades raras, estando descritas mais de 200 entidades, com uma evolução aguda ou crónica e com diferentes graus de inflamação e/ou de fibrose.1 Engloba um grupo heterogéneo de ...
Ilda Coelho +3 more
doaj +3 more sources
Pulmonary surfactant is a substance composed of a lipoprotein complex that is essential to pulmonary function. Pulmonary surfactant proteins play an important role in the structure, function, and metabolism of surfactant; 4 specific surfactant proteins ...
Priscila Pinheiro Ribeiro Lyra +1 more
doaj +2 more sources
Progressive dyspnea associated with a crazy-paving appearance on a chest computed tomography scan. [PDF]
A ‘crazy‐paving’ appearance of the lungs on computed tomography scanning of the chest was first described nearly 20 years ago in patients with pulmonary alveolar proteinosis, and was thought to be characteristic of this condition. However, this pattern has subsequently been reported in a variety of pulmonary diseases and is now considered to be ...
Maimon N, Paul N, Downey GP.
europepmc +2 more sources
Rare lung disease II: pulmonary alveolar proteinosis. [PDF]
The present article is the second in a series on rare lung diseases. It focuses on pulmonary alveolar proteinosis (PAP), a disorder in which lipoproteinaceous material accumulates in the alveolar space. PAP was first described in 1958, and for many years the nature of the material accumulating in the lungs was unknown. Major insights into PAP have been
Juvet SC +3 more
europepmc +2 more sources
Rare lung diseases I--Lymphangioleiomyomatosis. [PDF]
The present article is the first in a series that will review selected rare lung diseases. The objective of this series is to promote a greater understanding and awareness of these unusual conditions among respirologists. Each article will begin with a case that serves as a focal point for a discussion of the pathophysiology and management of the ...
Juvet SC, Hwang D, Downey GP.
europepmc +2 more sources
Proteinose alveolar pulmonar: Relato de caso / Pulmonary alveolar proteinose: Case report [PDF]
INTRODUÇÃO: A proteinose alveolar pulmonar (PAP), é descrita como uma doença rara, caracterizada pelo acúmulo de surfactante pulmonar, composto por glicoproteínas, nos alvéolos. Podendo ser de origem primária ou idiopática e secundária a outros fatores predisponentes, cujo tratamento se baseia em lavagem pulmonar total (LPT).
de Oliveira, Jady Rodrigues +11 more
openaire +2 more sources

