A Case of Autoimmune Pulmonary Alveolar Proteinosis [PDF]
Clinical Case ReportsChemotherapeutic agents or regular doses of Rituximab may represent a potential therapeutic option for refractory cases of autoimmune pulmonary alveolar proteinosis.
Meher Binte Ali +4 more
doaj +3 more sources
Primary pulmonary alveolar proteinosis [PDF]
Vojnosanitetski Pregled, 2012 Introduction. Pulmonary alveolar proteinosis is an uncommon disease characterized by the accumulation of surfactant proteins and phospholipids within the alveolar spaces. Acquired disease can be idiopathic (primary) and secondary.
Šarac Sanja +5 more
doaj +5 more sources
Pulmonary Alveolar Proteinosis [PDF]
Canadian Respiratory Journal, 2012 Pulmonary alveolar proteinosis (PAP) is a disease of alveolar accumulation of phospholipoproteinaceous material that results in gas exchange impairment leading to dyspnea and alveolar infiltrates.
Sandeep M Patel +3 more
doaj +7 more sources
Anaesthesia for serial whole-lung lavage in a patient with severe pulmonary alveolar proteinosis: a case report [PDF]
Journal of Medical Case Reports, 2008 Introduction Pulmonary alveolar proteinosis is a rare condition that requires treatment by whole-lung lavage. We report a case of severe pulmonary alveolar proteinosis and discuss a safe and effective strategy for the anaesthetic management of patients ...
Webb Stephen T +3 more
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Unsuspected pulmonary alveolar proteinosis in a patient with acquired immunodeficiency syndrome: a case report [PDF]
Journal of Medical Case Reports, 2011 Introduction Diffuse lung infiltrates are a common finding in patients with acquired immunodeficiency syndrome and causes range from infectious processes to malignancies or interstitial lung diseases.
Niazi Masooma +3 more
doaj +2 more sources
Pulmonary alveolar proteinosis [PDF]
European Respiratory Review, 2011 Pulmonary alveolar proteinosis (PAP) is a rare pulmonary disease characterised by alveolar accumulation of surfactant. It may result from mutations in surfactant proteins or granulocyte macrophage-colony stimulating factor (GM-CSF) receptor genes, it may
B. Crestani +7 more
doaj +8 more sources
Congenital Pulmonary Alveolar Proteinosis [PDF]
Case Reports in Pediatrics, 2013 Pulmonary alveolar proteinosis (PAP) is a rare syndrome characterized by pulmonary surfactant accumulation within the alveolar spaces. It occurs with a reported prevalence of 0.1 per 100,000 individuals. Two clinically different pediatric types have been
Saber Hammami +5 more
doaj +3 more sources
Therapeutic Whole Lung Lavage for Pulmonary Alveolar Proteinosis: Technique With Continuous Video‐Enabled Double Lumen Endotracheal Tube [PDF]
Respirology Case ReportsTherapeutic whole lung lavage with a continuous video‐enabled double‐lumen endotracheal tube improves the safety of therapeutic whole lung lavage in autoimmune pulmonary alveolar proteinosis.
Kevin Davidson
doaj +2 more sources
Whole Lung Lavage in Autoimmune Pulmonary Alveolar Proteinosis: Unique Challenges in a Resource‐Limited Setting [PDF]
Clinical Case ReportsAutoimmune pulmonary alveolar proteinosis (PAP) is characterized by antibodies to granulocyte–macrophage colony‐stimulating factor (GM‐CSF), alveolar macrophage dysfunction, and surfactant accumulation.
Ashesh Dhungana +6 more
doaj +2 more sources
Pulmonary alveolar proteinosis [PDF]
Nature Reviews Disease Primers, 2019 Pulmonary alveolar proteinosis (PAP) is a syndrome characterized by the accumulation of alveolar surfactant and dysfunction of alveolar macrophages. PAP results in progressive dyspnoea of insidious onset, hypoxaemic respiratory failure, secondary infections and pulmonary fibrosis.
Trapnell, Bruce C. +9 more
+8 more sources