Results 31 to 40 of about 8,581 (204)
Highlights of the Brazilian Thoracic Association guidelines for interstitial lung diseases [PDF]
, 2012 Interstitial lung diseases (ILDs) are heterogeneous disorders, involving a large number of conditions, the approach to which continues to pose an enormous challenge for pulmonologists.
Aidé, Miguel Abidon +24 more
core +3 more sources
Proceedings: Regenerative Medicine for Lung Diseases: A CIRM Workshop Report. [PDF]
, 2017 The mission of the California Institute of Regenerative Medicine (CIRM) is to accelerate treatments to patients with unmet medical needs. In September 2016, CIRM sponsored a workshop held at the University of California, Los Angeles, to discuss ...
DeWitt, Natalie D +2 more
core +1 more source
Pulmonary Alveolar Proteinosis in an AIDS Patient without Concurrent Pulmonary Infection
Canadian Respiratory Journal, 1995 Patients with acquired immunodeficiency syndrome (AIDS) are potentially at increased risk for developing secondary pulmonary alveolar proteinosis because of underlying immunosuppression and frequent opportunistic lung infections. This condition. however,
Allen T Liu +4 more
doaj +1 more source
BMC Gastroenterology, 2021 Background Gastrointestinal lesions, which sometimes develop in Behçet’s disease (BD), are referred to as intestinal BD. Although rare, intestinal BD can be accompanied by myelodysplastic syndrome (MDS) with abnormal karyotype trisomy 8, which is ...
Hiroshi Shimizu +15 more
doaj +1 more source
Autoimmune pulmonary alveolar proteinosis in children
ERJ Open Research, 2022 In childhood, a multitude of causes lead to pulmonary alveolar proteinosis (PAP), an excessive surfactant accumulation in the alveolar space, limiting gas exchange.
Matthias Griese +20 more
doaj +1 more source
Rituximab therapy in pulmonary alveolar proteinosis improves alveolar macrophage lipid homeostasis [PDF]
, 2012 Rationale Pulmonary Alveolar Proteinosis (PAP) patients exhibit an acquired deficiency of biologically active granulocyte-macrophage colony stimulating factor (GM-CSF) attributable to GM-CSF specific autoantibodies. PAP alveolar macrophages are foamy,
Barna, Barbara P +7 more
core +3 more sources
Journal of International Medical Research, 2022 Pulmonary alveolar proteinosis (PAP) is a rare respiratory system disorder. Patients with PAP are at risk for a wide variety of secondary infections. This current case report describes a patient with PAP complicated by tuberculosis.
Guangtao Fan +3 more
doaj +1 more source
Von Hippel-Lindau protein is required for optimal alveolar macrophage terminal differentiation, self-renewal, and function [PDF]
, 2018 The rapid transit from hypoxia to normoxia in the lung that follows the first breath in newborn mice coincides with alveolar macrophage (AM) differentiation.
Brandi, Paola +12 more
core +4 more sources
Proteinose alveolar congénita.
Acta Médica Portuguesa, 2005 Pulmonary Alveolar Proteinosis (PAP) is a rare entity characterized by the intra-alveolar accumulation of proteinaceous PAS positive and diastase resistant material. Its pathogenesis remains unclear, although a surfactant protein B deficiency and changes
Susana Pissarra +3 more
doaj +1 more source
Genetic determinants of risk in autoimmune pulmonary alveolar proteinosis
Nature Communications, 2021 Autoimmune pulmonary alveolar proteinosis (aPAP) is a complex lung disease caused by abnormal surfactant homeostasis. Here, the authors carry out a genome-wide association study of aPAP in a Japanese cohort, finding variants in the MHC and suggesting ...
Saori Sakaue +56 more
doaj +1 more source