Results 41 to 50 of about 8,581 (204)
Unusual cause of dyspnea in patient with Myelofibrosis: The Ruxolitinib lung
Respiratory Medicine Case ReportsAlthough pulmonary complications are frequent in patients suffering from hematological diseases, secondary pulmonary alveolar proteinosis is a very rare complication of myelofibrosis.
Antoine El Kik +4 more
doaj +1 more source
iPSC-Derived Macrophages Effectively Treat Pulmonary Alveolar Proteinosis in Csf2rb-Deficient Mice
Stem Cell Reports, 2018 Summary: Induced pluripotent stem cell (iPSC)-derived hematopoietic cells represent a highly attractive source for cell and gene therapy. Given the longevity, plasticity, and self-renewal potential of distinct macrophage subpopulations, iPSC-derived ...
Adele Mucci +22 more
doaj +1 more source
Innate immune activation by inhaled lipopolysaccharide, independent of oxidative stress, exacerbates silica-induced pulmonary fibrosis in mice [PDF]
, 2012 Acute exacerbations of pulmonary fibrosis are characterized by rapid decrements in lung function. Environmental factors that may contribute to acute exacerbations remain poorly understood.
AG Heppleston +55 more
core +3 more sources
Pulmonary Alveolar Proteinosis Syndrome [PDF]
Clinics in Chest Medicine, 2016 Pulmonary alveolar proteinosis (PAP) is a rare syndrome characterized by the accumulation of surfactant in alveoli and terminal airways resulting in respiratory failure. PAP comprises part of a spectrum of disorders of surfactant homeostasis (clearance and production).
Takuji, Suzuki, Bruce C, Trapnell
openaire +2 more sources
Idiopathic desquamative interstitial pneumonia in a child: a case report. [PDF]
, 2014 Desquamative interstitial pneumonia is a rare form of interstitial lung disease in children. Respiratory symptoms appear progressively, are often subtle, and diagnosis is often delayed by a mean of 6 months after onset.
Aubert, J.D. +4 more
core +1 more source
Whole lung lavage combined with Granulocyte-macrophage colony stimulating factor inhalation for an adult case of refractory pulmonary alveolar proteinosis [PDF]
, 2014 BACKGROUND: Whole-lung lavage (WLL) is classically the first-line treatment for symptomatic pulmonary alveolar proteinosis (PAP). However, some patients require multiple WLLs because of refractory nature of their PAP. In this instance, these patients may
Hong yan Yu +4 more
core +2 more sources
Pulmonary Alveolar Proteinosis
Apollo Medicine, 2008 I Seetharam Naidu, Sridhar
doaj +3 more sources
Indian Journal of Radiology and Imaging, 2018 Alveolar proteinosis is a rare pulmonary disease characterized by intra-alveolar accumulation of surfactant composed of lipoproteinaceous material, related to a lack of surfactant resorption by alveolar macrophages. Crazy paving pattern is characteristic,
Lova Hasina Rajaonarison Ny Ony Narindra +6 more
doaj +1 more source
Autoimmune hyperphosphatemic tumoral calcinosis in a patient with FGF23 autoantibodies [PDF]
, 2018 Hyperphosphatemic familial tumoral calcinosis (HFTC)/hyperostosis-hyperphosphatemia syndrome (HHS) is an autosomal recessive disorder of ectopic calcification due to deficiency of or resistance to intact fibroblast growth factor 23 (iFGF23). Inactivating
Burbelo +14 more
core +1 more source
Clinical &Translational Immunology, Volume 15, Issue 1, 2026.In this study, we analysed the immune responses of blood‐derived monocyte macrophages and iPSC‐derived macrophages following BCG/HKMT infection. We found that iPSC‐derived macrophages displayed a markedly stronger activation profile, including faster migration, increased reactive oxygen species production, elevated apoptosis marker expression and ...
Daniela Paasch +17 more
wiley +1 more source