Results 81 to 90 of about 61,025 (285)

Pulmonary alveolar proteinosis

Tzu Chi Medical Journal, 2015
Abstract not availableBangladesh Crit Care J September 2014; 2 (2): 90 ...
Cheng-Fa Chou, Wen-Chih Huang
openaire   +4 more sources

Autoimmune pulmonary alveolar proteinosis in an adolescent successfully treated with inhaled rhGM-CSF (molgramostim)

Respiratory Medicine Case Reports, 2018
Autoimmune pulmonary alveolar proteinosis (aPAP) is a rare parenchymal lung disease characterized by accumulation of surfactant in the airways with high levels of granulocyte-macrophage colony stimulating factor (GM-CSF) antibodies in blood.
Marta E. Gajewska, Sajitha S. Sritharan, Eric Santoni-Rugiu, Elisabeth M. Bendstrup   +3 more
doaj   +1 more source

Autoimmune hyperphosphatemic tumoral calcinosis in a patient with FGF23 autoantibodies [PDF]

, 2018
Hyperphosphatemic familial tumoral calcinosis (HFTC)/hyperostosis-hyperphosphatemia syndrome (HHS) is an autosomal recessive disorder of ectopic calcification due to deficiency of or resistance to intact fibroblast growth factor 23 (iFGF23). Inactivating
Burbelo, Christopher J. Romero, Daniela Egli-Spichtig, Emily Farrow, Farzana Perwad, Ichikawa, Lori C. Guthrie, Mary Scott Roberts, Michael J. Econs, Michael T. Collins, Peter D. Burbelo, Rachel I. Gafni, Shimada, Shoji Ichikawa, Uchida   +14 more
core   +1 more source

Molecular Investigation in Early‐Onset Interstitial Lung Disease: Results From 699 Unrelated Patients

Respirology, EarlyView.
ABSTRACT Background and Objective Interstitial lung diseases (ILDs) are rare and severe respiratory conditions that may ultimately result in pulmonary fibrosis (PF). The objective of this study was to present the results of molecular diagnosis of early‐onset ILD (from neonates to young adults < 50 years) in a reference genetic diagnostic laboratory ...
Camille Louvrier, Nadia Nathan, Vincent Cottin, Tifenn Desroziers, Valérie Nau, Yohan Soreze, Florence Dastot‐Le Moal, Philippe Reix, Diane Bouvry, Caroline Thumerelle, Martine Reynaud‐Gaubert, Alice Hadchouel, Grégoire Prévot, Effrosyni Manali, Caroline Kannengiesser, Ibrahima Ba, Serge Amselem, Véronique Houdouin, Raphaël Borie, Marie Legendre, on behalf of RespiRare and OrphaLung   +20 more
wiley   +1 more source

Fast-Track Extubation in a Patient Undergoing Whole Lung Lavage: A Case Report

Annals of Cardiac Anaesthesia
Pulmonary alveolar proteinosis (PAP) is a rare pulmonary pathology characterized by the accumulation of surfactant within type II alveolar epithelial cells.
Gade Sandeep, Subrata K. Singha, Anil Gupta, Keerthi Chinnadurai, Harishchandra Gupta   +4 more
doaj   +1 more source

Serial bronchoscopic lung lavage in pulmonary alveolar proteinosis under local anesthesia

Lung India, 2015
Pulmonary alveolar proteinosis (PAP) is a rare disease, characterized by alveolar accumulation of surfactant composed of proteins and lipids due to defective surfactant clearance by alveolar macrophages.
K Rennis Davis, D Thomas Vadakkan, E V Krishnakumar, A Muhammed Anas   +3 more
doaj   +1 more source

Pulmonary alveolar proteinosis - a case report [PDF]

, 2014
Efst á síðunni er hægt að nálgast greinina í heild sinni með því að smella á hlekkinnPróteinútfellingar í lungnablöðrum (pulmonary alveolar proteinosis, PAP) eru oftast af óþekktum orsökum en meingerð sjúkdómsins er rakin til skertrar átfrumuvirkni í ...
Eyþór Björnsson, Felix Valsson, Hrönn Harðardóttir, Ragnheiður M. Jóhannesdóttir, Sigfús Nikulásson, Steinn Jónsson, Tómas Guðbjartsson, Ólöf R. Ámundadóttir   +7 more
core  

Pulmonary Hypertension and Other Potentially Fatal Pulmonary Complications in Systemic Juvenile Idiopathic Arthritis [PDF]

, 2012
Objective Systemic juvenile idiopathic arthritis (JIA) is characterized by fevers, rash, and arthritis, for which interleukin‐1 (IL‐1) and IL‐6 inhibitors appear to be effective treatments.
Carol A. Wallace, Egla Rabinovich, Elizabeth Kessler, Jennifer E. Weiss, Jordi Antón, Karen Onel, Kathryn L. Haroldson, Marilynn Punaro, Melissa M. Hazen, Meredith Riebschleger, Murray H. Passo, Nico Wulffraat, null null, Patricia Woo, Peter R. Blier, Robert M. Rennebohm, Sheila Oliveira, Tzielan Lee, Valeria Gerloni, Yukiko Kimura   +19 more
core   +1 more source

Epithelial–Mesenchymal Transition in Human Alveolar Cells Exposed to Indium Chloride

Journal of Applied Toxicology, Volume 45, Issue 11, Page 2353-2362, November 2025.
ABSTRACT For workers in the industry, occupational exposure to indium compounds induces pulmonary disorders, such as interstitial pneumonia. Moreover, lung cancer has been reported in both humans and rodents exposed to indium compounds by inhalation. However, the biological mechanism underlying indium‐induced disorders is poorly understood.
Eiki Kimura, Sharif Ahmed, Haijiao Chen, Yusuke Hiraku   +3 more
wiley   +1 more source

Rescue of respiratory failure in pulmonary alveolar proteinosis due to pathogenic MARS1 variants

Pediatric Pulmonology, 2020
Pulmonary alveolar proteinosis (PAP) is a heterogeneous condition with more than 100 different underlying disorders that need to be differentiated to target therapeutic options, which are generally limited.
Dominic Lenz, M. Stahl, E. Seidl, D. Schöndorf, H. Brennenstuhl, Florian Gesenhues, T. Heinzmann, T. Longerich, Marisa I. Mendes, H. Prokisch, G. Salomons, C. Schön, Desirée E. C. Smith, O. Sommerburg, M. Wagner, J. Westhoff, K. Reiter, C. Staufner, M. Griese   +18 more
semanticscholar   +1 more source