Results 21 to 30 of about 4,339 (169)

Good's Syndrome with Pneumocystis Jiroveci Lymphadenitis and Pure Red Cell Aplasia [PDF]

Journal of Microbiology and Infectious Diseases, 2016
Pneumocystis jiroveci lymphadenitis is a rare manifestation of extrapulmonary pneumocystosis. A case of recurrent infection with lymphadenitis caused by Pneumocystis jiroveci in a middle-aged patient is described.
Jintana - Srisompong, Torpong - Thongngarm, Popchai - Ngamskulrungroj, Ruchira - Ruangchira-urai, Adhiratha - Boonyasiri
doaj   +1 more source

Pure red cell aplasia in a simultaneous pancreas-kidney transplantation patient: inside the erythroblast

Hematology Reports, 2012
A case of pure red cell aplasia in a simultaneous kidney-pancreas transplant recipient on immunosuppressive therapy is reported here. The patient presented with anemia unresponsive to erythropoietin treatment.
Francesca Labbadia, Eduardo Salido-Fierréz, Juliana Majado-Martinez, Valentin Cabañas-Perianes, José M. Moraleda Jiménez   +4 more
doaj   +1 more source

Secondary pure red cell aplasia in multiple myeloma treated with lenalidomide

Leukemia Research Reports, 2018
Pure red cell aplasia (PRCA) is a rare disorder characterized by marked erythroid hypoplasia with maturation arrest in the bone marrow. Secondary acquired PRCA may be associated with hematologic disorders.
Tomoki Ito, Aya Nakaya, Shinya Fujita, Atsushi Satake, Takahisa Nakanishi, Yoshiko Azuma, Yukie Tsubokura, Akiko Konishi, Masaaki Hotta, Hideaki Yoshimura, Kazuyoshi Ishii, Shosaku Nomura   +11 more
doaj   +1 more source

Aggressive Systemic Mastocytosis in Association with Pure Red Cell Aplasia

Case Reports in Hematology, 2018
Aggressive systemic mastocytosis (ASM) is characterized by mast cell accumulation in systemic organs. Though ASM may be associated with other hematological disorders, the association with pure red cell aplasia (PRCA) is rare and has not been reported ...
Dhauna Karam, Sean Swiatkowski, Mamata Ravipati, Bharat Agrawal   +3 more
doaj   +1 more source

Clonal hematopoiesis in adult pure red cell aplasia

Scientific Reports, 2021
Idiopathic pure red cell aplasia (PRCA) and secondary PRCA associated with thymoma and large granular lymphocyte leukemia are generally considered to be immune-mediated.
Naohito Fujishima, Junki Kohmaru, Souichi Koyota, Keiji Kuba, Tomoo Saga, Ayumi Omokawa, Yuki Moritoki, Shigeharu Ueki, Fumihiro Ishida, Shinji Nakao, Akira Matsuda, Akiko Ohta, Kaoru Tohyama, Hiroshi Yamasaki, Kensuke Usuki, Yasuhiro Nakashima, Shinya Sato, Yasushi Miyazaki, Yasuhito Nannya, Seishi Ogawa, Kenichi Sawada, Kinuko Mitani, Makoto Hirokawa   +22 more
doaj   +1 more source

Nanomedicine applications in lymphoma: Advancing precision diagnostics, targeted therapeutics, and prospective developments

VIEW, EarlyView.
Lymphoma is a group of blood cancers that can appear in lymph nodes, blood, bone marrow, spleen, liver, or the central nervous system, which makes drug delivery and disease monitoring difficult. This review summarizes how nanomedicine technologies may improve targeted treatment and imaging, while carefully separating approved or guideline‐supported ...
Mohd Ahmar Rauf, Yara Mashal, Afeefa Rao, Nasar Ata, Arun K. Iyer, Farhan Shah   +5 more
wiley   +1 more source

Red lines and green lights: Gene therapy for inherited erythroid disorders beyond the haemoglobinopathies

British Journal of Haematology, EarlyView.
Gene therapy is revolutionizing treatment paradigms for haemoglobinopathies, establishing a translational framework for disorders that impact red blood cell development. In their paper, Joshi et al. describe the preclinical and early clinical landscape of gene therapies for non‐haemoglobinopathy erythroid disorders and highlight common thematic ...
Gaurav Joshi, Nandakumar Natarajan, Kathryn E. Dickerson, Richard A. Voit   +3 more
wiley   +1 more source

Clinical profile of pure red cell aplasia

MRIMS Journal of Health Sciences, 2015
Clinical and hematological profiles of twelve patients with Pure Red Cell Aplasia (PRCA) are described. It was more common in fifth decade and in males. Eight patients had mild upper respiratory tract infection, eight patients had indigenous drug intake ...
E A Ashok Kumar, S Banavali
doaj   +1 more source

Prospective Study of Targeted Busulfan–Fludarabine Conditioning for Hematopoietic Stem Cell Transplantation in Genetic Rare Diseases

European Journal of Haematology, EarlyView.
ABSTRACT Objectives Genetic rare diseases (GRDs), including chronic granulomatous disease, familial hemophagocytic lymphohistiocytosis, and congenital neutropenia, often require hematopoietic stem cell transplantation (HSCT) as the only curative option.
Bo Kyung Kim, Kyung Taek Hong, Jung Yoon Choi, Hyun Jin Park, Kyung‐Sang Yu, In‐Jin Jang, Hyoung Jin Kang   +6 more
wiley   +1 more source

Management of Iron Overload in Infants and Toddlers With Diamond–Blackfan Anemia Syndrome: A French–Italian Study

American Journal of Hematology, Volume 101, Issue 8, Page 1856-1865, August 2026.
ABSTRACT Diamond–Blackfan Anemia Syndrome (DBAS) is a rare congenital anemia often requiring chronic red blood cell transfusions from infancy. Without appropriate chelation, iron overload develops early and may be severe; however, no data are available on chelation in patients under 3 years of age.
Francesca Torchio, Baptiste Lecalvez, Emanuela Garelli, Coralie Mallebranche, Adriana Carando, Marie‐Pierre Castex, Nathalie Garnier, Marco Zecca, Nathalie Aladjidi, Elisa Bertoni, Arthur Sterin, Maria Licciardello, Anne Sirvent, Antonella Sau, Isabelle Marie, Benedicte Bruno, Lydie M. Da Costa, Franca Fagioli, Paola Quarello, Thierry Leblanc   +19 more
wiley   +1 more source