Results 51 to 60 of about 122 (87)

Epidemiology of progressive intellectual and neurological deterioration in UK children

Developmental Medicine &Child Neurology, Volume 68, Issue 3, Page 418-428, March 2026.
This study of PIND in UK children was carried out via the British Paediatric Surveillance Unit from 1997 to 2024. It identified six cases of vCJD. 2367 children had other diagnoses explain their deterioration. There were 259 other diseases in the diagnosed group.
Christopher M. Verity, Polly J. Maunder, Anne Marie Winstone, Suvankar Pal   +3 more
wiley   +1 more source

Quantitative gait analysis following hemispherotomy for Rasmussen′s encephalitis

Journal of Pediatric Neurosciences, 2007
Peri-insular hemispherotomy is a form of disconnective hemispherectomy involving complete disconnection of all ascending / descending and commisural connections of one hemisphere.
Santhosh George Thomas, Judy Ann David, Suranjan Bhattacharji, Roy Thomas Daniel   +3 more
doaj   +1 more source

Systemic T Cell Receptor Profiling Reveals Adaptive Immune Activation and Potential Immune Signatures of Diagnosis and Brain Atrophy in Epilepsy

Annals of Clinical and Translational Neurology, Volume 13, Issue 2, Page 296-309, February 2026.
ABSTRACT Objective Epilepsy is increasingly associated with immune dysregulation and inflammation. The T cell receptor (TCR), a key mediator of adaptive immunity, shows repertoire alterations in various immune‐mediated diseases. The unique TCR sequence serves as a molecular barcode for T cells, and clonal expansion accompanied by reduced overall TCR ...
Yong‐Won Shin, Sang Bin Hong, Yong Woo Shin, Inpyeong Hwang, Jaeseong Oh, Jihyeon Choi, Narae Kim, Jangsup Moon, Keun‐Hwa Jung, Kyung‐Il Park, Ki‐Young Jung, Kon Chu, Sang Kun Lee   +12 more
wiley   +1 more source

Epilepsia partialis continua as the presenting manifestation of Creutzfeldt–Jakob disease: A video‐polygraphic clinical vignette

Epileptic Disorders, Volume 28, Issue 3, Page 920-924, June 2026.
Roberta Cutellè, Angelo Pascarella, Ada Santoro, Vittoria Cianci, Anna Mammì, Giovanbattista Gaspare Tripodi, Caterina Prestandrea, Sara Gasparini, Edoardo Ferlazzo   +8 more
wiley   +1 more source

Rasmussen Encephalitis Closely Mimicking Infantile Spasms: A Case Report [PDF]

Journal of Clinical and Diagnostic Research
Rasmussen Encephalitis (RE) is a rare, progressive neurological disorder primarily affecting children, with early-onset cases posing significant diagnostic challenges. In infants, RE may closely resemble more common conditions such as infantile spasms,
Touheer Pasha, Shilpi Agrawal, Mg Ravanagomagan   +2 more
doaj   +1 more source

The Quality of Life of a Teenager with Rasmussen’s Encephalitis — Case Report

Pielęgniarstwo Neurologiczne i Neurochirurgiczne, 2018
Introduction. Rasmussen’s Syndrome (RE), is a rare type of chronic focal encephalitis (CFE) of unexplained etiology and progressive course. It is characterized by resistant to treatment epileptic seizures.
Marta Lewicka, Ewa Barczykowska, Bogumiła Małecka, Ewa Kontna   +3 more
doaj   +1 more source

Aberrant activation of the mTOR signaling pathway in Rasmussen encephalitis

Scientific Reports
This study aimed to delineate the mechanistic target of the rapamycin (mTOR) pathway in the brain tissue of patients with Rasmussen encephalitis (RE) compared to individuals without epilepsy and those with focal cortical dysplasia (FCD) to identify ...
Jiao Qiao, Chongyang Tang, Mingguo Xie, Mingkun Gong, Cong Fu, Zizhang Cheng, Zheng Chen, Aoxue Mei, Yujie Bo, Meng Zhao, Tianfu Li, Taoyun Ji, Renxi Wang, Jiahui Deng, Guoming Luan   +14 more
doaj   +1 more source

A review of pediatric cerebral hemiatrophy: a series of cases

MGM Journal of Medical Sciences
Cerebral hemiatrophy represents a spectrum of neurological disorders marked by unilateral cerebral atrophy, often resulting in significant neurological and functional impairments.
Sumedha Varshney, Rahul Ranjan, Nirmal Pandey, Namrata, Ashok Yadav, Ramesh Chandra Rajput   +5 more
doaj   +1 more source

Research progress on pathogenesis and treatment of Rasmussen encephalitis

Chinese Journal of Contemporary Neurology and Neurosurgery
The pathogenesis of Rasmussen encephalitis (RE) remains unclear. Current theories suggest that viral infection, antibody⁃mediated humoral immune mechanisms, T lymphocytes mediated cellular immunity, and microglia mediated neurodegeneration may all be ...
WU Hong⁃mei, JI Tao⁃yun, ZHUANG Ji⁃xin   +2 more
doaj   +1 more source

Immune landscape of the affected brain in Rasmussen encephalitis

Scientific Reports
Rasmussen encephalitis (RE) is a rare neuroinflammatory disease characterized by intractable seizures and progressive brain atrophy that is usually confined to one cerebral hemisphere.
Giovanni Quinones-Valdez, Julia W. Chang, Shino D. Magaki, Harry V. Vinters, Noriko Salamon, Anthony C. Wang, Aria Fallah, Geoffrey C. Owens   +7 more
doaj   +1 more source