Results 41 to 50 of about 5,408,282 (157)

Rendu-Osler-Weber disease: update of medical and dental considerations

, 2008
Rendu-Osler-Weber disease, also known as hereditary hemorrhagic telangiectasia (HHT), is an autosomal dominant inherited disorder characterized by an aberrant vascular development. The reported prevalence is approximately 1 per 5,000-10,000. The clinical
van Dijk, F. S., van Hagen, J. M., Baart, J.A., van der Waal, I., van Hagen, J.M., Baart, J. A., Veldhuis, A. H. te, Veldhuis, E.C., van Dijk, F.S., Kwee, M.L., Veldhuis, E. C. te, Kwee, M. L., te Veldhuis, A.H., te Veldhuis, E.C.   +13 more
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Telangiectasia hemorrágica hereditária: ácido tranexâmico no tratamento de úlcera plantar Hereditary hemorrhagic telangiectasia: tranexamic acid for plantar ulcer

Anais Brasileiros de Dermatologia, 2005
Relato de um caso de úlcera plantar por fístula arteriovenosa em paciente portador de telangiectasia hemorrágica hereditária ou doença de Rendu-Osler-Weber tratado com ácido tranexâmico.
Gabriella Corrêa de Albuquerque, Célia Regina S. Corrêa de Carvalho, Cristiane R. de Oliveira, Dayse Pereira Terra, Sérgio Soares Quinete   +4 more
doaj   +1 more source

Endoscopic Classification of Severe Spontaneous Epistaxis: A Case‐Series of 445 Patients

Laryngoscope Investigative Otolaryngology, Volume 11, Issue 2, April 2026.
Epistaxis can be related to several histopathological findings. ABSTRACT Objective To identify the anatomical location and characterize the histopathological findings of severe spontaneous epistaxis through endoscopic evaluation and tissue biopsy.
Wen Zhang, Guangjin Chen, Jérôme R. Lechien   +2 more
wiley   +1 more source

[Rendu-Osler-Weber disease] [PDF]

, 2005
Contains fulltext : 48121.pdf (Publisher’s version ) (Open Access)Rendu-Osler-Weber disease or hereditary hemorrhagic telangiectasia (HHT) is a multisystem autosomal dominant hereditary disorder.
Sys, L.M., Hoogen, F.J.A. van den
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Novel Simplified Nasal Endoscopy Grading System for Hereditary Hemorrhagic Telangiectasia Patients

The Laryngoscope, Volume 136, Issue 2, Page 652-657, February 2026.
We validated a novel, simplified nasal endoscopy grading system for patients with Hereditary Hemorrhagic Telangiectasia (HHT). Our grading (mild, moderate, severe) demonstrated strong correlation with Epistaxis Severity Score (ESS) and Quality of Life (QoL), and showed substantial inter‐rater reliability (ICC = 0.8).
Ethan Soudry, Nimrod Amitai, Aiman Elmograbi, Igor Vainer, Meir Mei‐Zahav   +4 more
wiley   +1 more source

Osler-Weber-Rendu (OWR) Disease and Heart Failure

Clinical Medicine Insights: Cardiology, 2009
OWR is a genetic disease, transmitted as an autosomal dominant disorder characterized by arteriovenous malformations predominantly involving the mucocutaneous epithelium.
Arnon Blum, Rafea Shalabi
doaj   +1 more source

Rendú Osler Weber Syndrome; case report

Radiology Case Reports, 2022
Hereditary hemorrhagic telangiectasia (HHT), or Rendu-Osler-Weber disease, is a dominant autosomal disease characterized by the presence of multiple telangiectasia in skin and mucus, associated with arteriovenous malformations (AVM) of various organs ...
Oscar Manuel García Córdova, MD, Tania Cristina Pérez Morales, MD, Verónica Andrea del Pilar Barón Hernández, MD, José Sebastián Sotelo Cuéllar, MD   +3 more
doaj   +1 more source

Unmasking a Rare Genetic Puzzle: Hereditary Hemorrhagic Telangiectasia in a Black Kenyan Woman: A Case Report

Case Reports in Gastrointestinal Medicine, Volume 2026, Issue 1, 2026.
Background Hereditary hemorrhagic telangiectasia (HHT) is a rare genetic disorder characterized by mucocutaneous and visceral telangiectasias, often leading to severe complications. This case report presents an uncommon manifestation of HHT in a 57‐year‐old Black Kenyan female with upper gastrointestinal bleeding. Given the rarity of HHT in our region,
Lavender Otom, Priyanka Panwar, Farida Kaittany, Ben Clement Lomatayo, Yoshifumi Nakayama   +4 more
wiley   +1 more source

Rendu-Osler-weber disease. Case report [PDF]

, 2016
Rendu-Osler-Weber disease is the most frequently observed genetic hemorrhagic angiopathy with local wall thinning, distention of microcirculation vessels' lumen, and incomplete local hemostasis.
Kurochkin Sergei Vyacheslavovich, Gafurov Marat, Kurochkin S., Gafurov M., Zidikhanov Damir Ilshatovich, Chuvashaev I., Chuvashaev Iskander, Zidikhanov D.   +7 more
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Characterizing the Healthcare Utilization and Costs of Hereditary Hemorrhagic Telangiectasia

American Journal of Hematology, Volume 100, Issue 10, Page 1722-1735, October 2025.
ABSTRACT Hereditary hemorrhagic telangiectasia (HHT) is the second‐most common inherited bleeding disorder worldwide, afflicting one in 4000–5000 people, and is the most morbid inherited bleeding disorder of women. HHT causes recurrent severe epistaxis, chronic gastrointestinal bleeding, heavy menstrual bleeding, and arteriovenous malformations in the ...
Hanny Al‐Samkari, Tracy J. Mayne, Misty Troutt, Hemant Patle, Marianne Clancy, Eric Duhaime   +5 more
wiley   +1 more source