Results 91 to 100 of about 1,710,432 (184)

Differential diagnosis of hepatopulmonary syndrome (HPS): Portopulmonary hypertension (PPH) and hereditary hemorrhagic telangiectasia (HHT)

Biomolecules & Biomedicine, 2017
Hepatopulmonary syndrome (HPS) is a severe complication of advanced liver disease associated with an extremely poor prognosis. HPS is diagnosed in 4-47% of patients with cirrhosis and in 15-20% of candidates for liver transplantation.
Inna Krynytska, Mariya Marushchak, Anna Mikolenko, Anzhela Bob, Iryna Smachylo, Ludmyla Radetska, Olga Sopel   +6 more
doaj   +1 more source

Anesthetic Experience of Extrathoracic Surgery in Rendu-Osler-Weber Syndrome

Korean Journal of Anesthesiology, 2002
The Rendu-Osler-Weber syndrome (hereditary hemorrhagic telangiectasia) is an autosomal dominant disorder of blood vessels associated with mucocutaneous telangiectasis and arterivenous malformations in several organs. A pulmonary arteriovenous fistulae can cause hypoxemia, hemoptysis, polycythemia and clubbing.
Ik Sang Seung, Kyo Sang Kim
openaire   +1 more source

Clinical improvement after banding of a pulmonary branch artery in a symptomatic patient with Osler-Rendu-Weber syndrome.

, 2010
We report a symptomatic newborn with Osler-Rendu-Weber syndrome, multiple and diffuse pulmonary arteriovenous malformations, and right-to-left shunting in the left lung.
Ruf, B;Eicken, A;Schreiber, C;Hess, J
core   +1 more source

Hereditary Hemorrhagic Telangiectasia - a literature review

Journal of Education, Health and Sport
Introduction and purpose: Hereditary hemorrhagic telangiectasia (HHT), also known as Osler-Weber-Rendu syndrome, is a rare and complex vascular disorder characterized by abnormal blood vessel formation.
Marcel Stodolak, Aleksandra Krużel, Kamil Kłos, Piotr Sajdak, Justyna Tomasik, Marika Dębik, Łukasz Szydłowski, Klaudia Żurowska, Seweryn Ziajor, Artur Bednarski, Mikołaj Turski   +10 more
doaj   +1 more source

High-Output Heart Failure Contributing to Recurrent Epistaxis Kiesselbach Area Syndrome in a Patient With Hereditary Hemorrhagic Telangiectasia

Journal of Investigative Medicine High Impact Case Reports, 2017
Hereditary hemorrhagic telangiectasia (HHT), also known as Osler-Weber-Rendu syndrome, is a rare genetic blood disorder that leads to abnormal bleeding due to absent capillaries and multiple abnormal blood vessels known as arteriovenous malformations.
Venugopal Brijmohan Bhattad MD, Jennifer N. Bowman BA, Hemang B. Panchal MD, MPH, Timir K. Paul MD, PhD   +3 more
doaj   +1 more source

A Rare Association: Hereditary Hemorrhagic Telangiectasia with Liver Cirrhosis Causing Portal Hypertension

Case Reports in Gastrointestinal Medicine
Hereditary hemorrhagic telangiectasia (HHT), also known as Rendu–Osler–Weber syndrome, is a vascular disorder of autosomal dominant etiology. The hallmark clinical feature is the presence of recurrent episodes of epistaxis in patients with vascular ...
Denisse Morales-Tovar, Froylan D. Martínez-Sánchez, Alejandro Gabutti-Thomas, Rodolfo Rivera-Martínez, Jacqueline Córdova-Gallardo   +4 more
doaj   +1 more source

UEG Week 2025 Poster Presentations

United European Gastroenterology Journal, Volume 13, Issue S8, Page S803-S1476, October 2025.
wiley   +1 more source

Osler-Weber-Rendu syndrome - Pathological manifestations and autopsy considerations

, 2001
An 18-year-old university student with Osler-Weber-Rendu disease collapsed in the bathroom. Attempted resuscitation was unsuccessful. Her past history included recurrent epistaxes, mucosal telangiectasias, intracranial arteriovenous malformations with ...
Byard, R., Schliebs, J., Koszyca, B.
core   +1 more source

Rendu-Osler-Weber disease: update of medical and dental considerations

, 2008
Rendu-Osler-Weber disease, also known as hereditary hemorrhagic telangiectasia (HHT), is an autosomal dominant inherited disorder characterized by an aberrant vascular development. The reported prevalence is approximately 1 per 5,000-10,000. The clinical
van Dijk, F. S., van Hagen, J. M., Baart, J.A., van der Waal, I., van Hagen, J.M., Baart, J. A., Veldhuis, A. H. te, Veldhuis, E.C., van Dijk, F.S., Kwee, M.L., Veldhuis, E. C. te, Kwee, M. L., te Veldhuis, A.H., te Veldhuis, E.C.   +13 more
core   +1 more source

A case of Osler-Weber-Rendu syndrome, diagnosed at geriatric age, presenting with gastrointestinal bleeding, telangiectasias, and asymptomatic liver and lung angiodysplasia

Egyptian Liver Journal
Background Osler-Weber-Rendu syndrome (OWRS) is an autosomal dominant disease with recurrent epistaxis, mucocutaneous telangiectasias, and arteriovenous malformations.
ŞH Aktaş, S. Basat
doaj   +1 more source