Results 41 to 50 of about 8,159,171 (345)
CNS Drugs, 2019 Treatment with nusinersen has demonstrated significant and clinically meaningful benefits in clinical trials in infants and children with spinal muscular atrophy (SMA).
B. Darras +8 more
semanticscholar +1 more source
LEO Precise Orbit Determination with Inter-satellite Links
Remote Sensing, 2019 Traditional precise orbit determination (POD) for low Earth orbit (LEO) satellites relies on observations from ground stations and onboard receivers.
Xingxing Li +5 more
doaj +1 more source
Remote Sensing, 2017 Arctic tundra ecosystems exhibit small-scale variations in species composition, micro-topography as well as significant spatial and temporal variations in moisture.
Alison Leslie Beamish +3 more
doaj +1 more source
Remote Sensing, 2020 Urban land cover classification for high-resolution images is a fundamental yet challenging task in remote sensing image analysis. Recently, deep learning techniques have achieved outstanding performance in high-resolution image classification ...
Chun Liu +5 more
doaj +1 more source
Online refinement of day‐ahead forecasting using intraday data for campus‐level load
IET Generation, Transmission & Distribution, 2022 Day‐ahead forecasting for campus‐level load is important for better energy management, but especially difficult to be accurate, compared to large‐scale loads such as cities or regions.
Yuanfan Ji +3 more
doaj +1 more source
The unpredictably eruptive dynamics of spruce budworm populations in eastern Canada
Population Ecology, EarlyView.We examine historical population data for spruce budworm from several locations through the period 1930–1997, and use density‐dependent recruitment curves to test whether the pattern of population growth over time is more consistent with Royama's (1984; Ecological Monographs 54:429–462) linear R(t) model of harmonic oscillation at Green River New ...
Barry J. Cooke, Jacques Régnière
wiley +1 more source
PLoS ONE, 2018 Spinal muscular atrophy (SMA) is a monogenic disorder caused by loss of function mutations in the survival motor neuron 1 gene, which results in a broad range of disease severity, from neonatal to adult onset.
A. Chabanon +21 more
semanticscholar +1 more source
Network topology drives population temporal variability in experimental habitat networks
Population Ecology, EarlyView.Habitat patches connected by dispersal pathways form habitat networks. We explored how network topology affects population outcomes in laboratory experiments using a model species (Daphnia carinata). Central habitat nodes in complex lattice networks exhibited lower temporal variability in population sizes, suggesting they support more stable ...
Yiwen Xu +3 more
wiley +1 more source
Acid ceramidase deficiency: Farber disease and SMA-PME
Orphanet Journal of Rare Diseases, 2018 Acid ceramidase (ACDase) deficiency is a spectrum of disorders that includes a rare lysosomal storage disorder called Farber disease (FD) and a rare epileptic disorder called spinal muscular atrophy with progressive myoclonic epilepsy (SMA-PME).
Fabian P. S. Yu +3 more
semanticscholar +1 more source
High-Frequency Electromagnetic Induction (HFEMI) Sensor Results from IED Constituent Parts
Remote Sensing, 2019 The detection and classification of subsurface improvised explosive devices (IEDs) remains one of the most pressing military and civilian problems worldwide. These IEDs are often intentionally made with either very small metallic parts or less-conducting
Benjamin Barrowes +3 more
doaj +1 more source